{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,21]],"date-time":"2025-10-21T14:45:29Z","timestamp":1761057929396,"version":"3.44.0"},"reference-count":39,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[1973,2,1]],"date-time":"1973-02-01T00:00:00Z","timestamp":97372800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[1973,2,1]],"date-time":"1973-02-01T00:00:00Z","timestamp":97372800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["amjmed.com","clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["The American Journal of Medicine"],"published-print":{"date-parts":[[1973,2]]},"DOI":"10.1016\/0002-9343(73)90230-1","type":"journal-article","created":{"date-parts":[[2004,4,20]],"date-time":"2004-04-20T00:58:21Z","timestamp":1082422701000},"page":"251-259","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":48,"title":["Erythropoietic protoporphyria with features of a sideroblastic anaemia terminating in liver failure"],"prefix":"10.1016","volume":"54","author":[{"given":"A.J.","family":"Scott","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"A.J.","family":"Ansford","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"B.H.","family":"Webster","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H.C.W.","family":"Stringer","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/0002-9343(73)90230-1_BIB1","doi-asserted-by":"crossref","first-page":"448","DOI":"10.1016\/S0140-6736(61)92427-8","article-title":"Erythropoietic protoporphyria. A new porphyria syndrome with solar urticaria due to protoporphyrinaemia","volume":"2","author":"Magnus","year":"1961","journal-title":"Lancet"},{"key":"10.1016\/0002-9343(73)90230-1_BIB2","series-title":"The Metabolic Basis of Inherited Disease","article-title":"The porphyrias","author":"Schmid","year":"1966"},{"key":"10.1016\/0002-9343(73)90230-1_BIB3","doi-asserted-by":"crossref","first-page":"450","DOI":"10.1016\/0002-9343(63)90144-X","article-title":"Erythropoietic protoporphyria. A new type of inborn error of metabolism","volume":"35","author":"Haeger-Aronsen","year":"1963","journal-title":"Amer J Med"},{"key":"10.1016\/0002-9343(73)90230-1_BIB4","doi-asserted-by":"crossref","first-page":"1449","DOI":"10.1016\/S0140-6736(64)92022-7","article-title":"Erythropoietic protoporphyria","volume":"1","author":"Redeker","year":"1964","journal-title":"Lancet"},{"key":"10.1016\/0002-9343(73)90230-1_BIB5","doi-asserted-by":"crossref","first-page":"682","DOI":"10.1001\/archderm.1966.01600300006002","article-title":"Erythropoietic protoporphyria (Antea lipoid proteinosis) in sisters","volume":"94","author":"Cripps","year":"1966","journal-title":"Arch Derm (Chicago)"},{"key":"10.1016\/0002-9343(73)90230-1_BIB6","first-page":"500","article-title":"Hepatobiliary changes in erythropoietic protoporphyria","volume":"80","author":"Cripps","year":"1965","journal-title":"Arch Path (Chicago)"},{"key":"10.1016\/0002-9343(73)90230-1_BIB7","doi-asserted-by":"crossref","first-page":"157","DOI":"10.1136\/jcp.21.2.157","article-title":"Erythropoietic porphyrin hepatitis","volume":"21","author":"Barnes","year":"1968","journal-title":"J Clin Path"},{"key":"10.1016\/0002-9343(73)90230-1_BIB8","doi-asserted-by":"crossref","first-page":"14","DOI":"10.1111\/j.1365-2133.1971.tb14191.x","article-title":"Erythropoietic protoporphyria: two deaths from hepatic cirrhosis","volume":"84","author":"Donaldson","year":"1971","journal-title":"Brit J Derm"},{"key":"10.1016\/0002-9343(73)90230-1_BIB9","doi-asserted-by":"crossref","first-page":"532","DOI":"10.1182\/blood.V22.5.532.532","article-title":"Congenital erythropoietic protoporphyria, an experimental study","volume":"22","author":"Porter","year":"1963","journal-title":"Blood"},{"key":"10.1016\/0002-9343(73)90230-1_BIB10","first-page":"705","article-title":"Porphyrins in the bone marrow and circulating erythrocytes in experimental anemias","volume":"75","author":"Schmid","year":"1950"},{"key":"10.1016\/0002-9343(73)90230-1_BIB11","first-page":"424","article-title":"Lead poisoning as a disorder of heme synthesis","volume":"5","author":"Goldberg","year":"1968"},{"key":"10.1016\/0002-9343(73)90230-1_BIB12","doi-asserted-by":"crossref","first-page":"56","DOI":"10.1111\/j.1365-2141.1959.tb04013.x","article-title":"Refractory normoblastic anaemia: a clinical and hematological study of seven