{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,12]],"date-time":"2026-10-12T18:09:20Z","timestamp":1791828560789,"version":"4.3.4"},"reference-count":30,"publisher":"Elsevier BV","issue":"1-2","license":[{"start":{"date-parts":[[2018,9,1]],"date-time":"2018-09-01T00:00:00Z","timestamp":1535760000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2018,9,1]],"date-time":"2018-09-01T00:00:00Z","timestamp":1535760000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2018,7,18]],"date-time":"2018-07-18T00:00:00Z","timestamp":1531872000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"DOI":"10.13039\/501100005075","name":"University Medical Center Groningen","doi-asserted-by":"publisher","id":[{"id":"10.13039\/501100005075","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Molecular Genetics and Metabolism"],"published-print":{"date-parts":[[2018,9]]},"DOI":"10.1016\/j.ymgme.2018.07.004","type":"journal-article","created":{"date-parts":[[2018,7,20]],"date-time":"2018-07-20T00:39:07Z","timestamp":1532047147000},"page":"79-85","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":23,"title":["Safety issues associated with dietary management in patients with hepatic glycogen storage disease"],"prefix":"10.1016","volume":"125","author":[{"given":"Thomas A.H.","family":"Steunenberg","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fabian","family":"Peeks","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Irene J.","family":"Hoogeveen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John J.","family":"Mitchell","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Helen","family":"Mundy","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Foekje","family":"de Boer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8058-440X","authenticated-orcid":false,"given":"Charlotte M.A.","family":"Lubout","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carolina F.","family":"de Souza","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David A.","family":"Weinstein","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Terry G.J.","family":"Derks","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.ymgme.2018.07.004_bb0005","series-title":"Inborn Metabolic Diseases: Diagnosis and Treatment","first-page":"121","article-title":"The Glycogen storage diseases and related disorders","author":"Walter","year":"2016"},{"issue":"8","key":"10.1016\/j.ymgme.2018.07.004_bb0010","doi-asserted-by":"crossref","first-page":"423","DOI":"10.1056\/NEJM197602192940805","article-title":"Continuous nocturnal intragastric feeding for management of type 1 glycogen-storage disease","volume":"294","author":"Greene","year":"1976","journal-title":"N. Engl. J. Med."},{"issue":"4","key":"10.1016\/j.ymgme.2018.07.004_bb0015","doi-asserted-by":"crossref","first-page":"225","DOI":"10.1203\/00006450-197904000-00003","article-title":"Nocturnal gastric drip feeding in glucose-6-phosphatase deficient children","volume":"13","author":"Fernandes","year":"1979","journal-title":"Pediatr. Res."},{"issue":"3","key":"10.1016\/j.ymgme.2018.07.004_bb0020","doi-asserted-by":"crossref","first-page":"171","DOI":"10.1056\/NEJM198401193100306","article-title":"Cornstarch therapy in type I glycogen-storage disease","volume":"310","author":"Chen","year":"1984","journal-title":"N. Engl. J. Med."},{"issue":"5","key":"10.1016\/j.ymgme.2018.07.004_bb0025","doi-asserted-by":"crossref","first-page":"1272","DOI":"10.3945\/ajcn.2008.26352","article-title":"Use of modified cornstarch therapy to extend fasting in glycogen storage disease types Ia and Ib","volume":"88","author":"Correia","year":"2008","journal-title":"Am. J. Clin. Nutr."},{"issue":"1","key":"10.1016\/j.ymgme.2018.07.004_bb0030","first-page":"S119","article-title":"Guidelines for management of glycogen storage disease type I - European study on glycogen storage disease type I (ESGSD I)","volume":"161","author":"Rake","year":"2002","journal-title":"Eur. J. Pediatr."},{"issue":"5","key":"10.1016\/j.ymgme.2018.07.004_bb0035","doi-asserted-by":"crossref","first-page":"697","DOI":"10.1007\/s10545-016-9932-2","article-title":"Glycogen storage disease type III: diagnosis, genotype, management, clinical course and outcome","volume":"39","author":"Sentner","year":"2016","journal-title":"J. Inherit. Metab. Dis."