{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,15]],"date-time":"2026-04-15T19:14:30Z","timestamp":1776280470549,"version":"3.50.1"},"reference-count":27,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2017,12,1]],"date-time":"2017-12-01T00:00:00Z","timestamp":1512086400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","worldneurosurgery.org","clinicalkey.es","clinicalkey.fr","clinicalkey.com.au","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["World Neurosurgery"],"published-print":{"date-parts":[[2017,12]]},"DOI":"10.1016\/j.wneu.2017.08.176","type":"journal-article","created":{"date-parts":[[2017,9,5]],"date-time":"2017-09-05T17:00:46Z","timestamp":1504630846000},"page":"291-302","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":24,"special_numbering":"C","title":["Moyamoya Vasculopathy in PHACE Syndrome: Six New Cases and Review of the Literature"],"prefix":"10.1016","volume":"108","author":[{"given":"Domenico","family":"Tortora","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4730-5322","authenticated-orcid":false,"given":"Mariasavina","family":"Severino","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andrea","family":"Accogli","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4120-7350","authenticated-orcid":false,"given":"Carola","family":"Martinetti","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nadia","family":"Vercellino","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Valeria","family":"Capra","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andrea","family":"Rossi","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7312-0204","authenticated-orcid":false,"given":"Marco","family":"Pavanello","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.wneu.2017.08.176_bib1","doi-asserted-by":"crossref","first-page":"307","DOI":"10.1001\/archderm.1996.03890270083012","article-title":"PHACE syndrome. The association of posterior fossa brain malformations, hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, and eye abnormalities","volume":"132","author":"Frieden","year":"1996","journal-title":"Arch Dermatol"},{"key":"10.1016\/j.wneu.2017.08.176_bib2","first-page":"461","article-title":"Hemangiomas of the head, neck, and chest with associated vascular and brain anomalies: a complex neurocutaneous syndrome","volume":"17","author":"Pascual-Castroviejo","year":"1996","journal-title":"AJNR Am J Neuroradiol"},{"key":"10.1016\/j.wneu.2017.08.176_bib3","doi-asserted-by":"crossref","first-page":"381","DOI":"10.1111\/j.1525-1470.2009.00944.x","article-title":"PHACE syndrome: current knowledge, future directions","volume":"26","author":"Metry","year":"2009","journal-title":"Pediatr Dermatol"},{"key":"10.1016\/j.wneu.2017.08.176_bib4","doi-asserted-by":"crossref","first-page":"975","DOI":"10.1002\/ajmg.a.31189","article-title":"A\u00a0prospective study of PHACE syndrome in infantile hemangiomas: demographic features, clinical findings, and complications","volume":"140","author":"Metry","year":"2006","journal-title":"Am J Med Genet A"},{"key":"10.1016\/j.wneu.2017.08.176_bib5","doi-asserted-by":"crossref","first-page":"148","DOI":"10.1055\/s-0029-1239507","article-title":"Congenital and evolving vascular disorders associated with cutaneous hemangiomas: case report","volume":"40","author":"Pascual-Castroviejo","year":"2009","journal-title":"Neuropediatrics"},{"key":"10.1016\/j.wneu.2017.08.176_bib6","doi-asserted-by":"crossref","first-page":"308","DOI":"10.1161\/STROKEAHA.107.485185","article-title":"The cerebral vasculopathy of PHACES syndrome","volume":"39","author":"Heyer","year":"2008","journal-title":"Stroke"},{"key":"10.1016\/j.wneu.2017.08.176_bib7","doi-asserted-by":"crossref","first-page":"601","DOI":"10.1148\/radiology.207.3.9609880","article-title":"Cerebral