{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,22]],"date-time":"2026-09-22T21:26:46Z","timestamp":1790112406581,"version":"4.0.1"},"reference-count":102,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2019,2,1]],"date-time":"2019-02-01T00:00:00Z","timestamp":1548979200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2019,2,1]],"date-time":"2019-02-01T00:00:00Z","timestamp":1548979200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","nmd-journal.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Neuromuscular Disorders"],"published-print":{"date-parts":[[2019,2]]},"DOI":"10.1016\/j.nmd.2018.12.005","type":"journal-article","created":{"date-parts":[[2018,12,17]],"date-time":"2018-12-17T22:09:41Z","timestamp":1545084581000},"page":"85-96","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":32,"title":["The clinical management of neuromuscular disorders in intensive care"],"prefix":"10.1016","volume":"29","author":[{"given":"Maxwell S.","family":"Damian","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eelco F.M.","family":"Wijdicks","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"8","key":"10.1016\/j.nmd.2018.12.005_bib0001","doi-asserted-by":"crossref","first-page":"1405","DOI":"10.1007\/s00134-013-2960-6","volume":"39","author":"Damian","year":"2013","journal-title":"Intensive Care Med"},{"key":"10.1016\/j.nmd.2018.12.005_bib0002","doi-asserted-by":"crossref","first-page":"489","DOI":"10.1002\/ana.24908","article-title":"The neurology of acutely failing respiratory mechanics","volume":"81","author":"Wijdicks","year":"2017","journal-title":"Ann Neurol"},{"issue":"2","key":"10.1016\/j.nmd.2018.12.005_bib0003","first-page":"94","article-title":"The value of cough peak flow measurements in the assessment of extubation or decannulation readiness","volume":"21","author":"Winck","year":"2006","journal-title":"Rev Port Pneumol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0004","doi-asserted-by":"crossref","unstructured":"Lawn ND, Fletcher DD, Henderson RD, Wolter TD, Wijdicks EF. Anticipating mechanical ventilation in Guillain\u2013Barr\u00e9 syndrome. Arch Neurol. 200;58(6):893\u20138.","DOI":"10.1001\/archneur.58.6.893"},{"issue":"8","key":"10.1016\/j.nmd.2018.12.005_bib0005","doi-asserted-by":"crossref","first-page":"1058","DOI":"10.1002\/(SICI)1097-4598(199908)22:8<1058::AID-MUS8>3.0.CO;2-G","article-title":"Tracheostomy in Guillain\u2013Barr\u00e9 syndrome","volume":"22","author":"Lawn","year":"1999","journal-title":"Muscle Nerve"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0006","doi-asserted-by":"crossref","first-page":"68","DOI":"10.4187\/respcare.03507","article-title":"Neurally adjusted ventilatory assist during weaning from respiratory support in a case of Guillain\u2013Barr\u00e9 syndrome","volume":"60","author":"Dugernier","year":"2015","journal-title":"Respir Care"},{"issue":"8","key":"10.1016\/j.nmd.2018.12.005_bib0007","doi-asserted-by":"crossref","first-page":"1194","DOI":"10.1001\/archneur.62.8.1194","article-title":"Multidisciplinary consensus group. Supportive care for patients with Guillain\u2013Barr\u00e9 syndrome","volume":"62","author":"Hughes","year":"2005","journal-title":"Arch Neurol"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0008","doi-asserted-by":"crossref","first-page":"597","DOI":"10.1002\/ana.21737","article-title":"Pharmacokinetics of intravenous immunoglobulin and outcome in Guillain\u2013Barr\u00e9 syndrome","volume":"66","author":"Kuitwaard","year":"2009","journal-title":"Ann Neurol"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0009","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1097\/CND.0000000000000119","article-title":"Human immunoglobulin versus plasmapheresis in Guillain\u2013Barre syndrome and myasthenia gravis: a meta-analysis","volume":"18","author":"Ortiz-Salas","year":"2016","journal-title":"J Clin Neuromuscul Dis"},{"issue":"11","key":"10.1016\/j.nmd.2018.12.005_bib0010","doi-asserted-by":"crossref","first-page":"1015","DOI":"10.1007\/s004150050506","article-title":"Indicators of dysautonomia in severe Guillain\u2013Barr\u00e9 syndrome","volume":"246","author":"Pfeiffer","year":"1999","journal-title":"J Neurol"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0011","doi-asserted-by":"crossref","first-page":"356","DOI":"10.1111\/j.1529-8027.2012.00416.x","article-title":"Posterior