{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,24]],"date-time":"2026-08-24T14:42:10Z","timestamp":1787582530995,"version":"build-2736575974"},"reference-count":77,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-017"},{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-037"},{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-012"},{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-029"},{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-004"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","surgpath.theclinics.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Surgical Pathology Clinics"],"published-print":{"date-parts":[[2026,3]]},"DOI":"10.1016\/j.path.2025.09.003","type":"journal-article","created":{"date-parts":[[2025,10,25]],"date-time":"2025-10-25T03:39:02Z","timestamp":1761363542000},"page":"163-174","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":1,"title":["Beyond Sweet Syndrome"],"prefix":"10.1016","volume":"19","author":[{"given":"Alexandra C.","family":"Hristov","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.path.2025.09.003_bib1","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1111\/j.1365-2133.1964.tb14541.x","article-title":"An acute febrile neutrophilic dermatosis","volume":"76","author":"Sweet","year":"1964","journal-title":"Br J Dermatol"},{"key":"10.1016\/j.path.2025.09.003_bib2","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1186\/1750-1172-2-34","article-title":"Sweet\u2019s syndrome--a comprehensive review of an acute febrile neutrophilic dermatosis","volume":"2","author":"Cohen","year":"2007","journal-title":"Orphanet J Rare Dis"},{"issue":"7","key":"10.1016\/j.path.2025.09.003_bib3","doi-asserted-by":"crossref","first-page":"834","DOI":"10.1001\/archderm.141.7.834","article-title":"Histiocytoid Sweet syndrome: a dermal infiltration of immature neutrophilic granulocytes","volume":"141","author":"Requena","year":"2005","journal-title":"Arch Dermatol"},{"issue":"2","key":"10.1016\/j.path.2025.09.003_bib4","doi-asserted-by":"crossref","first-page":"220","DOI":"10.1111\/j.1600-0560.2007.00780.x","article-title":"Drug-associated histiocytoid Sweet\u2019s syndrome: a true neutrophilic maturation arrest variant","volume":"35","author":"Wu","year":"2008","journal-title":"J Cutan Pathol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib5","doi-asserted-by":"crossref","first-page":"334","DOI":"10.1097\/DAD.0b013e31811ec968","article-title":"Histiocytoid neutrophilic dermatoses and panniculitides: variations on a theme","volume":"29","author":"Chow","year":"2007","journal-title":"Am J Dermatopath"},{"issue":"11","key":"10.1016\/j.path.2025.09.003_bib6","doi-asserted-by":"crossref","first-page":"1495","DOI":"10.1001\/archderm.144.11.1495","article-title":"Two pediatric cases of nonbullous histiocytoid neutrophilic dermatitis presenting as a cutaneous manifestation of lupus erythematosus","volume":"144","author":"Camarillo","year":"2008","journal-title":"Arch Dermatol"},{"issue":"3","key":"10.1016\/j.path.2025.09.003_bib7","doi-asserted-by":"crossref","first-page":"496","DOI":"10.1016\/j.jaad.2008.09.007","article-title":"Bortezomib-induced histiocytoid Sweet syndrome","volume":"60","author":"Murase","year":"2009","journal-title":"J Am Acad Dermatol"},{"issue":"2 Suppl 1","key":"10.1016\/j.path.2025.09.003_bib8","doi-asserted-by":"crossref","first-page":"S58","DOI":"10.1016\/j.jaad.2008.03.044","article-title":"Dapsone-responsive histiocytoid Sweet\u2019s syndrome associated with Crohn\u2019s disease","volume":"59","author":"Spencer","year":"2008","journal-title":"J Am Acad Dermatol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib9","doi-asserted-by":"crossref","first-page":"334","DOI":"10.1097\/DAD.0b013e31811ec968","article-title":"Histiocytoid neutrophilic dermatoses and panniculitides: variations on a theme","volume":"29","author":"Chow","year":"2007","journal-title":"Am