{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,1]],"date-time":"2026-07-01T16:45:26Z","timestamp":1782924326734,"version":"3.54.5"},"reference-count":65,"publisher":"Elsevier BV","issue":"5","license":[{"start":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T00:00:00Z","timestamp":1777593600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T00:00:00Z","timestamp":1777593600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2026,2,13]],"date-time":"2026-02-13T00:00:00Z","timestamp":1770940800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":["clinicalkey.fr","em-consulte.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["La Revue de M\u00e9decine Interne"],"published-print":{"date-parts":[[2026,5]]},"DOI":"10.1016\/j.revmed.2026.02.005","type":"journal-article","created":{"date-parts":[[2026,3,5]],"date-time":"2026-03-05T20:30:41Z","timestamp":1772742641000},"page":"263-272","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":0,"title":["Les ent\u00e9ropathies associ\u00e9es aux d\u00e9ficits immunitaires humoraux primitifs\u00a0: mise au point"],"prefix":"10.1016","volume":"47","author":[{"ORCID":"https:\/\/orcid.org\/0009-0004-1902-5061","authenticated-orcid":false,"given":"Florentin","family":"Masoch","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3874-5580","authenticated-orcid":false,"given":"Isabelle","family":"Durieu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8867-1524","authenticated-orcid":false,"given":"Yoann","family":"Roubertou","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Quitterie","family":"Reynaud","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6474-5181","authenticated-orcid":false,"given":"Ma\u00ebl","family":"Richard","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"3","key":"10.1016\/j.revmed.2026.02.005_bib0330","doi-asserted-by":"crossref","first-page":"e20250007","DOI":"10.70962\/jhi.20250007","volume":"1","author":"Kindle","year":"2025","journal-title":"J Hum Immun"},{"key":"10.1016\/j.revmed.2026.02.005_bib0335","doi-asserted-by":"crossref","first-page":"149","DOI":"10.3389\/fimmu.2020.00149","article-title":"Non-infectious complications of common variable immunodeficiency: updated clinical spectrum, sequelae, and insights to pathogenesis","volume":"11","author":"Ho","year":"2020","journal-title":"Front Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0340","unstructured":"Inborn Errors of Immunity Committee (IEI). IUIS, https:\/\/iuis.org\/committees\/iei\/; 2019 [accessed 20\u00a0Feb 2025]."},{"issue":"11","key":"10.1016\/j.revmed.2026.02.005_bib0345","doi-asserted-by":"crossref","first-page":"1743","DOI":"10.14309\/ajg.0000000000002027","article-title":"An expert opinion\/approach: clinical presentations, diagnostic considerations, and therapeutic options for gastrointestinal manifestations of common variable immune deficiency","volume":"117","author":"Hashash","year":"2022","journal-title":"Am J Gastroenterol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0350","doi-asserted-by":"crossref","first-page":"1197","DOI":"10.1016\/j.jaci.2012.05.046","article-title":"Confirmation and improvement of criteria for clinical phenotyping in common variable immunodeficiency disorders in replicate cohorts","volume":"130","author":"Chapel","year":"2012","journal-title":"J Allergy Clin Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0355","doi-asserted-by":"crossref","first-page":"1740","DOI":"10.3389\/fimmu.2017.01740","article-title":"Common variable immunodeficiency non-infectious disease endotypes redefined using unbiased network clustering in large electronic datasets","volume":"8","author":"Farmer","year":"2018","journal-title":"Front Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0360","doi-asserted-by":"crossref","first-page":"139","DOI":"10.1016\/j.clim.2018.09.008","article-title":"CVID enteropathy is characterized by exceeding low mucosal IgA levels and interferon-driven inflammation possibly related to the presence of a pathobiont","volume":"197","author":"Shulzhenko","year":"2018","journal-title":"Clin Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0365","doi-asserted-by":"crossref","first-page":"1654","DOI":"10.3389\/fimmu.2020.01654","article-title":"Altered