{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,24]],"date-time":"2026-01-24T00:17:29Z","timestamp":1769213849068,"version":"3.49.0"},"reference-count":19,"publisher":"Elsevier BV","issue":"3","license":[{"start":{"date-parts":[[2016,12,1]],"date-time":"2016-12-01T00:00:00Z","timestamp":1480550400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","clinicalkey.es","clinicalkey.com.au","clinicalkey.fr","semarthritisrheumatism.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Seminars in Arthritis and Rheumatism"],"published-print":{"date-parts":[[2016,12]]},"DOI":"10.1016\/j.semarthrit.2016.07.007","type":"journal-article","created":{"date-parts":[[2016,7,21]],"date-time":"2016-07-21T13:47:47Z","timestamp":1469108867000},"page":"367-371","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":7,"title":["Autoinflammatory associated vasculitis"],"prefix":"10.1016","volume":"46","author":[{"given":"Shira","family":"Ginsberg","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Itzhak","family":"Rosner","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Michel","family":"Rozenbaum","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gleb","family":"Slobodin","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Karina","family":"Zilber","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nina","family":"Boulman","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lisa","family":"Kaly","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Abid","family":"Awisat","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nizar","family":"Jiries","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ofrat","family":"Beyar-Katz","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Doron","family":"Rimar","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.semarthrit.2016.07.007_bib1","first-page":"353","article-title":"Pediatric hereditary autoinflammatory syndromes","volume":"86","author":"Jesus","year":"2010","journal-title":"J Pediatr (Rio J)"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib2","doi-asserted-by":"crossref","first-page":"74","DOI":"10.1182\/asheducation-2005.1.74","article-title":"Hereditary periodic fever syndromes","author":"Kastner","year":"2005","journal-title":"Hematology Am Soc Hematol Educ Program"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib3","doi-asserted-by":"crossref","first-page":"1581","DOI":"10.1093\/hmg\/7.10.1581","article-title":"The hereditary periodic fever syndromes: molecular analysis of a new family of inflammatory diseases","volume":"7","author":"Centola","year":"1998","journal-title":"Hum Mol Genet"},{"issue":"Suppl 1","key":"10.1016\/j.semarthrit.2016.07.007_bib4","doi-asserted-by":"crossref","first-page":"A130","DOI":"10.1186\/1546-0096-11-S1-A130","article-title":"NLRP3 mosaicism as a cause of late-onset CAPS","volume":"11","author":"Zhou","year":"2013","journal-title":"Pediatric Rheumatology"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib5","doi-asserted-by":"crossref","first-page":"1263","DOI":"10.1007\/s00296-011-1840-z","article-title":"Coexistence of vasculitides with familial Mediterranean fever","volume":"31","author":"Aksu","year":"2011","journal-title":"Rheumatol Int"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib6","doi-asserted-by":"crossref","first-page":"1087","DOI":"10.1016\/S0140-6736(84)92505-4","article-title":"Hyperimmunoglobulinaemia D and periodic fever: a new syndrome","volume":"1","author":"Van Der Meer","year":"1984","journal-title":"Lancet"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib7","doi-asserted-by":"crossref","first-page":"138","DOI":"10.1111\/j.1525-1470.2005.22210.x","article-title":"Henoch\u2013Schonlein purpura in a child with hyperimmunoglobulinemia D and periodic fever syndrome","volume":"22","author":"Wickiser","year":"2005","journal-title":"Pediatr Dermatol"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib8","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1001\/archderm.1994.01690010063008","article-title":"Cutaneous manifestations and histologic findings in the hyperimmunoglobulinemia D syndrome. International Hyper IgD Study Group","volume":"130","author":"Drenth","year":"1994","journal-title":"Arch Dermatol"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib9","doi-asserted-by":"crossref","first-page":"1621","DOI":"10.1001\/archderm.1990.01670360085015","article-title":"IgD immune complex vasculitis in a patient with hyperimmunoglobulinemia D and periodic fever","volume":"126","author":"Broom","year":"1990","journal-title":"Arch Dermatol"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib10","first-page":"659","article-title":"Cryopyrin-associated periodic syndrome","volume":"16","author":"Giat","year":"2014","journal-title":"Isr Med Assoc J"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib11","first-page":"116","article-title":"Urticarial vasculitis as a symptom of Muckle\u2013Wells syndrome?","volume":"42","author":"Grassegger","year":"1991","journal-title":"Hautarzt"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib12","doi-asserted-by":"crossref","first-page":"907","DOI":"10.1590\/S0365-05962010000600022","article-title":"Four cases of Muckle\u2013Wells syndrome within the same family","volume":"85","author":"Pereira","year":"2010","journal-title":"Ann Bras Dermatol"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib13","first-page":"2505","article-title":"Diagnosis of Muckle\u2013Wells syndrome\u201433 years later","volume":"34","author":"Fye","year":"2007","journal-title":"J Rheumatol"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib14","doi-asserted-by":"crossref","first-page":"1518","DOI":"10.1136\/ard.2003.016733","article-title":"Small vessel vasculitis and relapsing panniculitis in tumour necrosis factor receptor associated periodic syndrome (TRAPS)","volume":"63","author":"Lamprecht","year":"2004","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib15","doi-asserted-by":"crossref","first-page":"2426","DOI":"10.1056\/NEJMoa0807865","article-title":"An autoinflammatory disease with deficiency of the interleukin-1\u2013receptor antagonist","volume":"360","author":"Aksentijevich","year":"2009","journal-title":"N Engl J Med"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib16","doi-asserted-by":"crossref","first-page":"507","DOI":"10.1056\/NEJMoa1312625","article-title":"Activated STING in a vascular and pulmonary syndrome","volume":"371","author":"Liu","year":"2014","journal-title":"N Engl J Med"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib17","first-page":"394","article-title":"Interleukin-1 activation of vascular endothelium. Effects on procoagulant activity and leukocyte adhesion","volume":"121","author":"Bevilacqua","year":"1985","journal-title":"Am J Pathol"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib18","doi-asserted-by":"crossref","first-page":"4242","DOI":"10.1182\/blood.V84.12.4242.bloodjournal84124242","article-title":"Interleukin-1 induces interleukin-8 secretion from endothelial cells by a juxtacrine mechanism","volume":"84","author":"Kaplanski","year":"1994","journal-title":"Blood"},{"key":"10.1016\/j.semarthrit.2016.07.007_bib19","doi-asserted-by":"crossref","first-page":"168","DOI":"10.1097\/MAJ.0000000000000284","article-title":"Role of interferon alpha in endothelial dysfunction: insights into endothelial nitric oxide synthase\u2013related mechanisms","volume":"348","author":"Jones Buie","year":"2014","journal-title":"Am J Med Sci"}],"container-title":["Seminars in Arthritis and Rheumatism"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0049017216301226?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0049017216301226?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2020,9,24]],"date-time":"2020-09-24T06:12:27Z","timestamp":1600927947000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0049017216301226"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,12]]},"references-count":19,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2016,12]]}},"alternative-id":["S0049017216301226"],"URL":"https:\/\/doi.org\/10.1016\/j.semarthrit.2016.07.007","relation":{},"ISSN":["0049-0172"],"issn-type":[{"value":"0049-0172","type":"print"}],"subject":[],"published":{"date-parts":[[2016,12]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Autoinflammatory associated vasculitis","name":"articletitle","label":"Article Title"},{"value":"Seminars in Arthritis and Rheumatism","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.semarthrit.2016.07.007","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2016 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}