J Dermatopathol"},{"issue":"5","key":"10.1016\/j.path.2025.09.003_bib10","doi-asserted-by":"crossref","first-page":"562","DOI":"10.1111\/j.1365-2230.2010.04002.x","article-title":"Histiocytoid Sweet syndrome","volume":"36","author":"Apalla","year":"2011","journal-title":"Clin Exp Dermatol"},{"issue":"12","key":"10.1016\/j.path.2025.09.003_bib11","doi-asserted-by":"crossref","first-page":"1491","DOI":"10.1111\/j.1365-4632.2011.05141.x","article-title":"Distinct variant of Sweet\u2019s syndrome: bortezomib-induced histiocytoid Sweet\u2019s syndrome in a patient with multiple myeloma","volume":"51","author":"Kim","year":"2012","journal-title":"Int J Dermatol"},{"issue":"1","key":"10.1016\/j.path.2025.09.003_bib12","doi-asserted-by":"crossref","first-page":"131","DOI":"10.1016\/j.jaad.2014.09.025","article-title":"Histiocytoid Sweet syndrome is infiltrated predominantly by M2-like macrophages","volume":"72","author":"Peroni","year":"2015","journal-title":"J Am Acad Dermatol"},{"issue":"3","key":"10.1016\/j.path.2025.09.003_bib13","doi-asserted-by":"crossref","first-page":"305","DOI":"10.4103\/0378-6323.152743","article-title":"Histiocytoid Sweet syndrome related to bortezomib: a mimicker of cutaneous infiltration by myeloma","volume":"81","author":"Llamas-Velasco","year":"2015","journal-title":"Indian J Dermatol Venereol Leprol"},{"issue":"7","key":"10.1016\/j.path.2025.09.003_bib14","doi-asserted-by":"crossref","first-page":"1396","DOI":"10.3760\/cma.j.issn.0366-6999.20132274","article-title":"Histiocytoid Sweet\u2019s syndrome associated with rheumatoid arthritis and pleuritis","volume":"127","author":"Wang","year":"2014","journal-title":"Chin Med J (Engl)"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib15","doi-asserted-by":"crossref","first-page":"335","DOI":"10.1684\/ejd.2015.2586","article-title":"Histiocytoid Sweet\u2019s syndrome: a localized cutaneous proliferation of macrophages frequently associated with chronic myeloproliferative disease","volume":"25","author":"Magro","year":"2015","journal-title":"Eur J Dermatol"},{"issue":"3","key":"10.1016\/j.path.2025.09.003_bib16","doi-asserted-by":"crossref","first-page":"256","DOI":"10.1097\/CMR.0000000000000438","article-title":"Histiocytoid Sweet\u2019s syndrome during combined therapy with BRAF and MEK inhibitors for metastatic melanoma","volume":"28","author":"Morgado-Carrasco","year":"2018","journal-title":"Melanoma Res"},{"issue":"2","key":"10.1016\/j.path.2025.09.003_bib17","doi-asserted-by":"crossref","first-page":"661","DOI":"10.1016\/j.jaad.2020.02.048","article-title":"Risk of malignancy in histiocytoid Sweet syndrome: a systematic review and reappraisal","volume":"83","author":"Haber","year":"2020","journal-title":"J Am Acad Dermatol"},{"issue":"2","key":"10.1016\/j.path.2025.09.003_bib18","doi-asserted-by":"crossref","first-page":"348","DOI":"10.1111\/ced.14361","article-title":"Palbociclib-induced histiocytoid Sweet syndrome","volume":"46","author":"Fusta-Novell","year":"2021","journal-title":"Clin Exp Dermatol"},{"issue":"10","key":"10.1016\/j.path.2025.09.003_bib19","doi-asserted-by":"crossref","first-page":"1355","DOI":"10.1111\/1346-8138.17201","article-title":"Proteasome inhibitor-associated histiocytoid Sweet\u2019s syndrome: clinical and histological similarities to Nakajo-Nishimura syndrome suggest a potential mechanism","volume":"51","author":"Cho","year":"2024","journal-title":"J Dermatol"},{"issue":"1","key":"10.1016\/j.path.2025.09.003_bib20","doi-asserted-by":"crossref","first-page":"47","DOI":"10.1097\/DAD.0000000000002286","article-title":"Histiocytoid Sweet syndrome presenting in two sisters with deficiency of deaminase type 2","volume":"45","author":"Hui Ong","year":"2023","journal-title":"Am J Dermatopathol"},{"issue":"7","key":"10.1016\/j.path.2025.09.003_bib21","doi-asserted-by":"crossref","first-page":"e220","DOI":"10.1111\/1346-8138.16745","article-title":"Histiocytoid