vasculopathy and neurologic sequelae in infants with cervicofacial hemangioma: report of eight patients","volume":"207","author":"Burrows","year":"1998","journal-title":"Radiology"},{"key":"10.1016\/j.wneu.2017.08.176_bib8","doi-asserted-by":"crossref","first-page":"934","DOI":"10.1007\/s002340100594","article-title":"Posterior fossa and arterial abnormalities in patients with facial capillary haemangioma: presumed incomplete phenotypic expression of PHACES syndrome","volume":"43","author":"Rossi","year":"2001","journal-title":"Neuroradiology"},{"key":"10.1016\/j.wneu.2017.08.176_bib9","first-page":"1602","article-title":"Agenesis of bilateral internal carotid arteries in the PHACE syndrome","volume":"27","author":"Rossi","year":"2006","journal-title":"AJNR Am J Neuroradiol"},{"key":"10.1016\/j.wneu.2017.08.176_bib10","doi-asserted-by":"crossref","first-page":"1980","DOI":"10.3174\/ajnr.A2206","article-title":"Cervical and intracranial arterial anomalies in 70 patients with PHACE syndrome","volume":"31","author":"Hess","year":"2010","journal-title":"AJNR Am J Neuroradiol"},{"key":"10.1016\/j.wneu.2017.08.176_bib11","doi-asserted-by":"crossref","first-page":"19271","DOI":"10.5070\/D3198019271","article-title":"PHACES syndrome with moyamoya vasculopathy \u2014a case report","volume":"19","author":"Sathishkumar","year":"2013","journal-title":"Dermatol Online J"},{"key":"10.1016\/j.wneu.2017.08.176_bib12","doi-asserted-by":"crossref","first-page":"2557","DOI":"10.1002\/ajmg.a.38258","article-title":"RNF213 variants in a child with PHACE syndrome and moyamoya vasculopathy","volume":"173","author":"Schilter","year":"2017","journal-title":"Am J Med Genet A"},{"key":"10.1016\/j.wneu.2017.08.176_bib13","doi-asserted-by":"crossref","first-page":"24","DOI":"10.1016\/j.jpeds.2016.07.054","article-title":"PHACE syndrome: consensus-derived diagnosis and care recommendations","volume":"178","author":"Garzon","year":"2016","journal-title":"J\u00a0Pediatr"},{"key":"10.1016\/j.wneu.2017.08.176_bib14","doi-asserted-by":"crossref","first-page":"419","DOI":"10.1016\/j.pediatrneurol.2006.06.021","article-title":"The neurologic aspects of PHACE: case report and review of the literature","volume":"35","author":"Heyer","year":"2006","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.wneu.2017.08.176_bib15","doi-asserted-by":"crossref","first-page":"70","DOI":"10.3171\/2015.5.PEDS1578","article-title":"Bilateral pial synangiosis in a child with PHACE syndrome","volume":"17","author":"Jack","year":"2016","journal-title":"J\u00a0Neurosurg Pediatr"},{"key":"10.1016\/j.wneu.2017.08.176_bib16","doi-asserted-by":"crossref","first-page":"959","DOI":"10.1542\/peds.2005-1683","article-title":"Early stroke and cerebral vasculopathy in children with facial hemangiomas and PHACE association","volume":"117","author":"Drolet","year":"2006","journal-title":"Pediatrics"},{"key":"10.1016\/j.wneu.2017.08.176_bib17","doi-asserted-by":"crossref","first-page":"227","DOI":"10.1007\/s00234-002-0902-z","article-title":"PHACES syndrome: a review of eight previously unreported cases with late arterial occlusions","volume":"46","author":"Bhattacharya","year":"2004","journal-title":"Neuroradiology"},{"key":"10.1016\/j.wneu.2017.08.176_bib18","doi-asserted-by":"crossref","first-page":"313","DOI":"10.1016\/S0090-3019(81)80017-1","article-title":"A\u00a0new surgical treatment of moyamoya disease in children: a preliminary report","volume":"15","author":"Matsushima","year":"1981","journal-title":"Surg Neurol"},{"key":"10.1016\/j.wneu.2017.08.176_bib19","doi-asserted-by":"crossref","first-page":"29","DOI":"10.2176\/nmc.17pt1.29","article-title":"A\u00a0surgical treatment of \u201cmoyamoya\u201d disease, \u201cencephalo-myo