{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,12]],"date-time":"2026-09-12T14:43:28Z","timestamp":1789224208811,"version":"build-2803163510"},"reference-count":15,"publisher":"Elsevier BV","issue":"6","license":[{"start":{"date-parts":[[2013,6,1]],"date-time":"2013-06-01T00:00:00Z","timestamp":1370044800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Seminars in Arthritis and Rheumatism"],"published-print":{"date-parts":[[2013,6]]},"DOI":"10.1016\/j.semarthrit.2012.09.001","type":"journal-article","created":{"date-parts":[[2012,12,25]],"date-time":"2012-12-25T05:45:53Z","timestamp":1356414353000},"page":"582-589","source":"Crossref","is-referenced-by-count":29,"title":["A descriptive analysis of 14 cases of progressive-psuedorheumatoid-arthropathy of childhood from south India: Review of literature in comparison with Juvenile Idiopathic Arthritis"],"prefix":"10.1016","volume":"42","author":[{"given":"Alka V.","family":"Ekbote","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Debashish","family":"Danda","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sathish","family":"Kumar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sumita","family":"Danda","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vrisha","family":"Madhuri","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sridhar","family":"Gibikote","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"1","key":"10.1016\/j.semarthrit.2012.09.001_bib1","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1007\/BF00661902","article-title":"Progressive pseudorheumatoid arthritis of childhood (PPAC). A hereditary disorder simulating rheumatoid arthritis","volume":"140","author":"Spranger","year":"1983","journal-title":"Eur J Pediatr"},{"issue":"2","key":"10.1016\/j.semarthrit.2012.09.001_bib2","doi-asserted-by":"crossref","first-page":"399","DOI":"10.1002\/ajmg.1320140224","article-title":"Progressive pseudorheumatoid arthropathy of childhood (PPAC): a hereditary disorder simulating juvenile rheumatoid arthritis","volume":"14","author":"Spranger","year":"1983","journal-title":"Am J Med Genet"},{"issue":"1","key":"10.1016\/j.semarthrit.2012.09.001_bib3","doi-asserted-by":"crossref","first-page":"94","DOI":"10.1038\/12699","article-title":"Mutations in the CCN gene family member WISP3 cause progressive pseudorheumatoid dysplasia","volume":"23","author":"Hurvitz","year":"1999","journal-title":"Nat Genet"},{"issue":"9","key":"10.1016\/j.semarthrit.2012.09.001_bib4","doi-asserted-by":"crossref","first-page":"985","DOI":"10.1007\/s00109-007-0193-2","article-title":"Cellular and molecular responses in progressive pseudorheumatoid dysplasia articular cartilage associated with compound heterozygous WISP3 gene mutation","volume":"85","author":"Zhou","year":"2007","journal-title":"J Mol Med"},{"issue":"1\u20132","key":"10.1016\/j.semarthrit.2012.09.001_bib5","first-page":"105108","article-title":"A homozygous recurring mutation in WISP3 causing progressive pseudorheumatoid arthropathy","volume":"24","author":"Temiz","year":"2011","journal-title":"J Pediatr Endocrinol Metab"},{"issue":"7","key":"10.1016\/j.semarthrit.2012.09.001_bib6","doi-asserted-by":"crossref","first-page":"559","DOI":"10.1136\/jmg.34.7.559","article-title":"Progressive pseudorheumatoid dysplasia: report of a family and review","volume":"34","author":"El-Shanti","year":"1997","journal-title":"J Med Genet"},{"issue":"1","key":"10.1016\/j.semarthrit.2012.09.001_bib7","first-page":"93","article-title":"Progressive pseudorheumatoid arthritis of childhood","volume":"38","author":"Mittal","year":"2001","journal-title":"Indian Pediatr"},{"issue":"1","key":"10.1016\/j.semarthrit.2012.09.001_bib8","doi-asserted-by":"crossref","first-page":"53","DOI":"10.1007\/s00296-003-0341-0","article-title":"Clinical, radiographic, and genetic diagnosis of progressive pseudorheumatoid dysplasia in a patient with severe polyarthropathy","volume":"24","author":"Ehl","year":"2004","journal-title":"Rheumatol Int"},{"issue":"9783","key":"10.1016\/j.semarthrit.2012.09.001_bib9","doi-asserted-by":"crossref","first-page":"2138","DOI":"10.1016\/S0140-6736(11)60244-4","article-title":"Juvenile idiopathic arthritis","volume":"377","author":"Prakken","year":"2011","journal-title":"Lancet"},{"issue":"5","key":"10.1016\/j.semarthrit.2012.09.001_bib10","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1007\/s11926-996-0006-6","article-title":"Prognostic factors in juvenile idiopathic arthritis","volume":"3","author":"Prieur","year":"2001","journal-title":"Curr Rheumatol Rep"},{"issue":"6","key":"10.1016\/j.semarthrit.2012.09.001_bib11","doi-asserted-by":"crossref","first-page":"411","DOI":"10.1007\/BF00204601","article-title":"Progressive pseudorheumatoid chondrodysplasia: a report of nine cases in three families","volume":"23","author":"Rezai-Delui","year":"1994","journal-title":"Skeletal Radiol"},{"issue":"3","key":"10.1016\/j.semarthrit.2012.09.001_bib12","doi-asserted-by":"crossref","first-page":"244","DOI":"10.1111\/j.1440-1673.1986.tb01748.x","article-title":"Radiographic features of progressive pseudorheumatoid arthritis","volume":"30","author":"Kozlowski","year":"1986","journal-title":"Australas Radiol"},{"issue":"7","key":"10.1016\/j.semarthrit.2012.09.001_bib13","doi-asserted-by":"crossref","first-page":"2289","DOI":"10.1002\/art.34411","article-title":"Dual regulation of metalloproteinase expression in chondrocytes by Wnt-1-inducible signalling pathway protein 3\/CCN6","volume":"64","author":"Baker","year":"2012","journal-title":"Arthritis Rheum"},{"issue":"2","key":"10.1016\/j.semarthrit.2012.09.001_bib14","doi-asserted-by":"crossref","first-page":"118","DOI":"10.1002\/ajmg.a.30906","article-title":"Molecular study of WISP3 in nine families originating from the Middle-East and presenting with progressive pseudorheumatoid dysplasia: identification of two novel mutations, and description of a founder effect","volume":"138A","author":"Delague","year":"2005","journal-title":"Am J Med Genet A"},{"issue":"3","key":"10.1016\/j.semarthrit.2012.09.001_bib15","doi-asserted-by":"crossref","first-page":"455","DOI":"10.1007\/BF02845540","article-title":"Progressive pseudorheumatoid arthropathy of childhood","volume":"66","author":"Cogulu","year":"1999","journal-title":"Indian J Pediatr"}],"container-title":["Seminars in Arthritis and Rheumatism"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0049017212002247?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0049017212002247?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,10,19]],"date-time":"2018-10-19T22:03:43Z","timestamp":1539986623000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0049017212002247"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2013,6]]},"references-count":15,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2013,6]]}},"alternative-id":["S0049017212002247"],"URL":"https:\/\/doi.org\/10.1016\/j.semarthrit.2012.09.001","relation":{},"ISSN":["0049-0172"],"issn-type":[{"value":"0049-0172","type":"print"}],"subject":[],"published":{"date-parts":[[2013,6]]}}}