{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,29]],"date-time":"2025-11-29T08:03:39Z","timestamp":1764403419706,"version":"3.37.3"},"reference-count":15,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2025,1,1]],"date-time":"2025-01-01T00:00:00Z","timestamp":1735689600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2025,1,1]],"date-time":"2025-01-01T00:00:00Z","timestamp":1735689600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2024,10,3]],"date-time":"2024-10-03T00:00:00Z","timestamp":1727913600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["clinicalkey.fr","clinicalkey.jp","clinicalkey.es","clinicalkey.com.au","clinicalkey.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Radiology Case Reports"],"published-print":{"date-parts":[[2025,1]]},"DOI":"10.1016\/j.radcr.2024.10.018","type":"journal-article","created":{"date-parts":[[2024,10,30]],"date-time":"2024-10-30T21:03:59Z","timestamp":1730322239000},"page":"414-418","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":1,"title":["Cerebral adrenoleukodystrophy presenting as status epilepticus: Unveiling the neurological maze"],"prefix":"10.1016","volume":"20","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-3742-2835","authenticated-orcid":false,"given":"Saket Satyasham","family":"Toshniwal","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S.","family":"Jiwan Kinkar","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sunil","family":"Kumar","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sourya","family":"Acharya","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"issue":"1","key":"10.1016\/j.radcr.2024.10.018_bib0001","doi-asserted-by":"crossref","first-page":"52","DOI":"10.1002\/jdn.10003","article-title":"X-linked adrenoleukodystrophy: pathology, pathophysiology, diagnostic testing, newborn screening and therapies","volume":"80","author":"Turk","year":"2020","journal-title":"Int J Dev Neurosci"},{"issue":"12","key":"10.1016\/j.radcr.2024.10.018_bib0002","doi-asserted-by":"crossref","first-page":"1721","DOI":"10.1016\/j.bbamcr.2006.07.010","article-title":"X-linked adrenoleukodystrophy: clinical, biochemical and pathogenetic aspects","volume":"1763","author":"Berger","year":"2006","journal-title":"Biochim Biophys Acta"},{"key":"10.1016\/j.radcr.2024.10.018_bib0003","article-title":"X-linked adult-onset adrenoleukodystrophy: psychiatric and neurological manifestations","volume":"5","author":"Shamim","year":"2017","journal-title":"SAGE Open Med Case Rep"},{"key":"10.1016\/j.radcr.2024.10.018_bib0004","first-page":"97","article-title":"A novel catastrophic presentation of X-linked adrenoleukodystrophy","volume":"24","author":"Vawter-Lee","year":"2015","journal-title":"JIMD Rep"},{"key":"10.1016\/j.radcr.2024.10.018_bib0005","doi-asserted-by":"crossref","DOI":"10.1016\/j.biopha.2021.112214","article-title":"Management of adrenoleukodystrophy: from pre-clinical studies to the development of new therapies","volume":"143","author":"Ma","year":"2021","journal-title":"Biomed Pharmacother"},{"issue":"2","key":"10.1016\/j.radcr.2024.10.018_bib0006","doi-asserted-by":"crossref","first-page":"174","DOI":"10.1002\/jimd.12581","article-title":"Neurocognitive and mental health impact of adrenoleukodystrophy across the lifespan: insights for the era of newborn screening","volume":"46","author":"Pierpont","year":"2023","journal-title":"J Inherit Metab Dis"},{"issue":"3","key":"10.1016\/j.radcr.2024.10.018_bib0007","doi-asserted-by":"crossref","first-page":"619","DOI":"10.1148\/rg.253045118","article-title":"Childhood X-linked adrenoleukodystrophy: clinical-pathologic overview and MR imaging manifestations at initial evaluation and follow-up","volume":"25","author":"Kim","year":"2005","journal-title":"Radiographics"},{"key":"10.1016\/j.radcr.2024.10.018_bib0008","article-title":"Adrenoleukodystrophy: a forgotten diagnosis in children with primary Addison's disease","volume":"2012","author":"Nascimento","year":"2012","journal-title":"BMJ Case Rep"},{"issue":"1","key":"10.1016\/j.radcr.2024.10.018_bib0009","first-page":"95","article-title":"Involvement of the pontomedullary corticospinal tracts: a useful finding in the diagnosis of X-linked adrenoleukodystrophy","volume":"18","author":"Barkovich","year":"1997","journal-title":"AJNR Am J Neuroradiol"},{"issue":"3","key":"10.1016\/j.radcr.2024.10.018_bib0010","doi-asserted-by":"crossref","first-page":"192","DOI":"10.4103\/1817-1745.123661","article-title":"Childhood adrenoleukodystrophy\u2013Classic and variant\u2013review of clinical manifestations and magnetic resonance imaging","volume":"8","author":"Rai","year":"2013","journal-title":"J Pediatr Neurosci"},{"issue":"2","key":"10.1016\/j.radcr.2024.10.018_bib0011","first-page":"470","article-title":"X-linked adrenoleukodystrophy is a frequent cause of idiopathic Addison's disease in young adult male patients","volume":"81","author":"Laureti","year":"1996","journal-title":"J Clin Endocrinol Metab"},{"issue":"8","key":"10.1016\/j.radcr.2024.10.018_bib0012","doi-asserted-by":"crossref","first-page":"770","DOI":"10.1097\/00007611-199808000-00017","article-title":"Adrenoleukodystrophy: unusual clinical and radiographic manifestation","volume":"91","author":"Williams","year":"1998","journal-title":"South Med J"},{"key":"10.1016\/j.radcr.2024.10.018_bib0013","doi-asserted-by":"crossref","first-page":"1049","DOI":"10.1007\/s00431-011-1401-1","article-title":"Early diagnosis of cerebral X-linked adrenoleukodystrophy in boys with Addison's disease improves survival and neurological outcomes","volume":"170","author":"Polgreen","year":"2011","journal-title":"Eur J Pediatr"},{"issue":"3","key":"10.1016\/j.radcr.2024.10.018_bib0014","doi-asserted-by":"crossref","first-page":"258","DOI":"10.7861\/clinmedicine.17-3-258","article-title":"Adrenal insufficiency - recognition and management","volume":"17","author":"Pazderska","year":"2017","journal-title":"Clin Med (Lond)"},{"issue":"1","key":"10.1016\/j.radcr.2024.10.018_bib0015","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1038\/s41572-021-00252-7","article-title":"Adrenal insufficiency","volume":"7","author":"Hahner","year":"2021","journal-title":"Nat Rev Dis Primers"}],"container-title":["Radiology Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1930043324011270?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1930043324011270?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,2,23]],"date-time":"2025-02-23T11:15:30Z","timestamp":1740309330000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1930043324011270"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,1]]},"references-count":15,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2025,1]]}},"alternative-id":["S1930043324011270"],"URL":"https:\/\/doi.org\/10.1016\/j.radcr.2024.10.018","relation":{},"ISSN":["1930-0433"],"issn-type":[{"type":"print","value":"1930-0433"}],"subject":[],"published":{"date-parts":[[2025,1]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Cerebral adrenoleukodystrophy presenting as status epilepticus: Unveiling the neurological maze","name":"articletitle","label":"Article Title"},{"value":"Radiology Case Reports","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.radcr.2024.10.018","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2024 The Authors. Published by Elsevier Inc. on behalf of University of Washington.","name":"copyright","label":"Copyright"}]}}