{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,12]],"date-time":"2026-02-12T09:19:28Z","timestamp":1770887968711,"version":"3.50.1"},"reference-count":20,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2018,7,1]],"date-time":"2018-07-01T00:00:00Z","timestamp":1530403200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","worldneurosurgery.org","clinicalkey.es","clinicalkey.fr","clinicalkey.com.au","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["World Neurosurgery"],"published-print":{"date-parts":[[2018,7]]},"DOI":"10.1016\/j.wneu.2018.04.144","type":"journal-article","created":{"date-parts":[[2018,4,27]],"date-time":"2018-04-27T13:43:41Z","timestamp":1524836621000},"page":"225-228","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":4,"special_numbering":"C","title":["Case Report of Worth Syndrome and Chiari I Malformation: Unusual Association and Surgical Treatment"],"prefix":"10.1016","volume":"115","author":[{"given":"Martin Andres","family":"Merenzon","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Matias Agustin","family":"Dorman","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pablo","family":"Zuliani Sampaolesi","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pablo Alejandro","family":"Seoane","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fernando","family":"Latorre","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Eduardo Roberto","family":"Seoane","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.wneu.2018.04.144_bib1","doi-asserted-by":"crossref","first-page":"547","DOI":"10.1148\/125.2.547","article-title":"Autosomal dominant osteosclerosis","volume":"125","author":"Gorlin","year":"1977","journal-title":"Radiology"},{"key":"10.1016\/j.wneu.2018.04.144_bib2","doi-asserted-by":"crossref","first-page":"161","DOI":"10.1111\/j.1399-0004.1987.tb02789.x","article-title":"Autosomal dominant endosteal hyperostosis","volume":"31","author":"Perez-Vicente","year":"1987","journal-title":"Clin Genet"},{"key":"10.1016\/j.wneu.2018.04.144_bib3","doi-asserted-by":"crossref","first-page":"46","DOI":"10.1002\/ajmg.1320510111","article-title":"Neurological involvement in Worth type endosteal hyperostosis: report of a family","volume":"51","author":"Ades","year":"1994","journal-title":"Am J Med Genet"},{"key":"10.1016\/j.wneu.2018.04.144_bib4","doi-asserted-by":"crossref","first-page":"600","DOI":"10.1016\/S1079-2104(99)70141-1","article-title":"Autosomal dominant osteosclerosis. Report of a kindred","volume":"87","author":"Curran","year":"1999","journal-title":"Oral Surg Oral Med Oral Pathol Oral Radiol Endod"},{"key":"10.1016\/j.wneu.2018.04.144_bib5","first-page":"2703","article-title":"Dominant generalized cortical hyperostosis with multiple involvement of the cranial nerves","volume":"5","author":"Lapresle","year":"1976","journal-title":"Nouv Presse Med"},{"key":"10.1016\/j.wneu.2018.04.144_bib6","first-page":"151","article-title":"Endosteal hyperostosis with dominant transmission. Description of 8 cases in 3 generations of the same nuclear family","volume":"68","author":"Moretti","year":"1981","journal-title":"Radiol Med"},{"key":"10.1016\/j.wneu.2018.04.144_bib7","first-page":"2849","article-title":"Cortical generalized hyperostosis. An observation","volume":"7","author":"Demonchy","year":"1978","journal-title":"Nouv Presse Med"},{"key":"10.1016\/j.wneu.2018.04.144_bib8","first-page":"275","article-title":"International nomenclature of constitutional diseases of bone","volume":"27","author":"Beighton","year":"1984","journal-title":"Ann Radiol"},{"key":"10.1016\/j.wneu.2018.04.144_bib9","doi-asserted-by":"crossref","first-page":"2650","DOI":"10.1210\/jc.2001-011428","article-title":"Autosomal dominant hyperostosis\/osteosclerosis with high serum alkaline phosphatase activity","volume":"88","author":"Hernandez-Cassis","year":"2003","journal-title":"J\u00a0Clin Endocrinol Metab"},{"key":"10.1016\/j.wneu.2018.04.144_bib10","doi-asserted-by":"crossref","first-page":"763","DOI":"10.1086\/368277","article-title":"Six novel missense mutations in the LDL receptor-related protein 5 (LRP5) gene in different conditions with an increased bone density","volume":"72","author":"Van Wesenbeeck","year":"2003","journal-title":"Am J Hum