cases","volume":"5","author":"Dacie","year":"1959","journal-title":"Brit J Haemat"},{"key":"10.1016\/0002-9343(73)90230-1_BIB13","doi-asserted-by":"crossref","first-page":"662","DOI":"10.1182\/blood.V18.6.662.662","article-title":"Abnormal (\u201cringed\u201d) sideroblasts in various hematologic and non-hematologic disorders","volume":"18","author":"Bowman","year":"1961","journal-title":"Blood"},{"key":"10.1016\/0002-9343(73)90230-1_BIB14","doi-asserted-by":"crossref","first-page":"624","DOI":"10.1016\/S0140-6736(65)91714-9","article-title":"Biochemical and fluorescence microscopy screening tests for erythropoietic protoporphyria","volume":"1","author":"Rimington","year":"1965","journal-title":"Lancet"},{"year":"1961","author":"Rimington","series-title":"Association of Clinical Pathologists","key":"10.1016\/0002-9343(73)90230-1_BIB15"},{"key":"10.1016\/0002-9343(73)90230-1_BIB16","first-page":"7","article-title":"Isotope studies on a case of erythropoietic protoporphyria","volume":"26","author":"Gray","year":"1964","journal-title":"Clin Sci"},{"key":"10.1016\/0002-9343(73)90230-1_BIB17","first-page":"278","article-title":"Erythropoietic protoporphyria\u2014a misnomer","volume":"17","author":"Scholnick","year":"1969","journal-title":"Clin Res"},{"key":"10.1016\/0002-9343(73)90230-1_BIB18","doi-asserted-by":"crossref","first-page":"446","DOI":"10.1001\/archinte.1968.03640050056011","article-title":"The \u201cglucose effect\u201d in erythropoietic protoporphyria","volume":"121","author":"Redeker","year":"1968","journal-title":"Arch Intern Med (Chicago)"},{"key":"10.1016\/0002-9343(73)90230-1_BIB19","doi-asserted-by":"crossref","first-page":"396","DOI":"10.1016\/0026-0495(64)90113-1","article-title":"The effect of carbohydrate feeding on the inducation of \u03b4-amino levulinic acid synthetase","volume":"13","author":"Tschudy","year":"1964","journal-title":"Metabolism"},{"key":"10.1016\/0002-9343(73)90230-1_BIB20","doi-asserted-by":"crossref","first-page":"232","DOI":"10.1016\/0026-0495(64)90103-9","article-title":"Factors affecting the excretion of porphyrin precursors by patients with acute intermittent porphyria. I. The effect of diet","volume":"13","author":"Welland","year":"1964","journal-title":"Metabolism"},{"key":"10.1016\/0002-9343(73)90230-1_BIB21","doi-asserted-by":"crossref","first-page":"350","DOI":"10.1056\/NEJM196708172770706","article-title":"Porphyria precipitated by fasting","volume":"277","author":"Knudsen","year":"1967","journal-title":"New Eng J Med"},{"key":"10.1016\/0002-9343(73)90230-1_BIB22","doi-asserted-by":"crossref","first-page":"217","DOI":"10.1097\/00005792-196703000-00014","article-title":"Acute intermittent porphyria: effect of diet and griseofulvin","volume":"46","author":"Felsher","year":"1967","journal-title":"Medicine (Balt)"},{"key":"10.1016\/0002-9343(73)90230-1_BIB23","first-page":"409","article-title":"Toxic hepatic porphyrias","volume":"5","author":"De Matteis","year":"1968"},{"key":"10.1016\/0002-9343(73)90230-1_BIB24","doi-asserted-by":"crossref","first-page":"146","DOI":"10.1136\/bmj.3.5611.146","article-title":"Organochlorine pesticide residues in human fat in Great Britain","volume":"3","author":"Abbott","year":"1968","journal-title":"Brit Med J"},{"key":"10.1016\/0002-9343(73)90230-1_BIB25","doi-asserted-by":"crossref","first-page":"89","DOI":"10.1016\/0041-008X(62)90078-9","article-title":"Storage and excretion of DDT in starved rats","volume":"4","author":"Dale","year":"1962","journal-title":"Toxic Appl Pharmacol"},{"key":"10.1016\/0002-9343(73)90230-1_BIB26","doi-asserted-by":"crossref","first-page":"659","DOI":"10.1136\/bmj.1.5541.659","article-title":"Erythropoietic protoporphyria. A family study","volume":"1","author":"Donaldson","year":"1967","journal-title":"Brit Med J"},{"key":"10.1016\/0002-9343(73)90230-1_BIB27","doi-asserted-by":"crossref","first-page":"266","DOI":"10.1136\/gut.9.3.266","article-title":"Antibodies and immunoglobulins in liver disease","volume":"9","author":"Walker","year":"1968","journal-title":"Gut"},{"key":"10.1016\/0002-9343(73)90230-1_BIB28","doi-asserted-by":"crossref","first-page":"521","DOI":"10.1182\/blood.V22.5.521.521","article-title":"Congenital erythropoietic protoporphyria. I. Case reports, clinical studies and porphyrin analyses in two