Sweet syndrome as a rare skin manifestation of relapsing polychondritis","volume":"50","author":"Terao-Hirayama","year":"2023","journal-title":"J Dermatol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib22","doi-asserted-by":"crossref","first-page":"615","DOI":"10.1111\/bjd.21692","article-title":"Sweet-like syndrome and multiple COVID arm syndrome following COVID-19 vaccines: \u2019specific' patterns in a series of 192 patients","volume":"187","author":"Darrigade","year":"2022","journal-title":"Br J Dermatol"},{"key":"10.1016\/j.path.2025.09.003_bib23","article-title":"Sweet syndrome following Moderna COVID-19 vaccine: a case report","volume":"10","author":"Pelchat","year":"2022","journal-title":"SAGE Open Med Case Rep"},{"key":"10.1016\/j.path.2025.09.003_bib24","doi-asserted-by":"crossref","first-page":"106","DOI":"10.1016\/j.ijid.2021.11.030","article-title":"Histiocytoid Sweet syndrome associated with anorectal lymphogranuloma venereum in a patient with HIV infection","volume":"115","author":"Al-Hayani","year":"2022","journal-title":"Int J Infect Dis"},{"key":"10.1016\/j.path.2025.09.003_bib25","doi-asserted-by":"crossref","first-page":"96","DOI":"10.1016\/j.jdcr.2021.09.025","article-title":"Infantile histiocytoid Sweet syndrome without an underlying systemic association","volume":"17","author":"Stepien","year":"2021","journal-title":"JAAD Case Rep"},{"key":"10.1016\/j.path.2025.09.003_bib26","doi-asserted-by":"crossref","DOI":"10.1111\/pde.15932","article-title":"Histiocytoid Sweet syndrome with paradoxical neutropenia in a pediatric patient","author":"Boock","year":"2025","journal-title":"Pediatr Dermatol"},{"key":"10.1016\/j.path.2025.09.003_bib27","doi-asserted-by":"crossref","first-page":"927","DOI":"10.3389\/fimmu.2017.00927","article-title":"CANDLE syndrome as a paradigm of proteasome-related autoinflammation","volume":"8","author":"Torrelo","year":"2017","journal-title":"Front Immunol"},{"issue":"3","key":"10.1016\/j.path.2025.09.003_bib28","doi-asserted-by":"crossref","first-page":"489","DOI":"10.1016\/j.jaad.2009.04.046","article-title":"Chronic atypical neutrophilic dermatosis with lipodystrophy and elevated temperature (CANDLE) syndrome","volume":"62","author":"Torrelo","year":"2010","journal-title":"J Am Acad Dermatol"},{"issue":"15","key":"10.1016\/j.path.2025.09.003_bib29","doi-asserted-by":"crossref","DOI":"10.1097\/MD.0000000000003033","article-title":"Histiocytoid Sweet syndrome is more frequently associated with myelodysplastic syndromes than the classical neutrophilic variant: a comparative series of 62 patients","volume":"95","author":"Ghoufi","year":"2016","journal-title":"Medicine (Baltim)"},{"issue":"9","key":"10.1016\/j.path.2025.09.003_bib30","doi-asserted-by":"crossref","first-page":"1170","DOI":"10.1001\/archderm.142.9.1170","article-title":"Chronic recurrent lymphocytic Sweet syndrome as a predictive marker of myelodysplasia: a report of 9 cases","volume":"142","author":"Vignon-Pennamen","year":"2006","journal-title":"Arch Dermatol"},{"key":"10.1016\/j.path.2025.09.003_bib31","doi-asserted-by":"crossref","DOI":"10.2340\/actadv.v102.1123","article-title":"Leukaemia cutis: clinical features and outcomes of 56 patients","volume":"102","author":"Yook","year":"2022","journal-title":"Acta Derm Venereol"},{"issue":"2","key":"10.1016\/j.path.2025.09.003_bib32","doi-asserted-by":"crossref","first-page":"172","DOI":"10.2340\/00015555-0025","article-title":"Cutaneous infiltrations can herald an inapparent myelodysplastic syndrome","volume":"86","author":"Schneider","year":"2006","journal-title":"Acta Derm Venereol"},{"issue":"6","key":"10.1016\/j.path.2025.09.003_bib33","doi-asserted-by":"crossref","first-page":"596","DOI":"10.1097\/DAD.0b013e318158ddcd","article-title":"Panniculitis with histiocytoid\/immature neutrophils is not limited to histiocytoid panniculitic Sweet