microbiota, impaired quality of life, malabsorption, infection, and inflammation in CVID patients with diarrhoea","volume":"11","author":"van Schewick","year":"2020","journal-title":"Front Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0370","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1080\/1744666X.2021.2008241","article-title":"Gut inflammation in CVID: causes and consequences","volume":"18","author":"Andersen","year":"2022","journal-title":"Expert Rev Clin Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0375","doi-asserted-by":"crossref","first-page":"277","DOI":"10.1182\/blood-2007-11-124545","article-title":"Common variable immunodeficiency disorders: division into distinct clinical phenotypes","volume":"112","author":"Chapel","year":"2008","journal-title":"Blood"},{"issue":"9","key":"10.1016\/j.revmed.2026.02.005_bib0380","doi-asserted-by":"crossref","first-page":"1229","DOI":"10.1080\/1744666X.2025.2556435","article-title":"Non-infectious pulmonary and gastrointestinal manifestations in primary antibody deficiencies: lessons for the clinic","volume":"21","author":"Franco","year":"2025","journal-title":"Expert Rev Clin Immunol"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0385","doi-asserted-by":"crossref","first-page":"129","DOI":"10.1007\/s10875-025-01920-z","article-title":"CVID enteropathy is difficult to treat and shows a heterogeneous histopathology","volume":"45","author":"Juliana","year":"2025","journal-title":"J Clin Immunol"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0390","doi-asserted-by":"crossref","first-page":"116","DOI":"10.1016\/j.jaci.2013.12.1077","article-title":"Clinical picture and treatment of 2212\u00a0patients with common variable immunodeficiency","volume":"134","author":"Gathmann","year":"2014","journal-title":"J Allergy Clin Immunol"},{"issue":"6","key":"10.1016\/j.revmed.2026.02.005_bib0395","doi-asserted-by":"crossref","first-page":"627","DOI":"10.1007\/s10875-014-0056-x","article-title":"Autoimmunity and Inflammation in X-linked agammaglobulinemia","volume":"34","author":"Hernandez-Trujillo","year":"2014","journal-title":"J Clin Immunol"},{"issue":"9","key":"10.1016\/j.revmed.2026.02.005_bib0400","doi-asserted-by":"crossref","first-page":"3466","DOI":"10.1016\/j.jaip.2021.04.070","article-title":"Crohn's-like enteritis in X-linked agammaglobulinemia: a case series and systematic review","volume":"9","author":"Khan","year":"2021","journal-title":"J Allergy Clin Immunol Pract"},{"key":"10.1016\/j.revmed.2026.02.005_bib0405","doi-asserted-by":"crossref","first-page":"75","DOI":"10.1186\/s13223-023-00826-y","article-title":"Clinical manifestation for immunoglobulin A deficiency: a systematic review and meta-analysis","volume":"19","author":"Vosughimotlagh","year":"2023","journal-title":"Allergy Asthma Clin Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0410","doi-asserted-by":"crossref","first-page":"47","DOI":"10.1016\/S0022-3476(97)70123-9","article-title":"Clinical spectrum of X-linked hyper-IgM syndrome","volume":"131","author":"Levy","year":"1997","journal-title":"J Pediatr"},{"key":"10.1016\/j.revmed.2026.02.005_bib0415","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1093\/ecco-jcc\/jjab124","article-title":"Primary hypogammaglobulinaemia with inflammatory bowel disease-like features: An ECCO CONFER Multicentre Case Series","volume":"16","author":"Albshesh","year":"2022","journal-title":"J Crohns Colitis"},{"key":"10.1016\/j.revmed.2026.02.005_bib0420","doi-asserted-by":"crossref","first-page":"990","DOI":"10.1053\/j.gastro.2014.07.023","article-title":"The diagnostic approach to monogenic very early onset inflammatory bowel disease","volume":"147","author":"Uhlig","year":"2014","journal-title":"Gastroenterology"},{"issue":"10401","key":"10.1016\/j.revmed.2026.02.005_bib0425","doi-asserted-by":"crossref","first-page":"571","DOI":"10.1016\/S0140-6736(23)00966-2","article-title":"Ulcerative colitis","volume":"402","author":"Le