reversible encephalopathy syndrome as the initial manifestation of Guillain\u2013Barr\u00e9 syndrome: case report and review of the literature","volume":"17","author":"Rigamonti","year":"2012","journal-title":"J Peripher Nerv Syst"},{"issue":"1\u20132","key":"10.1016\/j.nmd.2018.12.005_bib0012","doi-asserted-by":"crossref","first-page":"100","DOI":"10.1016\/j.jns.2010.01.005","article-title":"Takotsubo cardiomyopathy associated with Guillain\u2013Barr\u00e9 syndrome: a differential diagnosis from dysautonomia not to be missed","volume":"291","author":"Martins","year":"2010","journal-title":"J Neurol Sci"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0013","doi-asserted-by":"crossref","first-page":"230","DOI":"10.1385\/NCC:5:3:230","article-title":"Factors predicting extubation success in patients with Guillain\u2013Barr\u00e9 syndrome","volume":"5","author":"Nguyen","year":"2006","journal-title":"Neurocrit Care"},{"issue":"12","key":"10.1016\/j.nmd.2018.12.005_bib0014","doi-asserted-by":"crossref","first-page":"2311","DOI":"10.1212\/WNL.54.12.2311","article-title":"Long-term outcome in patients with Guillain\u2013Barr\u00e9 syndrome requiring mechanical ventilation","volume":"54","author":"Fletcher","year":"2007","journal-title":"Neurology"},{"issue":"18","key":"10.1016\/j.nmd.2018.12.005_bib0015","doi-asserted-by":"crossref","first-page":"1548","DOI":"10.1212\/WNL.0b013e3181a41211","article-title":"Incidence and mortality rates of myasthenia gravis and myasthenic crisis in US hospitals","volume":"72","author":"Alshekhlee","year":"2009","journal-title":"Neurology"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0016","doi-asserted-by":"crossref","first-page":"280","DOI":"10.1159\/000063636","article-title":"Respiratory failure due to vocal cord paresis in myasthenia gravis","volume":"69","author":"Teramoto","year":"2002","journal-title":"Respiration"},{"issue":"2","key":"10.1016\/j.nmd.2018.12.005_bib0017","doi-asserted-by":"crossref","first-page":"145","DOI":"10.1007\/BF00582150","article-title":"Corticosteroids and neuromuscular transmission: electrophysiological investigation of the effects of prednisolone on normal and anticholinesterase-treated neuromuscular junction","volume":"380","author":"Dengler","year":"1979","journal-title":"Pflugers Arch"},{"key":"10.1016\/j.nmd.2018.12.005_bib0018","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1016\/j.atherosclerosissup.2017.05.016","article-title":"Therapeutic plasma exchange in a rare case of myasthenic crisis after Botox injection","volume":"30","author":"Chegini","year":"2017","journal-title":"Atheroscler Suppl"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0019","doi-asserted-by":"crossref","first-page":"511","DOI":"10.1056\/NEJMoa1602489","article-title":"Randomized trial of thymectomy in myasthenia gravis","volume":"375","author":"Wolfe","year":"2016","journal-title":"N Engl J Med"},{"issue":"10","key":"10.1016\/j.nmd.2018.12.005_bib0020","doi-asserted-by":"crossref","first-page":"2377","DOI":"10.1113\/jphysiol.2013.254599","article-title":"Why does acetylcholine exacerbate myasthenia caused by anti-MuSK antibodies?","volume":"591","author":"Engel","year":"2013","journal-title":"J Physiol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0021","article-title":"Three types of striational antibodies in myasthenia gravis","volume":"2011","author":"Suzuki","year":"2011","journal-title":"Autoimmune Dis"},{"key":"10.1016\/j.nmd.2018.12.005_bib0022","doi-asserted-by":"crossref","first-page":"393","DOI":"10.1186\/1752-1947-4-393","article-title":"Emotional stress as a trigger of myasthenic crisis and concomitant takotsubo cardiomyopathy: a case report","volume":"4","author":"Beydoun","year":"2010","journal-title":"J Med Case Rep"},{"key":"10.1016\/j.nmd.2018.12.005_bib0023","doi-asserted-by":"crossref","first-page":"616","DOI":"10.1016\/j.ijcard.2015.11.005","article-title":"Stress from myasthenic crisis triggers Takotsubo (broken heart) syndrome","volume":"203","author":"Finsterer","year":"2016","journal-title":"Int J Cardiol"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0024","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1001\/archneurol.2007.1","article-title":"Noninvasive ventilation in myasthenic crisis","volume":"65","author":"Seneviratne","year":"2008","journal-title":"Arch