{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T12:13:08Z","timestamp":1777637588781,"version":"3.51.4"},"reference-count":15,"publisher":"Elsevier BV","issue":"10","license":[{"start":{"date-parts":[[2016,12,1]],"date-time":"2016-12-01T00:00:00Z","timestamp":1480550400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","transplantation-proceedings.org","clinicalkey.es","clinicalkey.com.au","clinicalkey.fr","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Transplantation Proceedings"],"published-print":{"date-parts":[[2016,12]]},"DOI":"10.1016\/j.transproceed.2016.08.047","type":"journal-article","created":{"date-parts":[[2016,12,6]],"date-time":"2016-12-06T04:22:37Z","timestamp":1480998157000},"page":"3323-3327","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":10,"title":["Liver Transplantation in Polish Children With \u03b11-Antitrypsin Deficiency: A Single-Center Experience"],"prefix":"10.1016","volume":"48","author":[{"given":"A.","family":"Bakula","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J.","family":"Pawlowska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"O.","family":"Niewiadomska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"I.","family":"Jankowska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M.","family":"Teisseyre","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P.","family":"Kalici\u0144ski","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P.","family":"Socha","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.transproceed.2016.08.047_bib1","doi-asserted-by":"crossref","first-page":"77","DOI":"10.1183\/09031936.06.00062305","article-title":"Estimated numbers and prevalence of PI*S and PI*Z alleles of a-1-antitrypsin deficiency in European countries","volume":"27","author":"Blanco","year":"2006","journal-title":"Eur Respir J"},{"key":"10.1016\/j.transproceed.2016.08.047_bib2","doi-asserted-by":"crossref","first-page":"2520","DOI":"10.1016\/j.rmed.2007.06.032","article-title":"The prevalence of alpha-1 antitrypsin deficiency in a representative population sample from Poland","volume":"101","author":"Kaczor","year":"2007","journal-title":"Respir Med"},{"key":"10.1016\/j.transproceed.2016.08.047_bib3","doi-asserted-by":"crossref","first-page":"986","DOI":"10.1016\/S0168-8278(00)80103-8","article-title":"Prognosis of alpha-1-antitrypsin deficiency-related liver disease in the era of paediatric liver transplantation","volume":"32","author":"Francavilla","year":"2000","journal-title":"J\u00a0Hepatol"},{"key":"10.1016\/j.transproceed.2016.08.047_bib4","doi-asserted-by":"crossref","first-page":"731","DOI":"10.1111\/j.1399-0012.2010.01371.x","article-title":"Long-term outcome in 42 pediatric liver transplant patients with alpha-1antitrypsin deficiency: a single center experience","volume":"25","author":"Hughes","year":"2011","journal-title":"Clin Transplant"},{"key":"10.1016\/j.transproceed.2016.08.047_bib5","first-page":"3798","article-title":"Orthotopic liver transplantation for alpha-1-antitrypsin deficiency: an experience in 29 children and ten adults","volume":"19","author":"Esquivel","year":"1987","journal-title":"Transplant Proc"},{"key":"10.1016\/j.transproceed.2016.08.047_bib6","doi-asserted-by":"crossref","first-page":"886","DOI":"10.1002\/lt.24434","article-title":"Is severe progressive liver disease caused by alpha-1-antitrypsin deficiency more common in children or adults?","volume":"22","author":"Chu","year":"2016","journal-title":"Liver Transpl"},{"key":"10.1016\/j.transproceed.2016.08.047_bib7","doi-asserted-by":"crossref","first-page":"847","DOI":"10.1111\/j.1651-2227.1988.tb10767.x","article-title":"The natural history of liver disease in alpha-1-antitrypsin deficient children","volume":"77","author":"Sveger","year":"1988","journal-title":"Acta Pediatr Scand"},{"key":"10.1016\/j.transproceed.2016.08.047_bib8","first-page":"669","article-title":"Change in alpha 1-antitrypsin phenotype after orthotopic liver transplant","volume":"66","author":"Van Furth","year":"1986","journal-title":"Clin Exp Immunol"},{"key":"10.1016\/j.transproceed.2016.08.047_bib9","doi-asserted-by":"crossref","first-page":"207","DOI":"10.1111\/j.1432-2277.2000.tb01068.x","article-title":"Liver transplantation for alpha-1-antitrypsin deficiency in children","volume":"13","author":"Prachalias","year":"2000","journal-title":"Transpl Int"},{"key":"10.1016\/j.transproceed.2016.08.047_bib10","series-title":"Japan Medical Research Foundation, editor. Cholestasis in Infancy","first-page":"133","article-title":"The prognosis in childhood of liver disease associated with alpha-1-antitrypsin deficiency (PiZZ)","author":"Psacharopoulos","year":"1980"},{"key":"10.1016\/j.transproceed.2016.08.047_bib11","doi-asserted-by":"crossref","first-page":"3186","DOI":"10.1016\/j.transproceed.2007.09.046","article-title":"Good and bad prognosis of alpha-1-antitrypsin deficiency in children: when to list for liver transplantation","volume":"39","author":"Bakula","year":"2007","journal-title":"Transplant Proc"},{"key":"10.1016\/j.transproceed.2016.08.047_bib12","doi-asserted-by":"crossref","first-page":"882","DOI":"10.1136\/adc.58.11.882","article-title":"Outcome of liver disease associated with \u03b1-1-antitrypsin deficiency (PiZ)","volume":"58","author":"Psacharopoulos","year":"1983","journal-title":"Arch Dis Child"},{"key":"10.1016\/j.transproceed.2016.08.047_bib13","doi-asserted-by":"crossref","first-page":"966","DOI":"10.1111\/j.1651-2227.1991.tb11763.x","article-title":"Late haemorrhagic disease in Sweden 1987-89","volume":"80","author":"Ekelund","year":"1991","journal-title":"Acta Paediatr Scand"},{"key":"10.1016\/j.transproceed.2016.08.047_bib14","doi-asserted-by":"crossref","first-page":"661","DOI":"10.1016\/S0022-3476(83)80230-3","article-title":"Early assessment of evolution of liver disease associated with alpha-1-antitrypsin deficiency in childhood","volume":"102","author":"Nebbia","year":"1983","journal-title":"J\u00a0Pediatr"},{"key":"10.1016\/j.transproceed.2016.08.047_bib15","doi-asserted-by":"crossref","first-page":"864","DOI":"10.1016\/S0022-3476(05)80123-4","article-title":"Liver disease in alpha-1-antitrypsin deficiency: prognostic indicators","volume":"117","author":"Ibarguen","year":"1990","journal-title":"J\u00a0Pediatr"}],"container-title":["Transplantation Proceedings"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0041134516307023?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0041134516307023?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,9,6]],"date-time":"2018-09-06T05:51:27Z","timestamp":1536213087000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0041134516307023"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,12]]},"references-count":15,"journal-issue":{"issue":"10","published-print":{"date-parts":[[2016,12]]}},"alternative-id":["S0041134516307023"],"URL":"https:\/\/doi.org\/10.1016\/j.transproceed.2016.08.047","relation":{},"ISSN":["0041-1345"],"issn-type":[{"value":"0041-1345","type":"print"}],"subject":[],"published":{"date-parts":[[2016,12]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Liver Transplantation in Polish Children With \u03b11-Antitrypsin Deficiency: A Single-Center Experience","name":"articletitle","label":"Article Title"},{"value":"Transplantation Proceedings","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.transproceed.2016.08.047","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2016 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}