Berre","year":"2023","journal-title":"Lancet"},{"issue":"10432","key":"10.1016\/j.revmed.2026.02.005_bib0430","doi-asserted-by":"crossref","first-page":"1177","DOI":"10.1016\/S0140-6736(23)02586-2","article-title":"Crohn's disease","volume":"403","author":"Dolinger","year":"2024","journal-title":"Lancet"},{"key":"10.1016\/j.revmed.2026.02.005_bib0435","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1038\/nri3608","article-title":"Intestinal epithelial cells: regulators of barrier function and immune homeostasis","volume":"14","author":"Peterson","year":"2014","journal-title":"Nat Rev Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0440","doi-asserted-by":"crossref","first-page":"983","DOI":"10.1051\/medsci\/20163211014","article-title":"Le dialogue microbiote-cellules souches - Un \u00e9l\u00e9ment cl\u00e9 pour la r\u00e9g\u00e9n\u00e9ration intestinale","volume":"32","author":"Stedman","year":"2016","journal-title":"Med Sci (Paris)"},{"key":"10.1016\/j.revmed.2026.02.005_bib0445","doi-asserted-by":"crossref","first-page":"147","DOI":"10.1111\/j.1600-065X.2011.01078.x","article-title":"Epithelial barrier: an interface for the cross-communication between gut flora and immune system","volume":"245","author":"Goto","year":"2012","journal-title":"Immunol Rev"},{"key":"10.1016\/j.revmed.2026.02.005_bib0450","doi-asserted-by":"crossref","first-page":"961","DOI":"10.1051\/medsci\/20163211011","article-title":"Microbiote intestinal et d\u00e9veloppement du syst\u00e8me immunitaire","volume":"32","author":"Gaboriau-Routhiau","year":"2016","journal-title":"Med Sci (Paris)"},{"key":"10.1016\/j.revmed.2026.02.005_bib0455","doi-asserted-by":"crossref","first-page":"12","DOI":"10.1186\/s40168-024-01982-y","article-title":"Gut microbial dysbiosis, IgA, and Enterococcus in common variable immunodeficiency with immune dysregulation","volume":"13","author":"Berbers","year":"2025","journal-title":"Microbiome"},{"key":"10.1016\/j.revmed.2026.02.005_bib0460","doi-asserted-by":"crossref","first-page":"674","DOI":"10.1182\/blood.V87.2.674.bloodjournal872674","article-title":"Persistent activation of the tumor necrosis factor system in a subgroup of patients with common variable immunodeficiency--possible immunologic and clinical consequences","volume":"87","author":"Aukrust","year":"1996","journal-title":"Blood"},{"issue":"4","key":"10.1016\/j.revmed.2026.02.005_bib0465","doi-asserted-by":"crossref","first-page":"1436","DOI":"10.1016\/j.jaip.2019.10.024","article-title":"Gastrointestinal manifestations in common variable immunodeficiency (CVID) are associated with an altered immunophenotype including B- and T-cell dysregulation","volume":"8","author":"Barmettler","year":"2020","journal-title":"J Allergy Clin Immunol Pract"},{"key":"10.1016\/j.revmed.2026.02.005_bib0470","doi-asserted-by":"crossref","first-page":"1278197","DOI":"10.3389\/fimmu.2024.1278197","article-title":"Studying the cellular basis of small bowel enteropathy using high-parameter flow cytometry in mouse models of primary antibody deficiency","volume":"15","author":"Mohammed","year":"2024","journal-title":"Front Immunol"},{"issue":"7","key":"10.1016\/j.revmed.2026.02.005_bib0475","doi-asserted-by":"crossref","first-page":"1461","DOI":"10.1007\/s10875-022-01299-1","article-title":"Protein-losing enteropathy as a complication and\/or differential diagnosis of common variable immunodeficiency","volume":"42","author":"Sanges","year":"2022","journal-title":"J Clin Immunol"},{"issue":"3","key":"10.1016\/j.revmed.2026.02.005_bib0480","doi-asserted-by":"crossref","first-page":"767","DOI":"10.1016\/j.jaci.2022.09.029","article-title":"Duodenal inflammation in common variable immunodeficiency has altered transcriptional response to viruses","volume":"151","author":"Kaarb\u00f8","year":"2023","journal-title":"J Allergy Clin Immunol"},{"issue":"12","key":"10.1016\/j.revmed.2026.02.005_bib0485","doi-asserted-by":"crossref","first-page":"1585","DOI":"10.1038\/nm.2505","article-title":"Crosstalk between B lymphocytes, microbiota and the intestinal epithelium governs immunity versus metabolism in the gut","volume":"17","author":"Shulzhenko","year":"2011","journal-title":"Nat