Neurol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0025","doi-asserted-by":"crossref","first-page":"929","DOI":"10.1001\/archneur.65.7.929","article-title":"Predictors of extubation failure in myasthenic crisis","volume":"65","author":"Seneviratne","year":"2008","journal-title":"Arch Neurol"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0026","doi-asserted-by":"crossref","first-page":"1607","DOI":"10.1212\/WNL.46.6.1607","article-title":"Risk of cancer from azathioprine therapy in multiple sclerosis: a case-control study","volume":"46","author":"Confavreux","year":"1996","journal-title":"Neurology"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0027","doi-asserted-by":"crossref","first-page":"325","DOI":"10.1136\/ard.2002.005371","article-title":"Does long term treatment with azathioprine predispose to malignancy and death in patients with systemic lupus erythematosus?","volume":"63","author":"Nero","year":"2004","journal-title":"Ann Rheum Dis"},{"issue":"10","key":"10.1016\/j.nmd.2018.12.005_bib0028","doi-asserted-by":"crossref","first-page":"1316","DOI":"10.1212\/WNL.33.10.1316","article-title":"Myasthenia gravis: long-term correlation of binding and bungarotoxin blocking antibodies against acetylcholine receptors with changes in disease severity","volume":"33","author":"Besinger","year":"1983","journal-title":"Neurology"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0029","doi-asserted-by":"crossref","first-page":"1553","DOI":"10.1002\/mus.21185","article-title":"Construction of an efficient evaluative instrument for myasthenia gravis: the MG composite","volume":"38","author":"Burns","year":"2008","journal-title":"Muscle Nerve"},{"issue":"7","key":"10.1016\/j.nmd.2018.12.005_bib0030","doi-asserted-by":"crossref","first-page":"344","DOI":"10.1056\/NEJM197502132920706","article-title":"Polymyositis and dermatomyositis","volume":"292","author":"Bohan","year":"1975","journal-title":"N Engl J Med"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0031","doi-asserted-by":"crossref","first-page":"337","DOI":"10.1016\/j.nmd.2004.02.006","article-title":"119th ENMC international workshop: trial design in adult idiopathic inflammatory myopathies, with the exception of inclusion body myositis, 10\u201312 October 2003, Naarden, The Netherlands","volume":"14","author":"Hoogendijk","year":"2004","journal-title":"Neuromuscul Disord"},{"issue":"12","key":"10.1016\/j.nmd.2018.12.005_bib0032","doi-asserted-by":"crossref","first-page":"464","DOI":"10.1007\/s11926-014-0464-1","article-title":"Myositis specific and associated autoantibodies in the diagnosis and management of juvenile and adult idiopathic inflammatory myopathies","volume":"16","author":"Tansley","year":"2014","journal-title":"Curr Rheumatol Rep"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0033","doi-asserted-by":"crossref","first-page":"552","DOI":"10.1016\/j.semarthrit.2017.06.004","article-title":"Inflammatory myopathy associated with anti-mitochondrial antibodies: a distinct phenotype with cardiac involvement","volume":"47","author":"Albayda","year":"2018","journal-title":"Semin Arthritis Rheum"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0034","doi-asserted-by":"crossref","first-page":"382","DOI":"10.1016\/j.nmd.2010.03.011","article-title":"Oral dexamethasone pulse therapy versus daily prednisolone in sub-acute onset myositis, a randomised clinical trial","volume":"20","author":"van de Vlekkert","year":"2010","journal-title":"Neuromuscul Disord"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0035","doi-asserted-by":"crossref","first-page":"554","DOI":"10.1097\/WCO.0b013e328364e9d9","article-title":"Acquired necrotizing myopathies","volume":"26","author":"Allenbach","year":"2013","journal-title":"Curr Opin Neurol"},{"issue":"10","key":"10.1016\/j.nmd.2018.12.005_bib0036","doi-asserted-by":"crossref","first-page":"1038","DOI":"10.1136\/jnnp-2016-313166","article-title":"Clinical features and prognosis in anti-SRP and anti-HMGCR necrotising myopathy","volume":"87","author":"Watanabe","year":"2016","journal-title":"J Neurol Neurosurg Psychiatry"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0037","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1016\/j.nmd.2017.09.016","article-title":"Immune-mediated necrotizing myopathies working group. 