{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,22]],"date-time":"2026-09-22T09:52:08Z","timestamp":1790070728145,"version":"4.0.1"},"reference-count":48,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2011,6,1]],"date-time":"2011-06-01T00:00:00Z","timestamp":1306886400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Paediatric Respiratory Reviews"],"published-print":{"date-parts":[[2011,6]]},"DOI":"10.1016\/j.prrv.2010.10.005","type":"journal-article","created":{"date-parts":[[2010,11,27]],"date-time":"2010-11-27T09:55:18Z","timestamp":1290851718000},"page":"133-138","source":"Crossref","is-referenced-by-count":116,"title":["Respiratory Manifestations in Mucopolysaccharidoses"],"prefix":"10.1016","volume":"12","author":[{"given":"Marianne S.","family":"Muhlebach","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"William","family":"Wooten","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Joseph","family":"Muenzer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"6","key":"10.1016\/j.prrv.2010.10.005_bib0005","doi-asserted-by":"crossref","first-page":"237","DOI":"10.1186\/cc5069","article-title":"Bench-to-bedside review: the role of glycosaminoglycans in respiratory disease","volume":"10","author":"Souza-Fernandes","year":"2006","journal-title":"Crit Care"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0010","doi-asserted-by":"crossref","first-page":"104","DOI":"10.1016\/j.ymgme.2007.09.011","article-title":"Clinical and genetic spectrum of Sanfilippo type C (MPS IIIC) disease in The Netherlands","volume":"93","author":"Ruijter","year":"2008","journal-title":"Mol Genet Metab"},{"issue":"3","key":"10.1016\/j.prrv.2010.10.005_bib0015","doi-asserted-by":"crossref","first-page":"403","DOI":"10.1136\/adc.69.3.403","article-title":"Management of mucopolysaccharidosis type III","volume":"69","author":"Cleary","year":"1993","journal-title":"Arch Dis Child"},{"issue":"3","key":"10.1016\/j.prrv.2010.10.005_bib0020","doi-asserted-by":"crossref","first-page":"357","DOI":"10.1007\/BF01799267","article-title":"Mucopolysaccharidosis type IVA (Morquio syndrome): a clinical review","volume":"19","author":"Northover","year":"1996","journal-title":"J Inherit Metab Dis"},{"issue":"5","key":"10.1016\/j.prrv.2010.10.005_bib0025","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1016\/j.ijporl.2005.01.017","article-title":"Otorhinolaryngological manifestations of the mucopolysaccharidoses","volume":"69","author":"Simmons","year":"2005","journal-title":"Int J Pediatr Otorhinolaryngol"},{"issue":"1","key":"10.1016\/j.prrv.2010.10.005_bib0030","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1016\/j.ijporl.2009.09.042","article-title":"Role of the pediatric otolaryngologist in diagnosis and management of children with mucopolysaccharidoses","volume":"74","author":"Wold","year":"2010","journal-title":"Int J Pediatr Otorhinolaryngol"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0035","doi-asserted-by":"crossref","first-page":"135","DOI":"10.1165\/rcmb.2005-0256OC","article-title":"Identification of glycosaminoglycans in human airway secretions","volume":"34","author":"Monzon","year":"2006","journal-title":"Am J Respir Cell Mol Biol"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0040","doi-asserted-by":"crossref","first-page":"179","DOI":"10.1016\/S0165-5876(97)00176-6","article-title":"ABR and temporal bone pathology in Hurler's disease","volume":"43","author":"Komura","year":"1998","journal-title":"Int J Pediatr Otorhinolaryngol"},{"key":"10.1016\/j.prrv.2010.10.005_bib0045","series-title":"Morphological aspects of the mucopolysaccharidoses., Inborn Errors of Skin, Hair and Connective Tissue","author":"Spranger","year":"1975"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0050","doi-asserted-by":"crossref","first-page":"197","DOI":"10.1016\/j.ijporl.2006.09.016","article-title":"Age-related functional and histopathological changes of the ear in the MPS I mouse","volume":"71","author":"Schachern","year":"2007","journal-title":"Int J Pediatr Otorhinolaryngol"},{"issue":"3","key":"10.1016\/j.prrv.2010.10.005_bib0055","doi-asserted-by":"crossref","first-page":"205","DOI":"10.1016\/S0165-5876(85)80066-5","article-title":"Pathological and biochemical study in the adenoid of