},{"issue":"11","key":"10.1016\/j.ymgme.2018.07.004_bb0040","doi-asserted-by":"crossref","first-page":"e1","DOI":"10.1038\/gim.2014.128","article-title":"Diagnosis and management of glycogen storage disease type I: a practice guideline of the American College of Medical Genetics and Genomics","volume":"16","author":"Kishnani","year":"2014","journal-title":"Genetics Med."},{"key":"10.1016\/j.ymgme.2018.07.004_bb0045","series-title":"Integrated Addendum to ICH E6(R1): Guideline for Good Clinical Practise E6 (R2)","author":"International Conference on Harmonisation, (ICH)","year":"2016"},{"issue":"72-3","key":"10.1016\/j.ymgme.2018.07.004_bb0050","doi-asserted-by":"crossref","first-page":"274","DOI":"10.1136\/adc.72.3.274-b","article-title":"Hypoglycaemia complicating treatment regimens for glycogen storage disease","volume":"274-5","author":"Dunger","year":"1995","journal-title":"Arch. Dis. Child."},{"issue":"8101","key":"10.1016\/j.ymgme.2018.07.004_bb0055","doi-asserted-by":"crossref","first-page":"1203","DOI":"10.1016\/S0140-6736(78)92187-6","article-title":"Hypoglycaemia complicating feeding regimens for glycogen-storage disease","volume":"2","author":"Leonard","year":"1978","journal-title":"Lancet (Lond. Engl.)"},{"issue":"6","key":"10.1016\/j.ymgme.2018.07.004_bb0060","doi-asserted-by":"crossref","first-page":"858","DOI":"10.2337\/diacare.18.6.858","article-title":"Symptoms of hypoglycemia in children with IDDM","volume":"18","author":"McCrimmon","year":"1995","journal-title":"Diabetes Care"},{"issue":"10","key":"10.1016\/j.ymgme.2018.07.004_bb0065","doi-asserted-by":"crossref","first-page":"836","DOI":"10.1002\/(SICI)1096-9136(199810)15:10<836::AID-DIA681>3.0.CO;2-S","article-title":"Hypoglycaemic symptoms reported by children with type 1 diabetes mellitus and by their parents","volume":"15","author":"Ross","year":"1998","journal-title":"Diabet. Med."},{"issue":"8263","key":"10.1016\/j.ymgme.2018.07.004_bb0070","doi-asserted-by":"crossref","first-page":"113","DOI":"10.1016\/S0140-6736(82)90257-4","article-title":"Lactate as energy source for brain in glucose-6-phosphatase deficient child","volume":"1","author":"Fernandes","year":"1982","journal-title":"Lancet"},{"issue":"7","key":"10.1016\/j.ymgme.2018.07.004_bb0075","doi-asserted-by":"crossref","first-page":"728","DOI":"10.1093\/jpepsy\/jsn017","article-title":"Psychosocial functioning in youth with glycogen storage disease type I","volume":"33","author":"Storch","year":"2008","journal-title":"J. Pediatr. Psychol."},{"issue":"8","key":"10.1016\/j.ymgme.2018.07.004_bb0080","doi-asserted-by":"crossref","first-page":"863","DOI":"10.1023\/A:1013996325720","article-title":"Continuous glucose monitoring in children with glycogen storage disease type I","volume":"24","author":"Hershkovitz","year":"2001","journal-title":"J. Inherit. Metab. Dis."},{"issue":"3","key":"10.1016\/j.ymgme.2018.07.004_bb0085","doi-asserted-by":"crossref","first-page":"631","DOI":"10.1007\/s10545-011-9335-3","article-title":"The use of continuous glucose monitoring in the practical management of glycogen storage disorders","volume":"34","author":"White","year":"2011","journal-title":"J. Inherit. Metab. Dis."},{"key":"10.1016\/j.ymgme.2018.07.004_bb0090","first-page":"0056","article-title":"Continuous glucose monitoring in the treatment of obesity in patients with glycogen storage disease type Ia","volume":"2013","author":"Korljan Jelaska","year":"2013","journal-title":"Endocrinol. Diabetes Metab. Case Rep."},{"issue":"1","key":"10.1016\/j.ymgme.2018.07.004_bb0095","doi-asserted-by":"crossref","first-page":"101","DOI":"10.1038\/ejcn.2013.186","article-title":"Continuous glucose monitoring in children with glycogen storage disease type I","volume":"68","author":"Kasapkara","year":"2014","journal-title":"Eur. J. Clin. Nutr."},{"issue":"11","key":"10.1016\/j.ymgme.2018.07.004_bb0100","doi-asserted-by":"crossref","first-page":"787","DOI":"10.1089\/dia.2014.0378","article-title":"The performance and usability of a factory-calibrated flash glucose monitoring system","volume":"17","author":"Bailey","year":"2015","journal-title":"Diabetes Technol. Ther."},{"issue":"2","key":"10.1016\/j.ymgme.2018.07.004_bb0105","doi-asserted-by":"crossref","first-page":"74","DOI":"10.1034\/j.1399-5448.2002.30203.x","article-title":"Sweet dreams?