224th ENMC international workshop: Clinico-sero-pathological classification of immune-mediated necrotizing myopathies Zandvoort, The Netherlands, 14\u201316 October 2016","volume":"28","author":"Allenbach","year":"2018","journal-title":"Neuromuscul Disord"},{"key":"10.1016\/j.nmd.2018.12.005_bib0038","doi-asserted-by":"crossref","first-page":"93","DOI":"10.1186\/s13023-015-0310-1","article-title":"Malignant hyperthermia; a review","volume":"10","author":"Rosenberg","year":"2015","journal-title":"Orphanet J Rare Dis"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0039","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1007\/s12028-013-9914-2","article-title":"Serotonin syndrome in the intensive care unit: clinical presentations and precipitating medications","volume":"21","author":"Pedavally","year":"2014","journal-title":"Neurocrit Care"},{"key":"10.1016\/j.nmd.2018.12.005_bib0040","doi-asserted-by":"crossref","first-page":"51","DOI":"10.1186\/s13023-015-0264-3","article-title":"Rhabdomyolysis: a genetic perspective","volume":"10","author":"Scalco","year":"2015","journal-title":"Orphanet J Rare Dis"},{"issue":"8","key":"10.1016\/j.nmd.2018.12.005_bib0041","doi-asserted-by":"crossref","first-page":"651","DOI":"10.1016\/j.nmd.2014.05.005","article-title":"Rhabdomyolysis: review of the literature","volume":"24","author":"Zutt","year":"2014","journal-title":"Neuromuscul Disord"},{"issue":"12","key":"10.1016\/j.nmd.2018.12.005_bib0042","doi-asserted-by":"crossref","first-page":"2273","DOI":"10.1007\/s00467-017-3755-8","article-title":"Exome sequencing in Jewish and Arab patients with rhabdomyolysis reveals single-gene etiology in 43% of cases","volume":"32","author":"Vivante","year":"2017","journal-title":"Pediatr Nephrol"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0043","first-page":"35","article-title":"Muscle glycogenoses: an overview","volume":"26","author":"Di Mauro","year":"2007","journal-title":"Acta Myol"},{"issue":"10","key":"10.1016\/j.nmd.2018.12.005_bib0044","doi-asserted-by":"crossref","first-page":"546","DOI":"10.1016\/j.neurol.2016.07.018","article-title":"RYR1-related rhabdomyolysis: a common but probably underdiagnosed manifestation of skeletal muscle ryanodine receptor dysfunction","volume":"172","author":"Voermans","year":"2016","journal-title":"Rev Neurol (Paris)"},{"issue":"2","key":"10.1016\/j.nmd.2018.12.005_bib0045","doi-asserted-by":"crossref","first-page":"417","DOI":"10.1111\/ene.13528","article-title":"Rhabdomyolysis and fluctuating asymptomatic hyperCKemia associated with CACNA1S variant","volume":"25","author":"Anandan","year":"2017","journal-title":"Eur J Neurol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0046","doi-asserted-by":"crossref","first-page":"8","DOI":"10.1186\/s13023-016-0390-6","article-title":"Diagnosis of late-onset Pompe disease and other muscle disorders by next-generation sequencing","volume":"11","author":"L\u00e9vesque","year":"2016","journal-title":"Orphanet J Rare Dis"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0047","doi-asserted-by":"crossref","first-page":"806","DOI":"10.1097\/WCO.0000000000000391","article-title":"Neurologic complications of immune checkpoint inhibitors","volume":"29","author":"Hottinger","year":"2016","journal-title":"Curr Opin Neurol"},{"issue":"12","key":"10.1016\/j.nmd.2018.12.005_bib0048","first-page":"718","article-title":"Critical illness myopathy. Neurophysiological and muscular biopsy assessment in 33 patients","volume":"50","author":"Fern\u00e1ndez-Lorente","year":"2010","journal-title":"Rev Neurol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0049","doi-asserted-by":"crossref","first-page":"274","DOI":"10.1186\/s13054-015-0993-7","article-title":"Clinical review: intensive care unit acquired weakness","volume":"19","author":"Hermans","year":"2015","journal-title":"Crit Care"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0050","doi-asserted-by":"crossref","first-page":"R233","DOI":"10.1186\/cc10475","article-title":"Plasma from septic shock patients induces loss of muscle protein","volume":"15","author":"van Hees","year":"2011","journal-title":"Crit Care"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0051","doi-asserted-by":"crossref","first-page":"480","DOI":"10.1164\/rccm.200605-665OC","article-title":"Impact of intensive insulin therapy on neuromuscular complications and ventilator dependency in the medical intensive care unit","volume":"175","author":"Hermans","year":"2007","journal-title":"Am