syndrome","volume":"29","author":"Gerami","year":"2007","journal-title":"Am J Dermatopathol"},{"issue":"8","key":"10.1016\/j.path.2025.09.003_bib34","doi-asserted-by":"crossref","first-page":"919","DOI":"10.5858\/arpa.2018-0239-RA","article-title":"Dermatologic urgencies and emergencies: what every pathologist should know","volume":"143","author":"Abate","year":"2019","journal-title":"Arch Pathol Lab Med"},{"issue":"11","key":"10.1016\/j.path.2025.09.003_bib35","doi-asserted-by":"crossref","first-page":"834","DOI":"10.1111\/cup.14678","article-title":"Myelodysplasia cutis and VEXAS syndrome initially diagnosed as histiocytoid Sweet syndrome: a diagnostic pitfall","volume":"51","author":"Shimshak","year":"2024","journal-title":"J Cutan Pathol"},{"issue":"12","key":"10.1016\/j.path.2025.09.003_bib36","doi-asserted-by":"crossref","first-page":"1832","DOI":"10.1002\/art.24061","article-title":"Stem cell transplant for myelodysplastic syndrome-associated histiocytoid Sweet\u2019s syndrome in a patient with arthritis and myalgias","volume":"59","author":"Kaiser","year":"2008","journal-title":"Arthritis Rheum"},{"issue":"1","key":"10.1016\/j.path.2025.09.003_bib37","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1111\/j.1346-8138.2011.01290.x","article-title":"Subcutaneous histiocytoid Sweet\u2019s syndrome in a patient associated with myelodysplastic syndrome-refractory anemia","volume":"39","author":"Lin","year":"2012","journal-title":"J Dermatol"},{"issue":"6","key":"10.1016\/j.path.2025.09.003_bib38","doi-asserted-by":"crossref","first-page":"777","DOI":"10.1111\/1756-185X.12103","article-title":"Histiocytoid Sweet syndrome and cutaneous polyarteritis nodosa secondary to myelodysplastic syndrome","volume":"16","author":"Pinal-Fernandez","year":"2013","journal-title":"Int J Rheum Dis"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib39","doi-asserted-by":"crossref","first-page":"339","DOI":"10.4212\/cjhp.v68i4.1475","article-title":"Histiocytoid variant of Sweet syndrome associated with azacitidine and recurrence upon rechallenge","volume":"68","author":"Bonazza","year":"2015","journal-title":"Can J Hosp Pharm"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib40","doi-asserted-by":"crossref","first-page":"394","DOI":"10.1111\/cup.12659","article-title":"Cutaneous histiocytoid Sweet syndrome and its relationship to hematological diseases","volume":"43","author":"Bush","year":"2016","journal-title":"J Cutan Pathol"},{"issue":"1","key":"10.1016\/j.path.2025.09.003_bib41","doi-asserted-by":"crossref","first-page":"9","DOI":"10.5826\/dpc.0601a04","article-title":"Histiocytoid Sweet\u2019s syndrome in a patient with myelodsyplastic syndrome: report and review of the literature","volume":"6","author":"Shalaby","year":"2016","journal-title":"Dermatol Pract Concept"},{"issue":"7","key":"10.1016\/j.path.2025.09.003_bib42","doi-asserted-by":"crossref","first-page":"651","DOI":"10.1001\/jamadermatol.2016.6092","article-title":"Clinicopathologic, immunohistochemical, and molecular features of histiocytoid Sweet Syndrome","volume":"153","author":"Alegria-Landa","year":"2017","journal-title":"JAMA Dermatol"},{"issue":"8","key":"10.1016\/j.path.2025.09.003_bib43","doi-asserted-by":"crossref","first-page":"836","DOI":"10.1001\/jamadermatol.2017.1670","article-title":"Histiocytoid Sweet syndrome and myelodysplastic syndrome-reply","volume":"153","author":"Alegria-Landa","year":"2017","journal-title":"JAMA Dermatol"},{"issue":"8","key":"10.1016\/j.path.2025.09.003_bib44","doi-asserted-by":"crossref","first-page":"835","DOI":"10.1001\/jamadermatol.2017.1669","article-title":"Histiocytoid Sweet syndrome and myelodysplastic syndrome","volume":"153","author":"Vignon-Pennamen","year":"2017","journal-title":"JAMA Dermatol"},{"issue":"6","key":"10.1016\/j.path.2025.09.003_bib45","doi-asserted-by":"crossref","first-page":"1021","DOI":"10.1016\/j.jaad.2014.01.874","article-title":"Histiocytoid