{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,4]],"date-time":"2026-10-04T08:46:47Z","timestamp":1791103607126,"version":"4.1.0"},"reference-count":22,"publisher":"Elsevier BV","issue":"4","license":[{"start":{"date-parts":[[2011,5,1]],"date-time":"2011-05-01T00:00:00Z","timestamp":1304208000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Transplantation Proceedings"],"published-print":{"date-parts":[[2011,5]]},"DOI":"10.1016\/j.transproceed.2011.01.129","type":"journal-article","created":{"date-parts":[[2011,6,6]],"date-time":"2011-06-06T14:10:17Z","timestamp":1307369417000},"page":"1181-1183","source":"Crossref","is-referenced-by-count":56,"title":["Glycogen Storage Disease Type Ia and VI Associated With Hepatocellular Carcinoma: Two Case Reports"],"prefix":"10.1016","volume":"43","author":[{"given":"T.M.","family":"Manzia","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R.","family":"Angelico","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"L.","family":"Toti","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.","family":"Cillis","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"P.","family":"Ciano","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G.","family":"Orlando","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.","family":"Anselmo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"M.","family":"Angelico","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G.","family":"Tisone","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.transproceed.2011.01.129_bib1","doi-asserted-by":"crossref","first-page":"101","DOI":"10.2174\/1566524024605761","article-title":"Glycogen and its metabolism","volume":"2","author":"Roach","year":"2002","journal-title":"Curr Mol Med"},{"key":"10.1016\/j.transproceed.2011.01.129_bib2","series-title":"The Metabolic and Molecular Basis of Inherited Diseases","first-page":"1521","article-title":"Glycogen storage disease","author":"Chen","year":"2001"},{"key":"10.1016\/j.transproceed.2011.01.129_bib3","doi-asserted-by":"crossref","first-page":"2541","DOI":"10.3748\/wjg.v13.i18.2541","article-title":"Glycogen storage diseases: new perspectives","volume":"13","author":"Bayraktar","year":"2007","journal-title":"World J Gastroenterol"},{"issue":"Suppl 1","key":"10.1016\/j.transproceed.2011.01.129_bib4","doi-asserted-by":"crossref","first-page":"S112","DOI":"10.1007\/BF02680007","article-title":"Guidelines for management of glycogen storage disease type I\u2014European Study on Glycogen Storage Disease Type I (ESGSD I)","volume":"161","author":"Rake","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.transproceed.2011.01.129_bib5","doi-asserted-by":"crossref","first-page":"513","DOI":"10.1042\/0264-6021:3620513","article-title":"The glucose-6-phosphate system","volume":"362","author":"Van Schftingen","year":"2002","journal-title":"Biochem J"},{"issue":"Suppl 1","key":"10.1016\/j.transproceed.2011.01.129_bib6","doi-asserted-by":"crossref","first-page":"S20","DOI":"10.1007\/BF02679990","article-title":"Glycogen storage disease type I: diagnosis, management, clinical course and outcome","volume":"161","author":"Rake","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.transproceed.2011.01.129_bib7","doi-asserted-by":"crossref","first-page":"785","DOI":"10.1086\/301790","article-title":"Mutations in the liver glycogen phosphorylase gene (PYGL) underlying glycogenosis type VI","volume":"62","author":"Burwinkel","year":"1998","journal-title":"Am J Hum Genet"},{"key":"10.1016\/j.transproceed.2011.01.129_bib8","doi-asserted-by":"crossref","first-page":"483","DOI":"10.1016\/j.jhep.2009.05.026","article-title":"Liver transplantation for glycogen storage disease type Ia","volume":"51","author":"Reddy","year":"2009","journal-title":"J Hepatol"},{"key":"10.1016\/j.transproceed.2011.01.129_bib9","first-page":"166","article-title":"Hepatic adenoma in type Ia glycogen storage disease","volume":"111","author":"Coire","year":"1987","journal-title":"Arch Pathol Lab Med"},{"key":"10.1016\/j.transproceed.2011.01.129_bib10","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1007\/s10545-005-7500-2","article-title":"Hepatocellular carcinoma in glycogen storage disease type Ia: a case series","volume":"288","author":"Franco","year":"2005","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.transproceed.2011.01.129_bib11","doi-asserted-by":"crossref","first-page":"879","DOI":"10.1111\/j.1432-2277.2003.tb00258.x","article-title":"Glycogenosis storage type I diseases and evolutive