{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,11,10]],"date-time":"2026-11-10T15:28:31Z","timestamp":1794324511470,"version":"4.9.0"},"reference-count":23,"publisher":"Elsevier BV","issue":"9","license":[{"start":{"date-parts":[[2012,9,1]],"date-time":"2012-09-01T00:00:00Z","timestamp":1346457600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2012,9,1]],"date-time":"2012-09-01T00:00:00Z","timestamp":1346457600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2014,9,1]],"date-time":"2014-09-01T00:00:00Z","timestamp":1409529600000},"content-version":"vor","delay-in-days":730,"URL":"http:\/\/www.elsevier.com\/open-access\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","resmedjournal.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Respiratory Medicine"],"published-print":{"date-parts":[[2012,9]]},"DOI":"10.1016\/j.rmed.2012.06.014","type":"journal-article","created":{"date-parts":[[2012,7,9]],"date-time":"2012-07-09T20:18:59Z","timestamp":1341865139000},"page":"1278-1285","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":53,"title":["Different features of lung involvement in Niemann-Pick disease and Gaucher disease"],"prefix":"10.1016","volume":"106","author":[{"given":"Bora","family":"G\u00fclhan","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"U\u011fur","family":"\u00d6z\u00e7elik","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Figen","family":"G\u00fcrakan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"\u015eafak","family":"G\u00fc\u00e7er","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Diclehan","family":"Orhan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G\u00fczin","family":"Cinel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ebru","family":"Yal\u00e7\u0131n","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Deniz Do\u011fru","family":"Ers\u00f6z","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nural","family":"Kiper","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Aysel","family":"Y\u00fcce","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G\u00fclsev","family":"Kale","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.rmed.2012.06.014_bib1","doi-asserted-by":"crossref","first-page":"1207","DOI":"10.1002\/ppul.20725","article-title":"Lung disease in Niemann Pick disease","volume":"42","author":"Guillemot","year":"2007","journal-title":"Pediatr Pulmonol"},{"key":"10.1016\/j.rmed.2012.06.014_bib2","doi-asserted-by":"crossref","first-page":"407","DOI":"10.1093\/qjmed\/94.8.407","article-title":"Lung involvement and enzyme replacement therapy in Gaucher disease","volume":"94","author":"Goitein","year":"2001","journal-title":"Q J Med"},{"key":"10.1016\/j.rmed.2012.06.014_bib3","first-page":"54A","article-title":"The frequency and type of lung involvement in patients with Gaucher\u2019s disease","volume":"58","author":"Lee","year":"1988","journal-title":"Lab Invest"},{"key":"10.1016\/j.rmed.2012.06.014_bib4","doi-asserted-by":"crossref","first-page":"164","DOI":"10.1097\/00003072-199903000-00005","article-title":"Hepatopulmonary syndrome in Gaucher disease with right-to-left shunt: evaluation and measurement using Tc-99m MAA","volume":"24","author":"Kim","year":"1999","journal-title":"Clin Nucl Med"},{"key":"10.1016\/j.rmed.2012.06.014_bib5","doi-asserted-by":"crossref","first-page":"985","DOI":"10.1164\/ajrccm.157.3.9706057","article-title":"Pulmonary manifestations of Gaucher disease: an increased risk for L444P homozygotes?","volume":"157","author":"Santamaria","year":"1998","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.rmed.2012.06.014_bib6","doi-asserted-by":"crossref","first-page":"228","DOI":"10.1212\/01.wnl.0000194208.08904.0c","article-title":"Natural history of type A Niemann-Pick disease: possible endpoints for therapeutic trials","volume":"66","author":"McGovern","year":"2006","journal-title":"Neurology"},{"key":"10.1016\/j.rmed.2012.06.014_bib7","doi-asserted-by":"crossref","first-page":"990","DOI":"10.1097\/00004728-199611000-00023","article-title":"Case report. Pulmonary involvement in Niemann-Pick disease subtype B: CT findings","volume":"20","author":"Ferretti","year":"1996","journal-title":"J Comput Assist Tomogr"},{"key":"10.1016\/j.rmed.2012.06.014_bib8","doi-asserted-by":"crossref","first-page":"1241","DOI":"10.1053\/rmed.2000.0942","article-title":"Pulmonary involvement in Niemann-Pick disease: case report and literature review","volume":"94","author":"Minai","year":"2000","journal-title":"Respir Med"},{"key":"10.1016\/j.rmed.2012.06.014_bib9","doi-asserted-by":"crossref","first-page":"55","DOI":"10.1159\/000196305","article-title":"Asymptomatic pulmonary involvement in 2 children with Niemann-Pick disease type B","volume":"61","author":"Niggemann","year":"1994","journal-title":"Respiration"},{"key":"10.1016\/j.rmed.2012.06.014_bib10","doi-asserted-by":"crossref","first-page":"E672","DOI":"10.1542\/peds.2004-0887","article-title":"The natural history of type B Niemann-Pick disease:results from a 10-year longitudinal study","author":"Wasserstein","year":"2004","journal-title":"Pediatrics"},{"key":"10.1016\/j.rmed.2012.06.014_bib11","doi-asserted-by":"crossref","first-page":"838","DOI":"10.1259\/bjr\/33503694","article-title":"Case