{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T10:52:57Z","timestamp":1787741577829,"version":"build-2784847793"},"reference-count":43,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2015,1,1]],"date-time":"2015-01-01T00:00:00Z","timestamp":1420070400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2014,11,19]],"date-time":"2014-11-19T00:00:00Z","timestamp":1416355200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/3.0\/"}],"funder":[{"DOI":"10.13039\/100008484","name":"BioMarin Pharmaceutical Inc","doi-asserted-by":"crossref","id":[{"id":"10.13039\/100008484","id-type":"DOI","asserted-by":"crossref"}]}],"content-domain":{"domain":["mgmjournal.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Molecular Genetics and Metabolism"],"published-print":{"date-parts":[[2015,1]]},"DOI":"10.1016\/j.ymgme.2014.10.010","type":"journal-article","created":{"date-parts":[[2014,10,30]],"date-time":"2014-10-30T19:01:19Z","timestamp":1414695679000},"page":"11-18","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":46,"title":["Diagnostic evaluation, monitoring, and perioperative management of spinal cord compression in patients with Morquio syndrome"],"prefix":"10.1016","volume":"114","author":[{"given":"Joel","family":"Charrow","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tord D.","family":"Alden","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Catherine Ann R.","family":"Breathnach","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Geoffrey P.","family":"Frawley","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christian J.","family":"Hendriksz","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bianca","family":"Link","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"William G.","family":"Mackenzie","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Renzo","family":"Manara","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8991-5036","authenticated-orcid":false,"given":"Amaka C.","family":"Offiah","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Martha L.","family":"Solano","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mary","family":"Theroux","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.ymgme.2014.10.010_bb0005","series-title":"Online Mendelian Inheritance in Man, OMIM","year":"2008"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0010","series-title":"Online Mendelian Inheritance in Man, OMIM","year":"1986"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0015","author":"ExPASy"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0020","doi-asserted-by":"crossref","first-page":"335","DOI":"10.1042\/bj2030335","article-title":"Impaired degradation of keratan sulphate by Morquio A fibroblasts","volume":"203","author":"Glossl","year":"1982","journal-title":"Biochem. J."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0025","doi-asserted-by":"crossref","first-page":"759","DOI":"10.1016\/0006-291X(74)91022-5","article-title":"Morquio's syndrome: deficiency of a chondroitin sulfate N-acetylhexosamine sulfate sulfatase","volume":"61","author":"Matalon","year":"1974","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0030","doi-asserted-by":"crossref","first-page":"301","DOI":"10.1016\/j.ymgme.2013.04.009","article-title":"Pathogenesis of Morquio A syndrome: an autopsied case reveals systemic storage disorder","volume":"109","author":"Yasuda","year":"2013","journal-title":"Mol. Genet. Metab."},{"issue":"1\u20132","key":"10.1016\/j.ymgme.2014.10.010_bb0035","doi-asserted-by":"crossref","first-page":"129","DOI":"10.1016\/j.ymgme.2013.06.008","article-title":"Mucopolysaccharidosis IVA: correlation between genotype, phenotype and keratan sulfate levels","volume":"110","author":"D\u0169ng","year":"2013","journal-title":"Mol. Genet. Metab."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0040","doi-asserted-by":"crossref","first-page":"165","DOI":"10.1007\/s10545-007-0529-7","article-title":"International Morquio A Registry: clinical manifestation and natural course of Morquio A disease","volume":"30","author":"Montano","year":"2007","journal-title":"J. Inherit. Metab. Dis."},{"issue":"4","key":"10.1016\/j.ymgme.2014.10.010_bb0045","doi-asserted-by":"crossref","first-page":"360","DOI":"10.1007\/BF00281685","article-title":"Morquio syndrome: clinical findings in 11 patients with MPS IVA and 2 patients with MPS IVB","volume":"57","author":"Holzgreve","year":"1981","journal-title":"Hum. Genet."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0050","doi-asserted-by":"crossref","first-page":"263","DOI":"10.1136\/adc.72.3.263","article-title":"The mucopolysaccharidoses: a clinical review and guide to management","volume":"72","author":"Wraith","year":"1995","journal-title":"Arch. Dis. Child."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0055","series-title":"Scriver's The Online Metabolic & Molecular Bases of Inherited Disease","article-title":"The mucopolysaccharidoses","author":"Neufeld","year":"2007"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0060","series-title":"MPS IVA Spinal Cord Compression Guideline Advisory Board Meeting; December 8, 2012; Miami, Florida, USA","author":"Charrow","year":"2012"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0065","doi-asserted-by":"crossref","first-page":"381","DOI":"10.1007\/s002340050429","article-title":"MRI of the brain and craniocervical junction in Morquio's disease","volume":"39","author":"Hughes","year":"1997","journal-title":"Neuroradiology"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0070","doi-asserted-by":"crossref","first-page":"358","DOI":"10.1016\/S0967-5868(03)00033-X","article-title":"A case of mucopolysaccharidosis IV with lower leg paresis due to thoraco-lumbar kyphoscoliosis","volume":"10","author":"Ebara","year":"2003","journal-title":"J. Clin. Neurosci."