mucopolysaccharidosis II","volume":"10","author":"Fujitani","year":"1985","journal-title":"Int J Pediatr Otorhinolaryngol"},{"issue":"1","key":"10.1016\/j.prrv.2010.10.005_bib0060","doi-asserted-by":"crossref","first-page":"40","DOI":"10.1034\/j.1600-0455.2002.430108.x","article-title":"Airway changes in children with mucopolysaccharidoses","volume":"43","author":"Shih","year":"2002","journal-title":"Acta Radiol"},{"issue":"4","key":"10.1016\/j.prrv.2010.10.005_bib0065","doi-asserted-by":"crossref","first-page":"380","DOI":"10.1017\/S0022215100140526","article-title":"Failure to control the airway in a patient with Hunter's syndrome","volume":"112","author":"Gaitini","year":"1998","journal-title":"J Laryngol Otol"},{"issue":"457","key":"10.1016\/j.prrv.2010.10.005_bib0070","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1111\/j.1651-2227.2008.00650.x","article-title":"Diagnosis and management of respiratory involvement in Hunter syndrome","volume":"97","author":"Kamin","year":"2008","journal-title":"Acta Paediatr Suppl"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0075","doi-asserted-by":"crossref","first-page":"233","DOI":"10.1001\/archotol.130.2.233","article-title":"Airway management in mucopolysaccharide storage disorders","volume":"130","author":"Shinhar","year":"2004","journal-title":"Arch Otolaryngol Head Neck Surg"},{"issue":"4","key":"10.1016\/j.prrv.2010.10.005_bib0080","doi-asserted-by":"crossref","first-page":"225","DOI":"10.1007\/BF02388760","article-title":"Narrow trachea in mucopolysaccharidoses","volume":"15","author":"Peters","year":"1985","journal-title":"Pediatr Radiol"},{"issue":"4","key":"10.1016\/j.prrv.2010.10.005_bib0085","first-page":"317","article-title":"[Mucopolysaccharidosis 6-A (Maroteaux-Lamy disease): comparison of clinical and pathologico-anatomic findings in a 27-year-old patient]","volume":"42","author":"Keller","year":"1987","journal-title":"Helv Paediatr Acta"},{"issue":"3 Pt 1","key":"10.1016\/j.prrv.2010.10.005_bib0090","doi-asserted-by":"crossref","first-page":"280","DOI":"10.1288\/00005537-198703000-00005","article-title":"Hunter's syndrome: a study in airway obstruction","volume":"97","author":"Sasaki","year":"1987","journal-title":"Laryngoscope"},{"issue":"3","key":"10.1016\/j.prrv.2010.10.005_bib0095","doi-asserted-by":"crossref","first-page":"229","DOI":"10.1016\/S0165-5876(86)80034-9","article-title":"Upper airway obstruction in Hunter syndrome","volume":"11","author":"Brama","year":"1986","journal-title":"Int J Pediatr Otorhinolaryngol"},{"issue":"10","key":"10.1016\/j.prrv.2010.10.005_bib0100","doi-asserted-by":"crossref","first-page":"1205","DOI":"10.1001\/archotol.1990.01870100099022","article-title":"Management of tracheal lesions in Hurler syndrome","volume":"116","author":"Adachi","year":"1990","journal-title":"Arch Otolaryngol Head Neck Surg"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0105","doi-asserted-by":"crossref","first-page":"458","DOI":"10.1007\/s003300100932","article-title":"Tracheobronchial stent insertions in the management of major airway obstruction in a patient with Hunter syndrome (type-II mucopolysaccharidosis)","volume":"12","author":"Davitt","year":"2002","journal-title":"Eur Radiol"},{"issue":"7","key":"10.1016\/j.prrv.2010.10.005_bib0110","doi-asserted-by":"crossref","first-page":"679","DOI":"10.1002\/ppul.21246","article-title":"Skeletal dysplasias: Evaluation with impulse oscillometry and thoracoabdominal motion analysis","volume":"45","author":"Rodriguez","year":"2010","journal-title":"Pediatr Pulmonol"},{"issue":"4","key":"10.1016\/j.prrv.2010.10.005_bib0115","doi-asserted-by":"crossref","first-page":"209","DOI":"10.1097\/00005792-198807000-00002","article-title":"Respiratory complications of mucopolysaccharide storage disorders","volume":"67","author":"Semenza","year":"1988","journal-title":"Medicine (Baltimore)"},{"issue":"5 Pt 1","key":"10.1016\/j.prrv.2010.10.005_bib0120","doi-asserted-by":"crossref","first-page":"458","DOI":"10.1177\/000348948509400508","article-title":"Airway obstruction and sleep apnea in Hurler and Hunter syndromes","volume":"94","author":"Shapiro","year":"1985","journal-title":"Ann Otol Rhinol