J Resp Crit Care Med"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0052","doi-asserted-by":"crossref","first-page":"972","DOI":"10.1097\/CCM.0000000000002408","article-title":"Increased early systemic inflammation in ICU-acquired weakness; a prospective observational cohort study","volume":"45","author":"Witteveen","year":"2017","journal-title":"Crit Care Med"},{"issue":"9","key":"10.1016\/j.nmd.2018.12.005_bib0053","doi-asserted-by":"crossref","first-page":"1270","DOI":"10.1007\/s00134-017-4757-5","article-title":"The ICM research agenda on intensive care unit-acquired weakness","volume":"43","author":"Latronico","year":"2017","journal-title":"Int Care Med"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0054","doi-asserted-by":"crossref","first-page":"44","DOI":"10.7196\/SAMJ.2016.v106i1.10118","article-title":"Severe porphyric neuropathy \u2013 importance of screening for porphyria in Guillain\u2013Barr\u00e9 syndrome","volume":"106","author":"Schutte","year":"2015","journal-title":"S Afr Med J"},{"key":"10.1016\/j.nmd.2018.12.005_bib0055","doi-asserted-by":"crossref","first-page":"e10","DOI":"10.1111\/j.1468-1331.2007.01946.x","article-title":"Charcot\u2013Marie\u2013Tooth disease type 1A associated with acute porphyric neuropathy","volume":"14","author":"Jacob","year":"2007","journal-title":"Eur J Neurol"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0056","doi-asserted-by":"crossref","first-page":"435","DOI":"10.1016\/S1474-4422(14)70221-2","article-title":"End-of-life management in patients with amyotrophic lateral sclerosis","volume":"14","author":"Connolly","year":"2015","journal-title":"Lancet Neurol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0057","doi-asserted-by":"crossref","first-page":"205","DOI":"10.2147\/JMDH.S134992","article-title":"Amyotrophic lateral sclerosis: improving care with a multidisciplinary approach","volume":"10","author":"Hogden","year":"2017","journal-title":"J Multidiscip Healthc"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0058","doi-asserted-by":"crossref","DOI":"10.1002\/14651858.CD004427.pub2","article-title":"Mechanical ventilation for amyotrophic lateral sclerosis\/motor neuron disease","author":"Radunovic","year":"2009","journal-title":"Cochrane Database Syst Rev"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0059","doi-asserted-by":"crossref","DOI":"10.1371\/journal.pone.0177555","article-title":"Is survival improved by the use of NIV and PEG in amyotrophic lateral sclerosis (ALS)? A post-mortem study of 80 ALS patients","volume":"12","author":"Burkhardt","year":"2017","journal-title":"PLoS One"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0060","doi-asserted-by":"crossref","first-page":"241","DOI":"10.5692\/clinicalneurol.cn-000837","article-title":"Tracheostomy and invasive mechanical ventilation in amyotrophic lateral sclerosis: decision-making factors and survival analysis","volume":"56","author":"Kimura","year":"2016","journal-title":"Rinsho Shinkeigaku"},{"issue":"1\u20132","key":"10.1016\/j.nmd.2018.12.005_bib0061","doi-asserted-by":"crossref","first-page":"66","DOI":"10.1016\/j.jns.2012.08.011","article-title":"Tracheostomy mechanical ventilation in patients with amyotrophic lateral sclerosis: clinical features and survival analysis","volume":"323","author":"Spataro","year":"2012","journal-title":"J Neurol Sci"},{"key":"10.1016\/j.nmd.2018.12.005_bib0062","doi-asserted-by":"crossref","first-page":"w13830","DOI":"10.4414\/smw.2013.13830","article-title":"Is tracheostomy still an option in amyotrophic lateral sclerosis? Reflections of a multidisciplinary work group","volume":"143","author":"Heritier Barras","year":"2013","journal-title":"Swiss Med Wkly"},{"issue":"15","key":"10.1016\/j.nmd.2018.12.005_bib0063","doi-asserted-by":"crossref","first-page":"1218","DOI":"10.1212\/WNL.0b013e3181bc0141","article-title":"Practice parameter update: the care of the patient with amyotrophic lateral sclerosis: drug, nutritional, and respiratory therapies (an evidence-based review): report of the Quality Standards Subcommittee of the American Academy of Neurology","volume":"73","author":"Miller","year":"2009","journal-title":"Neurology"},{"key":"10.1016\/j.nmd.2018.12.005_bib0064","unstructured":"Motor neurone disease: Assessment and management. NICE guideline Published online 24 February 2016 