},{"issue":"2","key":"10.1016\/j.ymgme.2014.10.010_bb0075","doi-asserted-by":"crossref","first-page":"309","DOI":"10.1007\/s10545-012-9459-0","article-title":"Clinical overview and treatment options for non-skeletal manifestations of mucopolysaccharidosis type IVA","volume":"36","author":"Hendriksz","year":"2013","journal-title":"J. Inherit. Metab. Dis."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0080","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1016\/j.ymgme.2013.01.021","article-title":"The Morquio A Clinical Assessment Program: baseline results illustrating progressive, multisystemic clinical impairments in Morquio A subjects","volume":"109","author":"Harmatz","year":"2013","journal-title":"Mol. Genet. Metab."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0085","doi-asserted-by":"crossref","first-page":"394","DOI":"10.1097\/BCO.0b013e318269c313","article-title":"Pediatric orthopaedics: orthopaedic surgery for mucopolysaccharidosis","volume":"23","author":"White","year":"2012","journal-title":"Curr. Orthop. Pract."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0090","doi-asserted-by":"crossref","first-page":"307","DOI":"10.1302\/0301-620X.78B2.0780307","article-title":"Occipito\u2013atlanto-axial fusion in Morquio\u2013Brailsford syndrome. A ten-year experience","volume":"78","author":"Ransford","year":"1996","journal-title":"J. Bone Joint Surg. (Br.)"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0095","doi-asserted-by":"crossref","first-page":"851","DOI":"10.1302\/0301-620X.73B5.1910048","article-title":"The odontoid process in Morquio\u2013Brailsford's disease. The effects of occipitocervical fusion","volume":"73","author":"Stevens","year":"1991","journal-title":"J. Bone Joint Surg. (Br.)"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0100","doi-asserted-by":"crossref","first-page":"438","DOI":"10.2106\/JBJS.H.00148","article-title":"Cervical stenosis and spastic quadriparesis in Morquio disease (MPS IV). A case report with twenty-six-year follow-up","volume":"91","author":"White","year":"2009","journal-title":"J. Bone Joint Surg. Am."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0105","doi-asserted-by":"crossref","first-page":"47","DOI":"10.3233\/PRM-2010-0102","article-title":"Orthopedic management of mucopolysaccharide disease","volume":"3","author":"White","year":"2010","journal-title":"J. Pediatr. Rehabil. Med."},{"issue":"6","key":"10.1016\/j.ymgme.2014.10.010_bb0110","doi-asserted-by":"crossref","first-page":"1005","DOI":"10.1007\/s10545-013-9591-5","article-title":"Craniocervical decompression in patients with mucopolysaccharidosis VI: development of a scoring system to determine indication and outcome of surgery","volume":"36","author":"Lampe","year":"2013","journal-title":"J. Inherit. Metab. Dis."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0115","doi-asserted-by":"crossref","first-page":"339","DOI":"10.1007\/s10545-013-9586-2","article-title":"Spinal involvement in mucopolysaccharidosis IVA (Morquio\u2013Brailsford or Morquio A syndrome): presentation, diagnosis and management","volume":"36","author":"Solanki","year":"2013","journal-title":"J. Inherit. Metab. Dis."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0120","series-title":"Morquio\/GALNS Registry Development Scientific Summit; May 17 and 18, 2013; Miami, Florida, USA","author":"White","year":"2013"},{"issue":"3","key":"10.1016\/j.ymgme.2014.10.010_bb0125","doi-asserted-by":"crossref","first-page":"277","DOI":"10.1002\/ppul.22774","article-title":"Characterization of pulmonary function impairments in patients with mucopolysaccharidoses\u2013changes with age and treatment","volume":"49","author":"Lin","year":"2014","journal-title":"Pediatr. Pulmonol."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0130","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1164\/ajrccm.166.1.at1102","article-title":"ATS statement: guidelines for the six-minute walk test","volume":"166","year":"2002","journal-title":"Am. J. Respir. Crit. Care Med."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0135","doi-asserted-by":"crossref","first-page":"278","DOI":"10.1002\/(SICI)1099-0496(199804)25:4<278::AID-PPUL8>3.0.CO;2-G","article-title":"A step in the right direction: assessing exercise tolerance in cystic fibrosis","volume":"25","author":"Balfour-Lynn","year":"1998","journal-title":"Pediatr. Pulmonol."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0140","doi-asserted-by":"crossref","first-page":"783","DOI":"10.1378\/chest.92.5.783","article-title":"Stair climbing as an indicator of pulmonary function","volume":"92","author":"Bolton","year":"1987","journal-title":"Chest"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0145","doi-asserted-by":"crossref","first-page":"e681","DOI":"10.1542\/peds.2004-1023","volume":"115","author":"Harmatz","year":"2005","journal-title":"Pediatrics"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0150","first-page":"109","article-title":"The Timed Get-up-and-Go test revisited: measurement of the component tasks","volume":"37","author":"Wall","year":"2000","journal-title":"J. Rehabil. Res. Dev."