--nocturnal hypoglycemia in children with type 1 diabetes","volume":"3","author":"Matyka","year":"2002","journal-title":"Pediatr. Diabetes"},{"issue":"6","key":"10.1016\/j.ymgme.2018.07.004_bb0110","doi-asserted-by":"crossref","first-page":"1902","DOI":"10.2337\/diacare.26.6.1902","article-title":"Hypoglycemia in diabetes","volume":"26","author":"Cryer","year":"2003","journal-title":"Diabetes Care"},{"issue":"1","key":"10.1016\/j.ymgme.2018.07.004_bb0115","doi-asserted-by":"crossref","first-page":"186","DOI":"10.2337\/diacare.28.1.186","article-title":"Care of children and adolescents with type 1 diabetes: a statement of the American Diabetes Association","volume":"28","author":"Silverstein","year":"2005","journal-title":"Diabetes Care"},{"key":"10.1016\/j.ymgme.2018.07.004_bb0120","article-title":"Consensus guidelines for management of glycogen storage disease type 1b - European study on glycogen storage disease type 1","volume":"161","author":"Visser","year":"2002","journal-title":"Eur. J. Pediatr."},{"issue":"7","key":"10.1016\/j.ymgme.2018.07.004_bb0125","doi-asserted-by":"crossref","first-page":"446","DOI":"10.1097\/GIM.0b013e3181e655b6","article-title":"Glycogen storage disease type III diagnosis and management guidelines","volume":"12","author":"Kishnani","year":"2010","journal-title":"Genetics Med."},{"issue":"5","key":"10.1016\/j.ymgme.2018.07.004_bb0130","doi-asserted-by":"crossref","first-page":"695","DOI":"10.1007\/s10545-017-0039-1","article-title":"Clinical and biochemical heterogeneity between patients with glycogen storage disease type IA: the added value of CUSUM for metabolic control","volume":"40","author":"Peeks","year":"2017","journal-title":"J. Inherit. Metab. Dis."},{"issue":"1","key":"10.1016\/j.ymgme.2018.07.004_bb0135","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.ymgme.2013.02.005","article-title":"Dietary treatment of glycogen storage disease type Ia: uncooked cornstarch and\/or continuous nocturnal gastric drip-feeding?","volume":"109","author":"Derks","year":"2013","journal-title":"Mol. Genet. Metab."},{"issue":"4","key":"10.1016\/j.ymgme.2018.07.004_bb0140","doi-asserted-by":"crossref","first-page":"329","DOI":"10.1111\/jhn.12030","article-title":"Effect of dietary interventions in the maintenance of normoglycaemia in glycogen storage disease type 1a: a systematic review and meta-analysis","volume":"26","author":"Shah","year":"2013","journal-title":"J. Hum. Nutr. Diet."},{"key":"10.1016\/j.ymgme.2018.07.004_bb0145","doi-asserted-by":"crossref","DOI":"10.1007\/s10545-018-0167-2","article-title":"A preliminary study of telemedicine for patients with hepatic glycogen storage disease and their healthcare providers: from bedside to home site monitoring","author":"Hoogeveen","year":"2018","journal-title":"J. Inherit. Metab. Dis."},{"issue":"10","key":"10.1016\/j.ymgme.2018.07.004_bb0150","doi-asserted-by":"crossref","first-page":"1605","DOI":"10.1093\/ndt\/gfv209","article-title":"How to routinely collect data on patient-reported outcome and experience measures in renal registries in Europe: an expert consensus meeting","volume":"30","author":"Breckenridge","year":"2015","journal-title":"Nephrol. Dial. Transplant."}],"container-title":["Molecular Genetics and Metabolism"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1096719218302403?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1096719218302403?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,21]],"date-time":"2025-10-21T23:21:58Z","timestamp":1761088918000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1096719218302403"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,9]]},"references-count":30,"journal-issue":{"issue":"1-2","published-print":{"date-parts":[[2018,9]]}},"alternative-id":["S1096719218302403"],"URL":"https:\/\/doi.org\/10.1016\/j.ymgme.2018.07.004","relation":{},"ISSN":["1096-7192"],"issn-type":[{"value":"1096-7192","type":"print"}],"subject":[],"published":{"date-parts":[[2018,9]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Safety issues associated with dietary management in patients with hepatic glycogen storage disease","name":"articletitle","label":"Article Title"},{"value":"Molecular Genetics and Metabolism","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.ymgme.2018.07.004","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2018 The Authors. Published by Elsevier Inc.","name":"copyright","label":"Copyright"}]}}