http:\/\/www.nice.org.uk\/guidance\/ng42"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0065","doi-asserted-by":"crossref","first-page":"300","DOI":"10.1016\/j.neurol.2017.03.032","article-title":"Ethical considerations and palliative care in patients with amyotrophic lateral sclerosis: a review","volume":"173","author":"Danel-Brunaud","year":"2017","journal-title":"Rev Neurol (Paris)"},{"key":"10.1016\/j.nmd.2018.12.005_bib0066","doi-asserted-by":"crossref","first-page":"289","DOI":"10.1016\/j.jns.2017.02.012","article-title":"Takotsubo cardiomyopathy in amyotrophic lateral sclerosis","volume":"375","author":"Choi","year":"2017","journal-title":"J Neurol Sci"},{"key":"10.1016\/j.nmd.2018.12.005_bib0067","doi-asserted-by":"crossref","first-page":"339","DOI":"10.1016\/j.jns.2017.05.017","article-title":"Takotsubo in amyotrophic lateral sclerosis","volume":"379","author":"Finsterer","year":"2017","journal-title":"J Neurol Sci"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0068","doi-asserted-by":"crossref","first-page":"753","DOI":"10.1212\/01.WNL.0000151978.74467.E7","article-title":"Laryngospasm: an underdiagnosed symptom of X-linked spinobulbar muscular atrophy","volume":"64","author":"Sperfeld","year":"2005","journal-title":"Neurology"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0069","doi-asserted-by":"crossref","first-page":"566","DOI":"10.1016\/j.nmd.2011.12.004","article-title":"186th ENMC international workshop: congenital myasthenic syndromes 24\u201326 June 2011, Naarden, The Netherlands","volume":"22","author":"Chaouch","year":"2012","journal-title":"Neuromuscul Disord"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0070","doi-asserted-by":"crossref","first-page":"363","DOI":"10.1177\/0883073812436605","article-title":"Consensus statement on standard of care for congenital myopathies","volume":"27","author":"Wang","year":"2012","journal-title":"J Child Neurol"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0071","doi-asserted-by":"crossref","first-page":"727","DOI":"10.1007\/s00109-013-0994-4","article-title":"Neuromuscular junction abnormalities in DNM2-related centronuclear myopathy","volume":"91","author":"Gibbs","year":"2013","journal-title":"J Mol Med"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0072","doi-asserted-by":"crossref","first-page":"881","DOI":"10.1002\/mus.25602","article-title":"Hereditary myopathies with early respiratory insufficiency in adults","volume":"56","author":"Naddaf","year":"2017","journal-title":"Muscle Nerve"},{"issue":"15","key":"10.1016\/j.nmd.2018.12.005_bib0073","doi-asserted-by":"crossref","first-page":"1396","DOI":"10.1056\/NEJMoa0909859","article-title":"A randomised study of alglucosidase alfa in late onset Pompe's disease","volume":"362","author":"van der Ploeg","year":"2010","journal-title":"New Eng J Med"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0074","doi-asserted-by":"crossref","first-page":"621","DOI":"10.1007\/s00415-016-8219-8","article-title":"Survival and long-term outcomes in late-onset Pompe disease following algucosidase alpha treatment: a systematic review and meta-analysis","volume":"264","author":"Schoser","year":"2017","journal-title":"J Neurol"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0075","first-page":"345","article-title":"Hereditary myopathy with early respiratory failure: occurrence in various populations","volume":"85","author":"Palmio","year":"2014","journal-title":"JNNP"},{"issue":"Pt 6","key":"10.1016\/j.nmd.2018.12.005_bib0076","doi-asserted-by":"crossref","first-page":"1695","DOI":"10.1093\/brain\/aws102","article-title":"Titin mutation segregates with hereditary myopathy with early respiratory failure","volume":"135","author":"Pfeffer","year":"2012","journal-title":"Brain"},{"key":"10.1016\/j.nmd.2018.12.005_bib0077","doi-asserted-by":"crossref","first-page":"279","DOI":"10.1093\/brain\/awu033","article-title":"Hereditary myopathy with early respiratory failure is caused by mutations in the Titin FN3 119 domain","volume":"137","author":"Lange","year":"2014","journal-title":"Brain"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0078","doi-asserted-by":"crossref","first-page":"161","DOI":"10.1016\/j.nmd.2010.12.007","article-title":"Myofibrillar myopathies","volume":"21","author":"Selcen","year":"2011","journal-title":"Neuromuscul