Med"},{"key":"10.1016\/j.revmed.2026.02.005_bib0490","doi-asserted-by":"crossref","first-page":"712915","DOI":"10.3389\/fimmu.2021.712915","article-title":"Gut microbiome and common variable immunodeficiency: few certainties and many outstanding questions","volume":"12","author":"Varricchi","year":"2021","journal-title":"Front Immunol"},{"issue":"6","key":"10.1016\/j.revmed.2026.02.005_bib0495","doi-asserted-by":"crossref","first-page":"1455","DOI":"10.1038\/mi.2016.18","article-title":"Altered gut microbiota profile in common variable immunodeficiency associates with levels of lipopolysaccharide and markers of systemic immune activation","volume":"9","author":"J\u00f8rgensen","year":"2016","journal-title":"Mucosal Immunol"},{"issue":"5","key":"10.1016\/j.revmed.2026.02.005_bib0500","doi-asserted-by":"crossref","first-page":"1017","DOI":"10.1038\/s41385-021-00398-3","article-title":"Intestinal immunoregulation: lessons from human mendelian diseases","volume":"14","author":"Charbit-Henrion","year":"2021","journal-title":"Mucosal Immunol"},{"issue":"439","key":"10.1016\/j.revmed.2026.02.005_bib0505","doi-asserted-by":"crossref","first-page":"eaan1217","DOI":"10.1126\/scitranslmed.aan1217","article-title":"Microbial ecology perturbation in human IgA deficiency","volume":"10","author":"Fadlallah","year":"2018","journal-title":"Sci Transl Med"},{"issue":"4","key":"10.1016\/j.revmed.2026.02.005_bib0510","doi-asserted-by":"crossref","first-page":"1793","DOI":"10.1172\/JCI128322","article-title":"Bruton tyrosine kinase deficiency augments NLRP3\u00a0inflammasome activation and causes IL-1\u03b2-mediated colitis","volume":"130","author":"Mao","year":"2020","journal-title":"J Clin Invest"},{"issue":"8","key":"10.1016\/j.revmed.2026.02.005_bib0515","doi-asserted-by":"crossref","first-page":"102872","DOI":"10.1016\/j.autrev.2021.102872","article-title":"Inflammatory bowel disease in primary immunodeficiency disorders is a heterogeneous clinical entity requiring an individualized treatment strategy: A systematic review","volume":"20","author":"Both","year":"2021","journal-title":"Autoimmunity Rev"},{"issue":"6","key":"10.1016\/j.revmed.2026.02.005_bib0520","doi-asserted-by":"crossref","first-page":"1467","DOI":"10.1038\/ajg.2016.329","article-title":"A cross-sectional study of the prevalence of gastrointestinal symptoms and pathology in patients with common variable immunodeficiency","volume":"111","author":"J\u00f8rgensen","year":"2016","journal-title":"Am J Gastroenterol"},{"issue":"4","key":"10.1016\/j.revmed.2026.02.005_bib0525","doi-asserted-by":"crossref","first-page":"648","DOI":"10.14309\/ajg.0000000000000140","article-title":"A high prevalence of gastrointestinal manifestations in common variable immunodeficiency","volume":"114","author":"Pikkarainen","year":"2019","journal-title":"Am J Gastroenterol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0530","doi-asserted-by":"crossref","first-page":"jjaf106","DOI":"10.1093\/ecco-jcc\/jjaf106","article-title":"ECCO-ESGAR-ESP-IBUS guideline on diagnostics and monitoring of patients with inflammatory bowel disease: Part 1","volume":"19","author":"Kucharzik","year":"2025","journal-title":"J Crohns Colitis"},{"issue":"6","key":"10.1016\/j.revmed.2026.02.005_bib0535","doi-asserted-by":"crossref","first-page":"1932","DOI":"10.1016\/j.jaci.2018.02.055","article-title":"Phenotype, penetrance, and treatment of 133\u00a0cytotoxic T-lymphocyte antigen 4-insufficient subjects","volume":"142","author":"Schwab","year":"2018","journal-title":"J Allergy Clin Immunol"},{"issue":"10","key":"10.1016\/j.revmed.2026.02.005_bib0540","doi-asserted-by":"crossref","first-page":"2262","DOI":"10.1038\/ajg.2010.214","article-title":"The enteropathy associated with common variable immunodeficiency: the delineated frontiers with celiac disease","volume":"105","author":"Malamut","year":"2010","journal-title":"Am J Gastroenterol"},{"issue":"12","key":"10.1016\/j.revmed.2026.02.005_bib0545","doi-asserted-by":"crossref","first-page":"1800","DOI":"10.1097\/PAS.0b013e3180cab60c","article-title":"Gastrointestinal tract pathology in patients with common variable immunodeficiency (CVID): a clinicopathologic study and review","volume":"31","author":"Daniels","year":"2007","journal-title":"Am