brothers","volume":"22","author":"Porter","year":"1963","journal-title":"Blood"},{"key":"10.1016\/0002-9343(73)90230-1_BIB29","first-page":"235","article-title":"Erythropoietic protoporphyria","volume":"9","author":"Redeker","year":"1963","journal-title":"S Afr J Lab Clin Med"},{"key":"10.1016\/0002-9343(73)90230-1_BIB30","first-page":"26","article-title":"Intrahepatic porphyrastasis in erythropoietic protoporphyria","volume":"17","author":"Kniffen","year":"1969","journal-title":"Clin Res"},{"key":"10.1016\/0002-9343(73)90230-1_BIB31","first-page":"1027","article-title":"Protoporphyrin removal in intrahepatic porphyrastasis","volume":"58","author":"Kniffen","year":"1970","journal-title":"Gastroenterology"},{"key":"10.1016\/0002-9343(73)90230-1_BIB32","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1111\/j.1365-2133.1963.tb13945.x","article-title":"Disturbance of porphyrin metabolism caused by griseofulvin in mice","volume":"75","author":"De Matteis","year":"1963","journal-title":"Brit J Derm"},{"key":"10.1016\/0002-9343(73)90230-1_BIB33","doi-asserted-by":"crossref","first-page":"105","DOI":"10.1111\/j.1365-2133.1963.tb13946.x","article-title":"Protoporphyrin, cirrhosis and hepatoma in the livers of mice given griseofulvin","volume":"75","author":"Hurst","year":"1963","journal-title":"Brit J Derm"},{"key":"10.1016\/0002-9343(73)90230-1_BIB34","doi-asserted-by":"crossref","first-page":"53","DOI":"10.1111\/1523-1747.ep12551671","article-title":"Hepatic protoporphyria in weanling pigs","volume":"54","author":"Roe","year":"1970","journal-title":"J Invest Derm"},{"key":"10.1016\/0002-9343(73)90230-1_BIB35","doi-asserted-by":"crossref","first-page":"400","DOI":"10.1038\/jid.1969.167","article-title":"Factors affecting the induction of porphyria in the laboratory rat. Biochemical and photobiologic studies using diethyl 1,4 dehydro 2,4,6 trimethylpyridine 3,5 decarboxylate (DDC) as a porphyragenic agent","volume":"53","author":"Magnus","year":"1969","journal-title":"J Invest Derm"},{"key":"10.1016\/0002-9343(73)90230-1_BIB36","first-page":"247","article-title":"Erythropoietic protoporphyria. A brief report of the first South African case","volume":"9","author":"Sweeney","year":"1963","journal-title":"S Afr J Lab Clin Med"},{"key":"10.1016\/0002-9343(73)90230-1_BIB37","doi-asserted-by":"crossref","first-page":"321","DOI":"10.1042\/bj1040321","article-title":"Studies on ferrochelatase: The effects of thiols and other factors in the determination of activity","volume":"104","author":"Porra","year":"1967","journal-title":"Biochem J"},{"key":"10.1016\/0002-9343(73)90230-1_BIB38","doi-asserted-by":"crossref","first-page":"587","DOI":"10.1056\/NEJM196903132801104","article-title":"Sideroblastic anaemia with dermal photosensitivity and increased erythrocyte protoporphyrin","volume":"280","author":"Rothstein","year":"1969","journal-title":"New Eng J Med"},{"key":"10.1016\/0002-9343(73)90230-1_BIB39","first-page":"247","article-title":"Erythropoietic protoporphyria. A brief report of the first South African case","volume":"9","author":"Rimington","year":"1963","journal-title":"S Afr J Lab Clin Med"}],"container-title":["The American Journal of Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:0002934373902301?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:0002934373902301?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,9,3]],"date-time":"2025-09-03T06:20:45Z","timestamp":1756880445000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/0002934373902301"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1973,2]]},"references-count":39,"journal-issue":{"issue":"2","published-print":{"date-parts":[[1973,2]]}},"alternative-id":["0002934373902301"],"URL":"https:\/\/doi.org\/10.1016\/0002-9343(73)90230-1","relation":{},"ISSN":["0002-9343"],"issn-type":[{"type":"print","value":"0002-9343"}],"subject":[],"published":{"date-parts":[[1973,2]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Erythropoietic protoporphyria with features of a sideroblastic anaemia terminating in liver failure","name":"articletitle","label":"Article Title"},{"value":"The American Journal of Medicine","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/0002-9343(73)90230-1","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"converted-article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 1973 Published by Excerpta Medica Inc.","name":"copyright","label":"Copyright"}]}}