Disord"},{"issue":"12","key":"10.1016\/j.nmd.2018.12.005_bib0079","doi-asserted-by":"crossref","first-page":"1936","DOI":"10.1212\/01.wnl.0000188872.28149.9a","article-title":"A mutation in myotilin causes spheroid body myopathy","volume":"65","author":"Foroud","year":"2005","journal-title":"Neurology"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0080","doi-asserted-by":"crossref","first-page":"268","DOI":"10.1016\/j.nmd.2017.12.002","article-title":"Hereditary myopathy with early respiratory failure (HMERF): still rare, but common enough","volume":"28","author":"Tasca","year":"2018","journal-title":"Neuromuscul Disord"},{"key":"10.1016\/j.nmd.2018.12.005_bib0100","doi-asserted-by":"crossref","first-page":"1363","DOI":"10.1212\/01.WNL.0000123576.74801.75","article-title":"Mutations in myotilin cause myofibrillar myopathy","volume":"62","author":"Selcen","year":"2004","journal-title":"Neurology"},{"issue":"8","key":"10.1016\/j.nmd.2018.12.005_bib0101","doi-asserted-by":"crossref","first-page":"533","DOI":"10.1016\/j.nmd.2011.05.002","article-title":"Clinical and myopathological evaluation of early- and late-onset subtypes of myofibrillar myopathy","volume":"21","author":"Oliv\u00e9","year":"2011","journal-title":"Neuromuscul Disord"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0102","doi-asserted-by":"crossref","first-page":"909","DOI":"10.1002\/mus.24233","article-title":"Cardiac involvement in Dutch patients with sarcoglycanopathy: a cross-sectional cohort and follow-up study","volume":"50","author":"Schade van Westrum","year":"2014","journal-title":"Muscle Nerve"},{"issue":"8","key":"10.1016\/j.nmd.2018.12.005_bib0103","doi-asserted-by":"crossref","first-page":"650","DOI":"10.1016\/j.nmd.2008.06.365","article-title":"Cardiac assessment of limb-girdle muscular dystrophy 2I patients: an echography, Holter ECG and magnetic resonance imaging study","volume":"18","author":"Wahbi","year":"2008","journal-title":"Neuromuscul Disord"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0104","doi-asserted-by":"crossref","first-page":"e1187","DOI":"10.1542\/peds.2005-2469","article-title":"Cardiac involvement in Fukuyama-type congenital muscular dystrophy","volume":"117","author":"Nakanishi","year":"2006","journal-title":"Pediatrics"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0081","doi-asserted-by":"crossref","first-page":"457","DOI":"10.1097\/WCO.0000000000000477","article-title":"Sporadic late onset nemaline myopathy with monoclonal gammopathy of undetermined significance","volume":"30","author":"Uruha","year":"2017","journal-title":"Curr Opin Neurol"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0082","doi-asserted-by":"crossref","first-page":"86","DOI":"10.1186\/s13023-017-0640-2","article-title":"Sporadic late onset Nemaline myopathy: clinicopathological characteristics and review of 76 cases","volume":"12","author":"Schnitzler","year":"2017","journal-title":"Orphanet J Rare Dis"},{"issue":"10","key":"10.1016\/j.nmd.2018.12.005_bib0083","doi-asserted-by":"crossref","first-page":"1939","DOI":"10.1212\/01.WNL.0000144343.91136.CF","article-title":"Severe cardiac arrhythmias in young patients with myotonic dystrophy type 1","volume":"63","author":"Bassez","year":"2004","journal-title":"Neurol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0084","doi-asserted-by":"crossref","first-page":"508","DOI":"10.1016\/j.ijcard.2015.10.176","article-title":"Sudden cardiac death in neuromuscular disorders","volume":"203","author":"Finsterer","year":"2016","journal-title":"Int J Cardiol"},{"issue":"1","key":"10.1016\/j.nmd.2018.12.005_bib0085","doi-asserted-by":"crossref","first-page":"22","DOI":"10.15420\/aer.2012.1.22","article-title":"What should the cardiologist know about Lamin disease?","volume":"1","author":"Charron","year":"2012","journal-title":"Arrhythm Electrophysiol Rev"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0086","first-page":"260","article-title":"Treatment of metabolic acidosis","volume":"9","author":"Levraut","year":"2003","journal-title":"Curr Opin Crit Care"},{"issue":"5","key":"10.1016\/j.nmd.2018.12.005_bib0087","doi-asserted-by":"crossref","first-page":"1791","DOI":"10.1002\/hep.23891","article-title":"Polymerase \u03b3 gene POLG determines the risk of sodium valproate-induced liver