J Surg Pathol"},{"issue":"9","key":"10.1016\/j.revmed.2026.02.005_bib0550","doi-asserted-by":"crossref","first-page":"1244","DOI":"10.1136\/gut.35.9.1244","article-title":"Studies on the enteropathy associated with primary hypogammaglobulinaemia","volume":"35","author":"Teahon","year":"1994","journal-title":"Gut"},{"issue":"3","key":"10.1016\/j.revmed.2026.02.005_bib0555","doi-asserted-by":"crossref","first-page":"287","DOI":"10.1007\/s10875-017-0374-x","article-title":"Gastrointestinal manifestations in X-linked agammaglobulinemia","volume":"37","author":"Barmettler","year":"2017","journal-title":"J Clin Immunol"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0560","doi-asserted-by":"crossref","first-page":"251","DOI":"10.1002\/ibd.21376","article-title":"Characterization of immunologic defects in patients with common variable immunodeficiency (CVID) with intestinal disease","volume":"17","author":"Agarwal","year":"2011","journal-title":"Inflamm Bowel Dis"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0565","doi-asserted-by":"crossref","first-page":"81","DOI":"10.1016\/j.iac.2018.08.006","article-title":"Gastrointestinal manifestations and complications of primary immunodeficiency disorders","volume":"39","author":"Agarwal","year":"2019","journal-title":"Immunol Allergy Clin North Am"},{"issue":"8","key":"10.1016\/j.revmed.2026.02.005_bib0570","doi-asserted-by":"crossref","first-page":"733","DOI":"10.1056\/NEJMra2301594","article-title":"Protein-losing enteropathy","volume":"389","author":"Ozen","year":"2023","journal-title":"N Engl J Med"},{"issue":"10","key":"10.1016\/j.revmed.2026.02.005_bib0575","doi-asserted-by":"crossref","first-page":"1179","DOI":"10.1007\/s00431-010-1235-2","article-title":"Clinical practice","volume":"169","author":"Braamskamp","year":"2010","journal-title":"Eur J Pediatr"},{"issue":"7","key":"10.1016\/j.revmed.2026.02.005_bib0580","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1016\/j.revmed.2014.12.001","article-title":"[Protein-losing enteropathy]","volume":"36","author":"Amiot","year":"2015","journal-title":"Rev Med Interne"},{"key":"10.1016\/j.revmed.2026.02.005_bib0585","series-title":"Essential medical disorders of the stomach and small intestine","first-page":"401","article-title":"Protein-losing enteropathy","author":"Corning","year":"2019"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0590","doi-asserted-by":"crossref","first-page":"356","DOI":"10.1186\/s13023-025-03657-9","article-title":"Primary intestinal lymphangiectasia: French National Diagnosis and Care Protocol (PNDS; Protocole National de Diagnostic et de Soins)","volume":"20","author":"Vignes","year":"2025","journal-title":"Orphanet J Rare Dis"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0595","doi-asserted-by":"crossref","first-page":"28","DOI":"10.1007\/s10875-017-0456-9","article-title":"Autoimmune cytopenias and associated conditions in CVID: a report from the USIDNET Registry","volume":"38","author":"Feuille","year":"2018","journal-title":"J Clin Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0600","doi-asserted-by":"crossref","first-page":"1209570","DOI":"10.3389\/fimmu.2023.1209570","article-title":"Characterization of infectious and non-infectious gastrointestinal disease in common variable immunodeficiency: analysis of 114\u00a0patient cohort","volume":"14","author":"Sanchez","year":"2023","journal-title":"Front Immunol"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0605","doi-asserted-by":"crossref","first-page":"32","DOI":"10.1007\/s10875-023-01604-6","article-title":"CVID-associated intestinal disorders in the USIDNET Registry: an analysis of disease manifestations, functional status, comorbidities, and treatment","volume":"44","author":"Franzblau","year":"2023","journal-title":"J Clin Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0610","doi-asserted-by":"crossref","first-page":"1231242","DOI":"10.3389\/fimmu.2023.1231242","article-title":"Decline of gastric cancer mortality in common variable immunodeficiency in the years 2018-2022","volume":"14","author":"Milito","year":"2023","journal-title":"Front