Sweet syndrome may indicate leukemia cutis: a novel application of fluorescence in situ hybridization","volume":"70","author":"Chavan","year":"2014","journal-title":"J Am Acad Dermatol"},{"issue":"5","key":"10.1016\/j.path.2025.09.003_bib46","doi-asserted-by":"crossref","first-page":"649","DOI":"10.1111\/bjh.13485","article-title":"Chronic relapsing remitting sweet syndrome--a harbinger of myelodysplastic syndrome","volume":"170","author":"Kulasekararaj","year":"2015","journal-title":"Br J Haematol"},{"issue":"8","key":"10.1016\/j.path.2025.09.003_bib47","doi-asserted-by":"crossref","first-page":"1251","DOI":"10.1182\/blood.2021013967","article-title":"Clinical, pathological, and molecular features of myelodysplasia cutis","volume":"139","author":"Delaleu","year":"2022","journal-title":"Blood"},{"issue":"9","key":"10.1016\/j.path.2025.09.003_bib48","doi-asserted-by":"crossref","first-page":"2321","DOI":"10.1038\/jid.2015.146","article-title":"Myelodysplasia cutis versus leukemia cutis","volume":"135","author":"Osio","year":"2015","journal-title":"J Invest Dermatol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib49","doi-asserted-by":"crossref","first-page":"321","DOI":"10.1111\/ajd.12389","article-title":"Leukaemia cutis mimicking histiocytoid Sweet\u2019s syndrome in a woman with acute myeloid leukaemia","volume":"57","author":"Cheng","year":"2016","journal-title":"Australas J Dermatol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib50","doi-asserted-by":"crossref","first-page":"290","DOI":"10.1111\/cup.13418","article-title":"Histiocytoid Sweet syndrome harboring an isocitrate dehydrogenase 1 mutation: a case report and retrospective analysis of 29 cases of histiocytoid Sweet syndrome","volume":"46","author":"Libby","year":"2019","journal-title":"J Cutan Pathol"},{"issue":"3","key":"10.1016\/j.path.2025.09.003_bib51","doi-asserted-by":"crossref","first-page":"328","DOI":"10.1016\/j.pathol.2021.01.005","article-title":"Design, implementation and clinical utility of next generation sequencing in myeloid malignancies: acute myeloid leukaemia and myelodysplastic syndrome","volume":"53","author":"Hughes","year":"2021","journal-title":"Pathology"},{"issue":"9","key":"10.1016\/j.path.2025.09.003_bib52","doi-asserted-by":"crossref","DOI":"10.3390\/cancers11091364","article-title":"Next-generation sequencing improves diagnosis, prognosis and clinical management of myeloid neoplasms","volume":"11","author":"Carbonell","year":"2019","journal-title":"Cancers (Basel)"},{"issue":"8","key":"10.1016\/j.path.2025.09.003_bib53","doi-asserted-by":"crossref","first-page":"825","DOI":"10.1093\/ced\/llae015","article-title":"Clinical and histological features of histiocytoid Sweet syndrome associated with VEXAS syndrome","volume":"49","author":"Lecoeuvre","year":"2024","journal-title":"Clin Exp Dermatol"},{"key":"10.1016\/j.path.2025.09.003_bib54","doi-asserted-by":"crossref","DOI":"10.1097\/DAD.0000000000002969","article-title":"Histiocytoid Sweet syndrome as a manifestation of myelodysplasia cutis\/cutaneous VEXAS syndrome","author":"Ng","year":"2025","journal-title":"Am J Dermatopathol"},{"key":"10.1016\/j.path.2025.09.003_bib55","series-title":"WHO classification of tumours series","article-title":"Myelodysplastic neoplasms: introduction","author":"Khoury","year":"2024"},{"issue":"11","key":"10.1016\/j.path.2025.09.003_bib56","doi-asserted-by":"crossref","first-page":"1200","DOI":"10.1182\/blood.2022015850","article-title":"International consensus classification of myeloid neoplasms and acute leukemias: integrating morphologic, clinical, and genomic data","volume":"140","author":"Arber","year":"2022","journal-title":"Blood"},{"issue":"2","key":"10.1016\/j.path.2025.09.003_bib57","doi-asserted-by":"crossref","first-page":"367","DOI":"10.1111\/bjd.19547","article-title":"Identification of clonal skin myeloid cells by next-generation