toxicity","volume":"52","author":"Stewart","year":"2010","journal-title":"Hepatology"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0088","doi-asserted-by":"crossref","first-page":"346","DOI":"10.1034\/j.1600-0676.2000.020004346.x","article-title":"Mitochondrial diseases represent a risk factor for valproate-induced fulminant liver failure","volume":"20","author":"Kr\u00e4henb\u00fchl","year":"2000","journal-title":"Liver"},{"issue":"6","key":"10.1016\/j.nmd.2018.12.005_bib0089","doi-asserted-by":"crossref","first-page":"992","DOI":"10.1016\/j.mito.2011.08.010","article-title":"Rapid-onset, linezolid-induced lactic acidosis in MELAS","volume":"11","author":"McFarland","year":"2011","journal-title":"Mitochondrion"},{"issue":"13","key":"10.1016\/j.nmd.2018.12.005_bib0090","doi-asserted-by":"crossref","first-page":"1489","DOI":"10.1177\/0883073816661458","article-title":"Propofol is mitochondrion-toxic and may unmask a mitochondrial disorder","volume":"31","author":"Finsterer","year":"2016","journal-title":"J Child Neurol"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0091","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1007\/s10545-014-9796-2","article-title":"Treatment options for lactic acidosis and metabolic crisis in children with mitochondrial disease","volume":"38","author":"Danhauser","year":"2015","journal-title":"J Inherit Metab Dis"},{"issue":"2","key":"10.1016\/j.nmd.2018.12.005_bib0092","doi-asserted-by":"crossref","first-page":"177","DOI":"10.1016\/S1474-4422(09)70272-8","article-title":"DMD care considerations working group. Diagnosis and management of Duchenne muscular dystrophy, part 2: implementation of multidisciplinary care","volume":"9","author":"Bushby","year":"2010","journal-title":"Lancet Neurol"},{"key":"10.1016\/j.nmd.2018.12.005_bib0093","doi-asserted-by":"crossref","first-page":"66","DOI":"10.1186\/1743-0003-10-66","article-title":"MUNDUS project: MUltimodal neuroprosthesis for daily upper limb support","volume":"10","author":"Pedrocchi","year":"2013","journal-title":"J Neuroeng Rehabil"},{"key":"10.1016\/j.nmd.2018.12.005_bib0094","first-page":"1007","article-title":"BRIDGE \u2013 behavioural reaching interfaces during daily antigravity activities through upper limb exoskeleton: preliminary results","author":"Gandolla","year":"2017","journal-title":"IEEE Int Conf Rehabil Robot"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0095","doi-asserted-by":"crossref","first-page":"432","DOI":"10.1016\/j.healun.2009.08.030","article-title":"Clinical outcomes after cardiac transplantation in muscular dystrophy patients","volume":"29","author":"Wu","year":"2010","journal-title":"J Heart Lung Transpl"},{"issue":"3","key":"10.1016\/j.nmd.2018.12.005_bib0096","doi-asserted-by":"crossref","first-page":"379","DOI":"10.1002\/ehf2.12160","article-title":"Implantation of a left ventricular assist device to provide long-term support for end-stage Duchenne muscular dystrophy-associated cardiomyopathy","volume":"4","author":"Stoller","year":"2017","journal-title":"ESC Heart Fail"},{"issue":"4","key":"10.1016\/j.nmd.2018.12.005_bib0097","doi-asserted-by":"crossref","first-page":"1043","DOI":"10.1213\/ane.0b013e3181aa5cf6","article-title":"Malignant hyperthermia and muscular dystrophies","volume":"109","author":"Gurnaney","year":"2009","journal-title":"Anesth Analg"}],"container-title":["Neuromuscular Disorders"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0960896618304231?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0960896618304231?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,18]],"date-time":"2025-10-18T08:08:11Z","timestamp":1760774891000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0960896618304231"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,2]]},"references-count":102,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2019,2]]}},"alternative-id":["S0960896618304231"],"URL":"https:\/\/doi.org\/10.1016\/j.nmd.2018.12.005","relation":{},"ISSN":["0960-8966"],"issn-type":[{"value":"0960-8966","type":"print"}],"subject":[],"published":{"date-parts":[[2019,2]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"The clinical management of neuromuscular disorders in intensive care","name":"articletitle","label":"Article Title"},{"value":"Neuromuscular Disorders","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.nmd.2018.12.005","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2018 Elsevier B.V. All rights reserved.","name":"copyright","label":"Copyright"}]}}