Immunol"},{"issue":"7","key":"10.1016\/j.revmed.2026.02.005_bib0615","doi-asserted-by":"crossref","first-page":"151","DOI":"10.15761\/CCRR.1000149","article-title":"Improved outcomes on subcutaneous IgG in patients with humoral immunodeficiency and co-morbid bowel disease","volume":"1","author":"Shah","year":"2015","journal-title":"Clin Case Rep Rev"},{"issue":"1","key":"10.1016\/j.revmed.2026.02.005_bib0620","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1007\/s10875-025-01966-z","article-title":"IgA and IgM-enriched immunoglobulins in primary immunodeficiencies: a pilot study","volume":"46","author":"Collet","year":"2025","journal-title":"J Clin Immunol"},{"key":"10.1016\/j.revmed.2026.02.005_bib0625","doi-asserted-by":"crossref","first-page":"A74","DOI":"10.1016\/j.revmed.2025.03.020","article-title":"Ent\u00e9ropathies inflammatoires associ\u00e9es aux d\u00e9ficits immunitaires humoraux primitifs","volume":"46","author":"Masoch","year":"2025","journal-title":"Rev Med Interne"},{"issue":"9","key":"10.1016\/j.revmed.2026.02.005_bib0630","doi-asserted-by":"crossref","first-page":"1154","DOI":"10.1093\/ecco-jcc\/jjx024","article-title":"Successful treatment of common variable immunodeficiency-associated inflammatory bowel disease with ustekinumab","volume":"11","author":"Ruiz de Morales","year":"2017","journal-title":"J Crohns Colitis"},{"issue":"21","key":"10.1016\/j.revmed.2026.02.005_bib0635","doi-asserted-by":"crossref","first-page":"2307","DOI":"10.1182\/blood-2017-08-801191","article-title":"Effective \u201cactivated PI3K\u03b4 syndrome\u201d\u2013targeted therapy with the PI3K\u03b4 inhibitor leniolisib","volume":"130","author":"Rao","year":"2017","journal-title":"Blood"},{"issue":"7","key":"10.1016\/j.revmed.2026.02.005_bib0640","doi-asserted-by":"crossref","first-page":"2179","DOI":"10.3748\/wjg.v22.i7.2179","article-title":"Diet therapy for inflammatory bowel diseases: The established and the new","volume":"22","author":"Durchschein","year":"2016","journal-title":"World J Gastroenterol"},{"issue":"2","key":"10.1016\/j.revmed.2026.02.005_bib0645","doi-asserted-by":"crossref","first-page":"75","DOI":"10.14785\/lpsn-2014-0015","article-title":"Atypical presentation and manifestations in X-linked agammaglobulinemia patients with novel BTK mutations","volume":"2","author":"Nahum","year":"2015","journal-title":"LymphoSign J"},{"key":"10.1016\/j.revmed.2026.02.005_bib0325","doi-asserted-by":"crossref","first-page":"1456672","DOI":"10.3389\/fcimb.2024.1456672","article-title":"Fecal microbiota transplantation in a patient with chronic diarrhea and primary and secondary immunodeficiency (common variable immunodeficiency and splenectomy)","volume":"14","author":"Napi\u00f3rkowska-Baran","year":"2024","journal-title":"Front Cell Infect Microbiol"}],"container-title":["La Revue de M\u00e9decine Interne"],"original-title":[],"language":"fr","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0248866326000184?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0248866326000184?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,7,1]],"date-time":"2026-07-01T15:50:34Z","timestamp":1782921034000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0248866326000184"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,5]]},"references-count":65,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2026,5]]}},"alternative-id":["S0248866326000184"],"URL":"https:\/\/doi.org\/10.1016\/j.revmed.2026.02.005","relation":{},"ISSN":["0248-8663"],"issn-type":[{"value":"0248-8663","type":"print"}],"subject":[],"published":{"date-parts":[[2026,5]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Les ent\u00e9ropathies associ\u00e9es aux d\u00e9ficits immunitaires humoraux primitifs\u00a0: mise au point","name":"articletitle","label":"Article Title"},{"value":"La Revue de M\u00e9decine Interne","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.revmed.2026.02.005","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2026 The Authors. Published by Elsevier Masson SAS on behalf of Soci\u00e9t\u00e9 Nationale Fran\u00e7aise de M\u00e9decine Interne (SNFMI).","name":"copyright","label":"Copyright"}]}}