Genet"},{"key":"10.1016\/j.wneu.2018.04.144_bib11","first-page":"67","article-title":"Hyperostosis corticalis generalisata congenita","volume":"17","author":"Worth","year":"1966","journal-title":"J\u00a0Can Assoc Radiol"},{"key":"10.1016\/j.wneu.2018.04.144_bib12","doi-asserted-by":"crossref","first-page":"157","DOI":"10.1016\/j.surneu.2008.02.030","article-title":"Acquired Chiari malformation secondary to hyperostosis of the skull: a case report and literature review","volume":"72","author":"Albert","year":"2009","journal-title":"Surg Neurol"},{"issue":"suppl 1","key":"10.1016\/j.wneu.2018.04.144_bib13","first-page":"E212","article-title":"Aggressive cranial vault decompression for cranial hyperostosis: technical case report of two cases","volume":"57","author":"Mocco","year":"2005","journal-title":"Neurosurgery"},{"key":"10.1016\/j.wneu.2018.04.144_bib14","doi-asserted-by":"crossref","first-page":"83","DOI":"10.1080\/02688690701658737","article-title":"Foramen magnum decompression and expansile duroplasty for acquired Chiari type I malformation in craniometaphyseal dysplasia","volume":"22","author":"Sewell","year":"2008","journal-title":"Br J Neurosurg"},{"key":"10.1016\/j.wneu.2018.04.144_bib15","doi-asserted-by":"crossref","first-page":"198","DOI":"10.1055\/s-2008-1038536","article-title":"Chiari malformation caused by craniometaphyseal dysplasia: case report and review of the literature","volume":"18","author":"Cai","year":"2008","journal-title":"Eur J Pediatr Surg"},{"key":"10.1016\/j.wneu.2018.04.144_bib16","doi-asserted-by":"crossref","first-page":"960","DOI":"10.1097\/00006123-199710000-00039","article-title":"Foramen magnum decompression for cervicomedullary encroachment in craneiometaphyseal dysplasia: case report","volume":"41","author":"Day","year":"1997","journal-title":"Neurosurgery"},{"key":"10.1016\/j.wneu.2018.04.144_bib17","doi-asserted-by":"crossref","first-page":"E6","DOI":"10.3171\/2011.4.FOCUS1126","article-title":"Intracranial hypertension in two cases of craniometaphyseal displasia: differing surgical options","volume":"31","author":"Rivero-Garv\u00eda","year":"2011","journal-title":"Neurosurg Focus"},{"key":"10.1016\/j.wneu.2018.04.144_bib18","doi-asserted-by":"crossref","first-page":"369","DOI":"10.3171\/2011.1.PEDS10353","article-title":"Osteopetrosis with Chiari I malformation: presentation and surgical management","volume":"7","author":"Dlouhy","year":"2011","journal-title":"J\u00a0Neurosurg Pediatr"},{"key":"10.1016\/j.wneu.2018.04.144_bib19","doi-asserted-by":"crossref","first-page":"E2","DOI":"10.3171\/foc.2001.11.1.3","article-title":"Surgical treatment of Chiari I malformation: indication and approaches","volume":"11","author":"Alden","year":"2001","journal-title":"Neurosurg Focus"},{"key":"10.1016\/j.wneu.2018.04.144_bib20","doi-asserted-by":"crossref","first-page":"647","DOI":"10.3171\/2010.11.JNS102148","article-title":"Posterior fossa volume increase after surgery for Chiari malformation type I: a quantitative assessment using magnetic resonance imaging and correlations with the treatment response","volume":"115","author":"Noudel","year":"2011","journal-title":"J\u00a0Neurosurg"}],"container-title":["World Neurosurgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1878875018308647?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1878875018308647?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,6,26]],"date-time":"2018-06-26T15:47:20Z","timestamp":1530028040000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1878875018308647"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,7]]},"references-count":20,"alternative-id":["S1878875018308647"],"URL":"https:\/\/doi.org\/10.1016\/j.wneu.2018.04.144","relation":{},"ISSN":["1878-8750"],"issn-type":[{"value":"1878-8750","type":"print"}],"subject":[],"published":{"date-parts":[[2018,7]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Case Report of Worth Syndrome and Chiari I Malformation: Unusual Association and Surgical Treatment","name":"articletitle","label":"Article Title"},{"value":"World Neurosurgery","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.wneu.2018.04.144","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2018 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}