synangiosis\u201d","volume":"17","author":"Karasawa","year":"1977","journal-title":"Neurol Med Chir"},{"key":"10.1016\/j.wneu.2017.08.176_bib20","doi-asserted-by":"crossref","first-page":"1672","DOI":"10.1161\/STROKEAHA.112.650952","article-title":"Stroke in children with posterior fossa brain malformations, hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, and eye abnormalities (PHACE) syndrome: a systematic review of the literature","volume":"43","author":"Siegel","year":"2012","journal-title":"Stroke"},{"key":"10.1016\/j.wneu.2017.08.176_bib21","first-page":"1","article-title":"Direct versus indirect bypasses for adult ischemic-type moyamoya disease: a propensity score-matched analysis","author":"Deng","year":"2017","journal-title":"J\u00a0Neurosurg"},{"key":"10.1016\/j.wneu.2017.08.176_bib22","doi-asserted-by":"crossref","first-page":"691","DOI":"10.1016\/j.wneu.2015.01.016","article-title":"The importance of encephalo-myo-synangiosis in surgical revascularization strategies for moyamoya disease in children and adults","volume":"83","author":"Imai","year":"2015","journal-title":"World Neurosurg"},{"key":"10.1016\/j.wneu.2017.08.176_bib23","doi-asserted-by":"crossref","first-page":"73","DOI":"10.3171\/2010.4.PEDS09478","article-title":"Postoperative neurological deterioration in pediatric moyamoya disease: watershed shift and hyperperfusion","volume":"6","author":"Hayashi","year":"2010","journal-title":"J\u00a0Neurosurg Pediatr"},{"issue":"2 Suppl Pediatrics","key":"10.1016\/j.wneu.2017.08.176_bib24","doi-asserted-by":"crossref","first-page":"142","DOI":"10.3171\/ped.2004.100.2.0142","article-title":"Long-term outcome in children with moyamoya syndrome after cranial revascularization by pial synangiosis","volume":"100","author":"Scott","year":"2004","journal-title":"J\u00a0Neurosurg"},{"key":"10.1016\/j.wneu.2017.08.176_bib25","doi-asserted-by":"crossref","first-page":"1227","DOI":"10.1002\/lt.24187","article-title":"Pretransplant management of basilar artery aneurysm and moyamoya disease in a child with Alagille syndrome","volume":"21","author":"Pavanello","year":"2015","journal-title":"Liver Transpl"},{"key":"10.1016\/j.wneu.2017.08.176_bib26","first-page":"1","article-title":"Direct versus indirect revascularization procedures for moyamoya disease: a comparative effectiveness study","volume":"29","author":"Macyszyn","year":"2016","journal-title":"J\u00a0Neurosurg"},{"key":"10.1016\/j.wneu.2017.08.176_bib27","doi-asserted-by":"crossref","first-page":"1041","DOI":"10.1007\/s00381-012-1743-7","article-title":"Surgical revascularisation for childhood moyamoya","volume":"28","author":"Ng","year":"2012","journal-title":"Childs Nerv Syst"}],"container-title":["World Neurosurgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1878875017314869?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1878875017314869?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2023,8,25]],"date-time":"2023-08-25T13:15:10Z","timestamp":1692969310000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1878875017314869"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,12]]},"references-count":27,"alternative-id":["S1878875017314869"],"URL":"https:\/\/doi.org\/10.1016\/j.wneu.2017.08.176","relation":{},"ISSN":["1878-8750"],"issn-type":[{"value":"1878-8750","type":"print"}],"subject":[],"published":{"date-parts":[[2017,12]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Moyamoya Vasculopathy in PHACE Syndrome: Six New Cases and Review of the Literature","name":"articletitle","label":"Article Title"},{"value":"World Neurosurgery","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.wneu.2017.08.176","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2017 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}