{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,13]],"date-time":"2026-10-13T07:27:24Z","timestamp":1791876444404,"version":"4.3.4"},"reference-count":10,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2017,5,1]],"date-time":"2017-05-01T00:00:00Z","timestamp":1493596800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","sleep-journal.com","clinicalkey.es","clinicalkey.fr","clinicalkey.com.au","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Sleep Medicine"],"published-print":{"date-parts":[[2017,5]]},"DOI":"10.1016\/j.sleep.2017.02.015","type":"journal-article","created":{"date-parts":[[2017,3,10]],"date-time":"2017-03-10T17:16:20Z","timestamp":1489166180000},"page":"165-166","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":9,"special_numbering":"C","title":["Fatal familial insomnia: a video-polysomnographic case report"],"prefix":"10.1016","volume":"33","author":[{"given":"Thomas","family":"Megelin","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1761-5832","authenticated-orcid":false,"given":"Benjamin","family":"Thomas","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Xavier","family":"Ferrer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Imad","family":"Ghorayeb","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.sleep.2017.02.015_bib1","doi-asserted-by":"crossref","first-page":"654","DOI":"10.1136\/jnnp-2013-305978","article-title":"A\u00a0proposal of new diagnostic pathway for fatal familial insomnia","volume":"85","author":"Krasnianski","year":"2014","journal-title":"J\u00a0Neurol, Neurosurg Psychiatry"},{"key":"10.1016\/j.sleep.2017.02.015_bib2","doi-asserted-by":"crossref","first-page":"658","DOI":"10.1002\/ana.21358","article-title":"Fatal familial insomnia: clinical features and early identification","volume":"63","author":"Krasnianski","year":"2008","journal-title":"Ann Neurol"},{"key":"10.1016\/j.sleep.2017.02.015_bib3","doi-asserted-by":"crossref","first-page":"444","DOI":"10.1056\/NEJM199202133260704","article-title":"Fatal familial insomnia, a prion disease with a mutation at codon 178 of the prion protein gene","volume":"326","author":"Medori","year":"1992","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.sleep.2017.02.015_bib4","doi-asserted-by":"crossref","first-page":"555","DOI":"10.1111\/j.1750-3639.1998.tb00180.x","article-title":"The French FFI cases","volume":"8","author":"Julien","year":"1998","journal-title":"Brain Pathol"},{"key":"10.1016\/j.sleep.2017.02.015_bib5","doi-asserted-by":"crossref","first-page":"1491","DOI":"10.1136\/jnnp.2004.056606","article-title":"Phenotypic variability in familial prion diseases due to the D178N mutation","volume":"76","author":"Zarranz","year":"2005","journal-title":"J\u00a0Neurol, Neurosurg Psychiatry"},{"key":"10.1016\/j.sleep.2017.02.015_bib6","doi-asserted-by":"crossref","first-page":"140","DOI":"10.1016\/j.jns.2016.05.039","article-title":"Sexual disinhibition and agrypnia excitata in fatal familial insomnia","volume":"367","author":"de Souza","year":"2016","journal-title":"J\u00a0Neurol Sci"},{"key":"10.1016\/j.sleep.2017.02.015_bib7","first-page":"10171","article-title":"Clinical, histopathological and genetic studies in a case of fatal familial insomnia with review of the literature","volume":"8","author":"Peng","year":"2015","journal-title":"Int J Clin Exp Pathol"},{"key":"10.1016\/j.sleep.2017.02.015_bib8","doi-asserted-by":"crossref","first-page":"607","DOI":"10.1212\/01.wnl.0000266664.68223.40","article-title":"Agrypnia excitata in fatal familial insomnia","volume":"69","author":"Iriarte","year":"2007","journal-title":"A\u00a0Polygr study Neurol"},{"key":"10.1016\/j.sleep.2017.02.015_bib9","doi-asserted-by":"crossref","first-page":"521","DOI":"10.1111\/j.1750-3639.1998.tb00173.x","article-title":"The pathophysiology of fatal familial insomnia","volume":"8","author":"Lugaresi","year":"1998","journal-title":"Brain Pathol"},{"issue":"Suppl 2","key":"10.1016\/j.sleep.2017.02.015_bib10","doi-asserted-by":"crossref","first-page":"S3","DOI":"10.1016\/j.sleep.2011.10.004","article-title":"Agrypnia excitata","volume":"12","author":"Lugaresi","year":"2011","journal-title":"Sleep Med"}],"container-title":["Sleep Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1389945717300977?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1389945717300977?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2019,9,19]],"date-time":"2019-09-19T12:15:38Z","timestamp":1568895338000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1389945717300977"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,5]]},"references-count":10,"alternative-id":["S1389945717300977"],"URL":"https:\/\/doi.org\/10.1016\/j.sleep.2017.02.015","relation":{},"ISSN":["1389-9457"],"issn-type":[{"value":"1389-9457","type":"print"}],"subject":[],"published":{"date-parts":[[2017,5]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Fatal familial insomnia: a video-polysomnographic case report","name":"articletitle","label":"Article Title"},{"value":"Sleep Medicine","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.sleep.2017.02.015","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2017 Elsevier B.V. All rights reserved.","name":"copyright","label":"Copyright"}]}}