report. Pulmonary involvement in an adult male affected by type B Niemann Pick disease","volume":"76","author":"Gonzalez-Reimers","year":"2003","journal-title":"Br J Radiol"},{"key":"10.1016\/j.rmed.2012.06.014_bib12","doi-asserted-by":"crossref","first-page":"e341","DOI":"10.1542\/peds.2007-3016","article-title":"A prospective, cross-sectional survey study of the natural history of Niemann-Pick disease type B","volume":"122","author":"McGovern","year":"2008","journal-title":"Pediatrics"},{"key":"10.1016\/j.rmed.2012.06.014_bib13","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1007\/s00401-007-0296-4","article-title":"Immune system irregularities in lysosomal storage disorders","volume":"115","author":"Castenada","year":"2008","journal-title":"Acta Neuropathol"},{"key":"10.1016\/j.rmed.2012.06.014_bib14","doi-asserted-by":"crossref","first-page":"775","DOI":"10.1023\/B:BOLI.0000009950.81514.c8","article-title":"Niemann-Pick disease: sixteen-year follow-up of allogeneic bone marrow transplantation in a type B variant","volume":"26","author":"Victor","year":"2003","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.rmed.2012.06.014_bib15","doi-asserted-by":"crossref","first-page":"128","DOI":"10.1164\/ajrccm.165.1.2103113","article-title":"Successful treatment of endogenous lipoid pneumonia due to Niemann Pick type B disease with whole-lung lavage","volume":"165","author":"Nicholson","year":"2002","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.rmed.2012.06.014_bib16","doi-asserted-by":"crossref","first-page":"409","DOI":"10.1183\/09031936.94.07020409","article-title":"Value of bronchoalveolar lavage in lipidoses with pulmonary involvement","volume":"7","author":"Tabak","year":"1994","journal-title":"Eur Respir J"},{"key":"10.1016\/j.rmed.2012.06.014_bib17","doi-asserted-by":"crossref","first-page":"169","DOI":"10.1002\/ppul.20248","article-title":"Early pulmonary involvement in Niemann-Pick type B disease: lung lavage is not useful","volume":"40","author":"Uyan","year":"2005","journal-title":"Pediatr Pulmonol"},{"key":"10.1016\/j.rmed.2012.06.014_bib18","doi-asserted-by":"crossref","first-page":"339","DOI":"10.1148\/radiol.2381041696","article-title":"Type B Niemann-Pick disease: findings at Chest Radiography, thin-section CT, and pulmonary function Testing","volume":"238","author":"Mendelson","year":"2006","journal-title":"Radiology"},{"key":"10.1016\/j.rmed.2012.06.014_bib19","doi-asserted-by":"crossref","first-page":"987","DOI":"10.1038\/labinvest.3780311","article-title":"Analysis of the lung pathology and alveolar macrophage function in the acid sphingomyelinase-deficient mouse model of Niemann-Pick disease","volume":"81","author":"Dhami","year":"2001","journal-title":"Lab Invest"},{"key":"10.1016\/j.rmed.2012.06.014_bib20","doi-asserted-by":"crossref","first-page":"L518","DOI":"10.1152\/ajplung.00258.2002","article-title":"Alveolar lipoproteinosis in an acid sphingomyelinase-deficient mouse model of Niemann-Pick disease","volume":"284","author":"Ikegami","year":"2003","journal-title":"Am J Physiol Lung Cell Mol Physiol"},{"key":"10.1016\/j.rmed.2012.06.014_bib21","doi-asserted-by":"crossref","first-page":"315","DOI":"10.1016\/j.ejmg.2008.02.004","article-title":"Molecular analysis of Turkish Gaucher disease patients: identification of novel mutations in glucocerebrosidase (GBA) gene","volume":"51","author":"Emre","year":"2008","journal-title":"Eur J Med Genet"},{"key":"10.1016\/j.rmed.2012.06.014_bib22","first-page":"237","article-title":"Gaucher disease type I: analysis of two cases with thalassemic facies and pulmonary arterio-venous fistulas","volume":"43","author":"G\u00fcrakan","year":"2001","journal-title":"Turk J Pediatr"},{"key":"10.1016\/j.rmed.2012.06.014_bib23","doi-asserted-by":"crossref","first-page":"514","DOI":"10.1002\/ana.21491","article-title":"Randomized, controlled trial of miglustat in Gaucher\u2019s disease type 3","volume":"64","author":"Schiffmann","year":"2008","journal-title":"Ann Neurol"}],"container-title":["Respiratory Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0954611112002284?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0954611112002284?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,16]],"date-time":"2025-10-16T11:22:52Z","timestamp":1760613772000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0954611112002284"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2012,9]]},"references-count":23,"journal-issue":{"issue":"9","published-print":{"date-parts":[[2012,9]]}},"alternative-id":["S0954611112002284"],"URL":"https:\/\/doi.org\/10.1016\/j.rmed.2012.06.014","relation":{},"ISSN":["0954-6111"],"issn-type":[{"value":"0954-6111","type":"print"}],"subject":[],"published":{"date-parts":[[2012,9]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Different features of lung involvement in Niemann-Pick disease and Gaucher disease","name":"articletitle","label":"Article Title"},{"value":"Respiratory Medicine","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.rmed.2012.06.014","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2012 Elsevier Ltd. All rights reserved.","name":"copyright","label":"Copyright"}]}}