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0155","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1007\/s00247-002-0855-8","article-title":"Radiological diagnosis of the constitutional disorders of bone. As easy as A, B, C?","volume":"33","author":"Offiah","year":"2003","journal-title":"Pediatr. Radiol."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0160","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1007\/8904_2012_179","article-title":"Subjective and objective assessment of hand function in mucopolysaccharidosis IVa patients","volume":"9","author":"Aslam","year":"2013","journal-title":"JIMD Rep."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0165","doi-asserted-by":"crossref","first-page":"251","DOI":"10.1097\/ALN.0b013e31827773b2","article-title":"Practice guidelines for management of the difficult airway: an updated report by the American Society of Anesthesiologists Task Force on Management of the Difficult Airway","volume":"118","author":"Apfelbaum","year":"2013","journal-title":"Anesthesiology"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0175","doi-asserted-by":"crossref","first-page":"901","DOI":"10.1111\/j.1460-9592.2012.03904.x","article-title":"Anesthetic care and perioperative complications of children with Morquio syndrome","volume":"22","author":"Theroux","year":"2012","journal-title":"Paediatr. Anaesth."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0180","series-title":"Paraplegia after epidural-general anesthesia in a Morquio patient with moderate thoracic spinal stenosis","author":"Drummond","year":"2014"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0185","doi-asserted-by":"crossref","first-page":"608","DOI":"10.3171\/2012.2.PEDS11522","article-title":"Spinal cord infarction remote from maximal compression in a patient with Morquio syndrome","volume":"9","author":"Tong","year":"2012","journal-title":"J. Neurosurg. Pediatr."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0190","doi-asserted-by":"crossref","DOI":"10.1007\/s00586-014-3186-1","article-title":"Combined spinal arthrodesis with instrumentation for the management of progressive thoracolumbar kyphosis in children with mucopolysaccharidosis","author":"Garrido","year":"2014","journal-title":"Eur. Spine J."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0195","doi-asserted-by":"crossref","first-page":"101","DOI":"10.1016\/j.anclin.2013.10.001","article-title":"Neuromonitoring for scoliosis surgery","volume":"32","author":"Glover","year":"2014","journal-title":"Anesthesiol. Clin."},{"issue":"Suppl. 1","key":"10.1016\/j.ymgme.2014.10.010_bb0200","doi-asserted-by":"crossref","first-page":"S105","DOI":"10.1007\/s00586-011-1756-z","article-title":"The prevention of neural complications in the surgical treatment of scoliosis: the role of the neurophysiological intraoperative monitoring","volume":"20","author":"Pastorelli","year":"2011","journal-title":"Eur. Spine J."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0205","doi-asserted-by":"crossref","first-page":"523","DOI":"10.1007\/s00381-010-1115-0","article-title":"Intraoperative neurophysiological monitoring during complex spinal deformity cases in pediatric patients: methodology, utility, prognostication, and outcome","volume":"26","author":"Drake","year":"2010","journal-title":"Childs Nerv. Syst."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0210","doi-asserted-by":"crossref","first-page":"1779","DOI":"10.1016\/j.rmed.2007.02.013","article-title":"Special airway concerns in patients with mucopolysaccharidoses","volume":"101","author":"Steven","year":"2007","journal-title":"Respir. Med."},{"key":"10.1016\/j.ymgme.2014.10.010_bb0215","doi-asserted-by":"crossref","first-page":"227","DOI":"10.1097\/00000542-199401000-00034","article-title":"Threatening spinal cord compression during anesthesia in a child with mucopolysaccharidosis VI","volume":"80","author":"Linstedt","year":"1994","journal-title":"Anesthesiology"},{"key":"10.1016\/j.ymgme.2014.10.010_bb0220","doi-asserted-by":"crossref","first-page":"1228","DOI":"10.2106\/JBJS.J.01135","article-title":"Upper cervical fusion in children with morquio syndrome: intermediate to long-term results","volume":"95","author":"Dede","year":"2013","journal-title":"J. Bone Joint Surg. Am."}],"container-title":["Molecular Genetics and Metabolism"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1096719214003357?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1096719214003357?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2020,8,26]],"date-time":"2020-08-26T08:26:13Z","timestamp":1598430373000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1096719214003357"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015,1]]},"references-count":43,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2015,1]]}},"alternative-id":["S1096719214003357"],"URL":"https:\/\/doi.org\/10.1016\/j.ymgme.2014.10.010","relation":{},"ISSN":["1096-7192"],"issn-type":[{"value":"1096-7192","type":"print"}],"subject":[],"published":{"date-parts":[[2015,1]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Diagnostic evaluation, monitoring, and perioperative management of spinal cord compression in patients with Morquio syndrome","name":"articletitle","label":"Article Title"},{"value":"Molecular Genetics and Metabolism","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.ymgme.2014.10.010","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2014 The Authors. Published by Elsevier Inc.","name":"copyright","label":"Copyright"}]}}