sequencing in myelodysplasia cutis","volume":"184","author":"Delaleu","year":"2021","journal-title":"Br J Dermatol"},{"key":"10.1016\/j.path.2025.09.003_bib58","doi-asserted-by":"crossref","DOI":"10.3389\/fimmu.2021.715053","article-title":"Myeloid clonal infiltrate identified with next-generation sequencing in skin lesions associated with myelodysplastic syndromes and chronic myelomonocytic leukemia: a case series","volume":"12","author":"Martin de Fremont","year":"2021","journal-title":"Front Immunol"},{"issue":"5","key":"10.1016\/j.path.2025.09.003_bib59","doi-asserted-by":"crossref","first-page":"882","DOI":"10.1016\/j.jaad.2008.12.038","article-title":"Sweet syndrome with histiocytoid infiltrate and neutropenia: a rare combination","volume":"61","author":"Liu","year":"2009","journal-title":"J Am Acad Dermatol"},{"issue":"2","key":"10.1016\/j.path.2025.09.003_bib60","doi-asserted-by":"crossref","first-page":"246","DOI":"10.1684\/ejd.2018.3225","article-title":"Efficacy of etoposide for myelodysplasia cutis","volume":"28","author":"Rioli","year":"2018","journal-title":"Eur J Dermatol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib61","doi-asserted-by":"crossref","first-page":"773","DOI":"10.1111\/ced.15055","article-title":"Myelodysplasia cutis as the presenting sign of chronic myelomonocytic leukaemia","volume":"47","author":"Maglie","year":"2022","journal-title":"Clin Exp Dermatol"},{"key":"10.1016\/j.path.2025.09.003_bib62","article-title":"A rare case of late myelodysplasia cutis associated with essential thrombocythemia: a case report","volume":"10","author":"Fournier","year":"2022","journal-title":"SAGE Open Med Case Rep"},{"issue":"27","key":"10.1016\/j.path.2025.09.003_bib63","doi-asserted-by":"crossref","first-page":"2628","DOI":"10.1056\/NEJMoa2026834","article-title":"Somatic mutations in UBA1 and severe adult-onset autoinflammatory disease","volume":"383","author":"Beck","year":"2020","journal-title":"N Engl J Med"},{"key":"10.1016\/j.path.2025.09.003_bib64","doi-asserted-by":"crossref","first-page":"399","DOI":"10.3389\/fimmu.2017.00399","article-title":"NF-kappaB pathway in autoinflammatory diseases: dysregulation of protein modifications by ubiquitin defines a new category of autoinflammatory diseases","volume":"8","author":"Aksentijevich","year":"2017","journal-title":"Front Immunol"},{"key":"10.1016\/j.path.2025.09.003_bib65","series-title":"GeneReviews((R))","article-title":"VEXAS syndrome","author":"Hadjadj","year":"2025"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib66","doi-asserted-by":"crossref","first-page":"917","DOI":"10.1016\/j.jaad.2022.10.052","article-title":"Clinical and pathological features of cutaneous manifestations in VEXAS syndrome: a multicenter retrospective study of 59 cases","volume":"88","author":"Zakine","year":"2023","journal-title":"J Am Acad Dermatol"},{"issue":"6","key":"10.1016\/j.path.2025.09.003_bib67","doi-asserted-by":"crossref","first-page":"1209","DOI":"10.1016\/j.jaad.2022.01.042","article-title":"VEXAS syndrome (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) for the dermatologist","volume":"89","author":"Sterling","year":"2023","journal-title":"J Am Acad Dermatol"},{"issue":"8","key":"10.1016\/j.path.2025.09.003_bib68","doi-asserted-by":"crossref","first-page":"822","DOI":"10.1001\/jamadermatol.2024.1657","article-title":"Skin manifestations of VEXAS syndrome and associated genotypes","volume":"160","author":"Tan","year":"2024","journal-title":"JAMA Dermatol"},{"issue":"13","key":"10.1016\/j.path.2025.09.003_bib69","doi-asserted-by":"crossref","first-page":"1496","DOI":"10.1182\/blood.2022016985","article-title":"Translation of cytoplasmic UBA1 contributes to VEXAS syndrome pathogenesis","volume":"140","author":"Ferrada","year":"2022","journal-title":"Blood"},{"issue":"2","key":"10.1016\/j.path.2025.09.003_bib70","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1111\/cup.14757","article-title":"VEXAS