adenomatosis: an indication for liver transplantation","volume":"16","author":"Lerut","year":"2003","journal-title":"Transpl Int"},{"key":"10.1016\/j.transproceed.2011.01.129_bib12","doi-asserted-by":"crossref","first-page":"276","DOI":"10.1097\/00005176-199703000-00008","article-title":"Hepatocellular adenomas in glycogen storage disease type I and III: a series of 43 patients and review of the literature","volume":"24","author":"Labrune","year":"1997","journal-title":"J Pediatr Gastroenterol Nutr"},{"key":"10.1016\/j.transproceed.2011.01.129_bib13","doi-asserted-by":"crossref","first-page":"142","DOI":"10.1016\/S1096-7192(03)00068-4","article-title":"A novel mutation (G233D) in the glycogen storage disease and residual enzyme activity","volume":"79","author":"Tang","year":"2003","journal-title":"Mol Genet Metab"},{"key":"10.1016\/j.transproceed.2011.01.129_bib14","doi-asserted-by":"crossref","first-page":"S40","DOI":"10.1007\/BF02679992","article-title":"Type I glycogen storage disease: favourable outcome on a strict management regimen avoiding increased lactate production during childhood and adolescence","volume":"161","author":"Daublin","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.transproceed.2011.01.129_bib15","doi-asserted-by":"crossref","first-page":"S35","DOI":"10.1007\/BF02679991","article-title":"Effect of continuous glucose therapy with uncooked cornstarch on the long-term clinical course of type Ia glycogen storage disease","volume":"161","author":"Weinstein","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.transproceed.2011.01.129_bib16","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1007\/s10545-007-0519-9","article-title":"Glycogen storage disease types I and III: treatment updates","volume":"30","author":"Koeberl","year":"2007","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.transproceed.2011.01.129_bib17","doi-asserted-by":"crossref","first-page":"658","DOI":"10.1016\/j.jhep.2007.05.012","article-title":"Resection of hepatocellular adenoma in patients with glycogen storage disease type Ia","volume":"47","author":"Reddy","year":"2007","journal-title":"J Hepatol"},{"key":"10.1016\/j.transproceed.2011.01.129_bib18","doi-asserted-by":"crossref","first-page":"723","DOI":"10.1023\/A:1005544117285","article-title":"Long-term outcome of liver transplantation in patients with glycogen storage disease type Ia","volume":"22","author":"Faivre","year":"1999","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.transproceed.2011.01.129_bib19","doi-asserted-by":"crossref","first-page":"S53","DOI":"10.1007\/BF02679995","article-title":"Glycogen storage disease type I: indications for liver and\/or kidney transplantation","volume":"161","author":"Labrune","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.transproceed.2011.01.129_bib20","doi-asserted-by":"crossref","first-page":"848","DOI":"10.1002\/lt.21151","article-title":"Long-term results of living donor liver transplantation for glycogen storage disorders in children","volume":"13","author":"Shridhar","year":"2007","journal-title":"Liver Traspl"},{"key":"10.1016\/j.transproceed.2011.01.129_bib21","doi-asserted-by":"crossref","first-page":"42","DOI":"10.1111\/j.1399-3046.2005.00395.x","article-title":"Hepatocellular carcinoma in children and effect of living-donor liver transplantation on outcome","volume":"10","author":"Arikan","year":"2006","journal-title":"Pediatr Transplant"},{"key":"10.1016\/j.transproceed.2011.01.129_bib22","doi-asserted-by":"crossref","first-page":"266","DOI":"10.1080\/08998280.2008.11928410","article-title":"Hepatocellular carcinoma: management of an increasingly common problem","volume":"21","author":"Davis","year":"2008","journal-title":"Proc (Bayl Univ Med Cent)"}],"container-title":["Transplantation Proceedings"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0041134511002132?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0041134511002132?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2019,6,11]],"date-time":"2019-06-11T08:59:50Z","timestamp":1560243590000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0041134511002132"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,5]]},"references-count":22,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2011,5]]}},"alternative-id":["S0041134511002132"],"URL":"https:\/\/doi.org\/10.1016\/j.transproceed.2011.01.129","relation":{},"ISSN":["0041-1345"],"issn-type":[{"value":"0041-1345","type":"print"}],"subject":[],"published":{"date-parts":[[2011,5]]}}}