Laryngol"},{"issue":"7","key":"10.1016\/j.prrv.2010.10.005_bib0125","doi-asserted-by":"crossref","first-page":"558","DOI":"10.1046\/j.1440-1754.2003.00218.x","article-title":"Hurler's syndrome with cor pulmonale secondary to obstructive sleep apnoea treated by continuous positive airway pressure","volume":"39","author":"Chan","year":"2003","journal-title":"J Paediatr Child Health"},{"issue":"5 Suppl","key":"10.1016\/j.prrv.2010.10.005_bib0130","doi-asserted-by":"crossref","first-page":"S27","DOI":"10.1016\/j.jpeds.2004.01.052","article-title":"The mucopolysaccharidoses: a heterogeneous group of disorders with variable pediatric presentations","volume":"144","author":"Muenzer","year":"2004","journal-title":"J Pediatr"},{"issue":"5","key":"10.1016\/j.prrv.2010.10.005_bib0135","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1055\/s-2008-1071352","article-title":"Severe type Hunter's syndrome. Polysomnographic and neuropathological study","volume":"23","author":"Kurihara","year":"1992","journal-title":"Neuropediatrics"},{"issue":"4","key":"10.1016\/j.prrv.2010.10.005_bib0140","doi-asserted-by":"crossref","first-page":"473","DOI":"10.1007\/s10545-008-0878-x","article-title":"Neurological findings in Hunter disease: pathology and possible therapeutic effects reviewed","volume":"31","author":"Al Sawaf","year":"2008","journal-title":"J Inherit Metab Dis"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0145","doi-asserted-by":"crossref","first-page":"192","DOI":"10.1111\/j.1600-079X.2005.00294.x","article-title":"Impairment of the melatonin rhythm in children with Sanfilippo syndrome","volume":"40","author":"Guerrero","year":"2006","journal-title":"J Pineal Res"},{"issue":"1","key":"10.1016\/j.prrv.2010.10.005_bib0150","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.survophthal.2005.11.007","article-title":"Mucopolysaccharidoses and the eye","volume":"51","author":"Ashworth","year":"2006","journal-title":"Surv Ophthalmol"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0155","doi-asserted-by":"crossref","first-page":"212","DOI":"10.1016\/j.bbr.2010.01.045","article-title":"Circadian rhythm and suprachiasmatic nucleus alterations in the mouse model of mucopolysaccharidosis IIIB","volume":"209","author":"Canal","year":"2010","journal-title":"Behav Brain Res"},{"issue":"12","key":"10.1016\/j.prrv.2010.10.005_bib0160","doi-asserted-by":"crossref","first-page":"1239","DOI":"10.1136\/adc.2004.065482","article-title":"Sleep disturbance in Sanfilippo syndrome: a parental questionnaire study","volume":"90","author":"Fraser","year":"2005","journal-title":"Arch Dis Child"},{"issue":"6","key":"10.1016\/j.prrv.2010.10.005_bib0165","doi-asserted-by":"crossref","first-page":"e1228","DOI":"10.1542\/peds.2008-0999","article-title":"Multidisciplinary management of Hunter syndrome","volume":"124","author":"Muenzer","year":"2009","journal-title":"Pediatrics"},{"issue":"1","key":"10.1016\/j.prrv.2010.10.005_bib0170","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1542\/peds.2008-0416","article-title":"Mucopolysaccharidosis I: management and treatment guidelines","volume":"123","author":"Muenzer","year":"2009","journal-title":"Pediatrics"},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0175","doi-asserted-by":"crossref","first-page":"171","DOI":"10.1016\/j.ymgme.2006.08.007","article-title":"A follow-up study of MPS I patients treated with laronidase enzyme replacement therapy for 6 years","volume":"90","author":"Sifuentes","year":"2007","journal-title":"Mol Genet Metab"},{"issue":"5","key":"10.1016\/j.prrv.2010.10.005_bib0180","doi-asserted-by":"crossref","first-page":"581","DOI":"10.1016\/j.jpeds.2004.01.046","article-title":"Enzyme replacement therapy for mucopolysaccharidosis I: a randomized, double-blinded, placebo-controlled, multinational study of recombinant human alpha-L-iduronidase (laronidase)","volume":"144","author":"Wraith","year":"2004","journal-title":"J Pediatr"},{"issue":"5","key":"10.1016\/j.prrv.2010.10.005_bib0185","doi-asserted-by":"crossref","first-page":"418","DOI":"10.1034\/j.1399-0004.2002.620512.x","article-title":"Sleep disturbance in mucopolysaccharidosis type III (Sanfilippo syndrome): a survey of managing clinicians","volume":"62","author":"Fraser","year":"2002","journal-title":"Clin Genet"},{"key":"10.1016\/j.prrv.2010.10.005_bib0190","unstructured":"Smith, R. 1980. Anaesthesia for infants and children. In Co., CM, editor, 4th ed, St. Louis. 