syndrome: Histiocytoid cells with feathery cytoplasm as a clue to the diagnosis","volume":"52","author":"Ko","year":"2025","journal-title":"J Cutan Pathol"},{"issue":"7","key":"10.1016\/j.path.2025.09.003_bib71","doi-asserted-by":"crossref","first-page":"938","DOI":"10.1111\/ijd.16635","article-title":"Cutaneous involvement in VEXAS syndrome: clinical and histopathologic findings","volume":"62","author":"Hines","year":"2023","journal-title":"Int J Dermatol"},{"issue":"10","key":"10.1016\/j.path.2025.09.003_bib72","doi-asserted-by":"crossref","first-page":"637","DOI":"10.1097\/DAD.0000000000002716","article-title":"The histopathology of vacuoles, E1 Enzyme, X-linked, autoinflammatory, somatic syndrome: report of 12 skin biopsies from 6 patients","volume":"46","author":"Brumbaugh","year":"2024","journal-title":"Am J Dermatopathol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib73","first-page":"2201","article-title":"Myelodysplastic syndrome and sweet\u2019s syndrome are associated with a mutation in isocitrate dehydrogenase 1","volume":"38","author":"Snyder","year":"2018","journal-title":"Anticancer Res"},{"issue":"12","key":"10.1016\/j.path.2025.09.003_bib74","doi-asserted-by":"crossref","first-page":"864","DOI":"10.1111\/j.1365-4362.1992.tb03544.x","article-title":"Pelgeroid-like anomalous cells in the diagnosis of neutrophilic dermatosis associated with myelodysplastic syndrome","volume":"31","author":"Nogita","year":"1992","journal-title":"Int J Dermatol"},{"issue":"4","key":"10.1016\/j.path.2025.09.003_bib75","doi-asserted-by":"crossref","first-page":"1111","DOI":"10.1038\/jid.2012.408","article-title":"Evidence of differentiation in myeloid malignancies associated neutrophilic dermatosis: a fluorescent in situ hybridization study of 14 patients","volume":"133","author":"Sujobert","year":"2013","journal-title":"J Invest Dermatol"},{"issue":"9","key":"10.1016\/j.path.2025.09.003_bib76","doi-asserted-by":"crossref","first-page":"1873","DOI":"10.1016\/j.jid.2019.12.040","article-title":"Next-generation sequencing in myeloid neoplasm-associated sweet\u2019s syndrome demonstrates clonal relation between malignant cells and skin-infiltrating neutrophils","volume":"140","author":"Passet","year":"2020","journal-title":"J Invest Dermatol"},{"issue":"1","key":"10.1016\/j.path.2025.09.003_bib77","doi-asserted-by":"crossref","DOI":"10.1016\/j.modpat.2023.100352","article-title":"Cutaneous manifestations of myeloid neoplasms exhibit broad and divergent morphologic and immunophenotypic features but share ancestral clonal mutations with bone marrow","volume":"37","author":"Sadigh","year":"2024","journal-title":"Mod Pathol"}],"container-title":["Surgical Pathology Clinics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1875918125000613?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1875918125000613?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,2,4]],"date-time":"2026-02-04T16:46:18Z","timestamp":1770223578000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1875918125000613"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,3]]},"references-count":77,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2026,3]]}},"alternative-id":["S1875918125000613"],"URL":"https:\/\/doi.org\/10.1016\/j.path.2025.09.003","relation":{},"ISSN":["1875-9181"],"issn-type":[{"value":"1875-9181","type":"print"}],"subject":[],"published":{"date-parts":[[2026,3]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Beyond Sweet Syndrome","name":"articletitle","label":"Article Title"},{"value":"Surgical Pathology Clinics","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.path.2025.09.003","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2025 Elsevier Inc. All rights are reserved, including those for text and data mining, AI training, and similar technologies.","name":"copyright","label":"Copyright"}]}}