533\u2013536."},{"issue":"2","key":"10.1016\/j.prrv.2010.10.005_bib0195","doi-asserted-by":"crossref","first-page":"126","DOI":"10.1111\/j.1365-2044.1984.tb09499.x","article-title":"Anaesthetic considerations in the mucopolysaccharidoses","volume":"39","author":"King","year":"1984","journal-title":"Anaesthesia"},{"issue":"1","key":"10.1016\/j.prrv.2010.10.005_bib0200","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1007\/BF03010548","article-title":"The mucopolysaccharidoses and anaesthesia: a report of clinical experience","volume":"35","author":"Herrick","year":"1988","journal-title":"Can J Anaesth"},{"issue":"4","key":"10.1016\/j.prrv.2010.10.005_bib0205","doi-asserted-by":"crossref","first-page":"459","DOI":"10.1177\/0310057X9602400408","article-title":"Anaesthesia for children with mucopolysaccharidoses","volume":"24","author":"Moores","year":"1996","journal-title":"Anaesth Intensive Care"},{"issue":"3","key":"10.1016\/j.prrv.2010.10.005_bib0210","doi-asserted-by":"crossref","first-page":"403","DOI":"10.1016\/0022-3468(93)90240-L","article-title":"Children with mucopolysaccharidosis: perioperative care, morbidity, mortality, and new findings","volume":"28","author":"Belani","year":"1993","journal-title":"J Pediatr Surg"},{"issue":"3","key":"10.1016\/j.prrv.2010.10.005_bib0215","doi-asserted-by":"crossref","first-page":"273","DOI":"10.1016\/S0165-5876(98)00063-9","article-title":"Acute airway obstruction in Hunter syndrome","volume":"44","author":"Yoskovitch","year":"1998","journal-title":"Int J Pediatr Otorhinolaryngol"},{"issue":"5","key":"10.1016\/j.prrv.2010.10.005_bib0220","doi-asserted-by":"crossref","first-page":"441","DOI":"10.1046\/j.1460-9592.2003.00969.x","article-title":"Postobstructive pulmonary oedema during anaesthesia in children with mucopolysaccharidoses","volume":"13","author":"Walker","year":"2003","journal-title":"Paediatr Anaesth"},{"issue":"1","key":"10.1016\/j.prrv.2010.10.005_bib0225","doi-asserted-by":"crossref","first-page":"123","DOI":"10.1016\/j.pcl.2009.11.004","article-title":"Current international perspectives on hematopoietic stem cell transplantation for inherited metabolic disorders","volume":"57","author":"Boelens","year":"2010","journal-title":"Pediatr Clin North Am"},{"issue":"1","key":"10.1016\/j.prrv.2010.10.005_bib0230","doi-asserted-by":"crossref","first-page":"229","DOI":"10.1542\/peds.2007-3847","article-title":"Long-term efficacy and safety of laronidase in the treatment of mucopolysaccharidosis I","volume":"123","author":"Clarke","year":"2009","journal-title":"Pediatrics"},{"issue":"4","key":"10.1016\/j.prrv.2010.10.005_bib0235","doi-asserted-by":"crossref","first-page":"533","DOI":"10.1016\/j.jpeds.2005.12.014","article-title":"Enzyme replacement therapy for mucopolysaccharidosis VI: a phase 3, randomized, double-blind, placebo-controlled, multinational study of recombinant human N-acetylgalactosamine 4-sulfatase (recombinant human arylsulfatase B or rhASB) and follow-on, open-label extension study","volume":"148","author":"Harmatz","year":"2006","journal-title":"J Pediatr"},{"issue":"8","key":"10.1016\/j.prrv.2010.10.005_bib0240","doi-asserted-by":"crossref","first-page":"465","DOI":"10.1097\/01.gim.0000232477.37660.fb","article-title":"A phase II\/III clinical study of enzyme replacement therapy with idursulfase in mucopolysaccharidosis II (Hunter syndrome)","volume":"8","author":"Muenzer","year":"2006","journal-title":"Genet Med"}],"container-title":["Paediatric Respiratory Reviews"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1526054210000990?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1526054210000990?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T14:51:31Z","timestamp":1711983091000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1526054210000990"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,6]]},"references-count":48,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2011,6]]}},"alternative-id":["S1526054210000990"],"URL":"https:\/\/doi.org\/10.1016\/j.prrv.2010.10.005","relation":{},"ISSN":["1526-0542"],"issn-type":[{"value":"1526-0542","type":"print"}],"subject":[],"published":{"date-parts":[[2011,6]]}}}