{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,20]],"date-time":"2025-10-20T17:47:26Z","timestamp":1760982446320},"reference-count":22,"publisher":"Cambridge University Press (CUP)","issue":"8","license":[{"start":{"date-parts":[[2007,6,29]],"date-time":"2007-06-29T00:00:00Z","timestamp":1183075200000},"content-version":"unspecified","delay-in-days":2889,"URL":"https:\/\/www.cambridge.org\/core\/terms"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J. Laryngol. Otol."],"published-print":{"date-parts":[[1999,8]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>A severe malformation of the inner ear, often referred to as severe labyrinthine dysplasia or common cavity deformity, consists of an absent or dilated cochlear basal coil, wide communication with the vestibule and a tapered internal acoustic meatus and can be associated with absent hearing. We discuss two children with severe labyringthine dysplasia as shown by computed tomography (CT) scans and, in the first case, an absent VIIIth nerve bilaterally shown by magnetic resonance imaging (MRI). In 1995, both cases were precluded from cochlear implantation, on the basis of the absent VIIIth nerve (first case) and increased risk of CSF leak during operation (second case). However, audiometric results and vocalization patterns of both children suggested the presence of some residual hearing function, while recently reported specific surgical techniques have been found to be safe and effective in the cochlear implantation of the common cavity deformity. The management of such cases should be decided on the grounds of a full audiological assessment in conjunction with the radiological features, in the light of current surgical trends shown to be safe and effective.<\/jats:p>","DOI":"10.1017\/s0022215100145001","type":"journal-article","created":{"date-parts":[[2007,11,30]],"date-time":"2007-11-30T10:11:52Z","timestamp":1196417512000},"page":"714-716","source":"Crossref","is-referenced-by-count":11,"title":["Useful residual hearing despite radiological findings suggestive of anacusis"],"prefix":"10.1017","volume":"113","author":[{"given":"Doris Eva","family":"Bamiou","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Cliodna O","family":"Mahoney","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tony","family":"Sirimanna","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"56","published-online":{"date-parts":[[2007,6,29]]},"reference":[{"key":"S0022215100145001_ref022","doi-asserted-by":"publisher","DOI":"10.1288\/00005537-198601000-00005"},{"key":"S0022215100145001_ref001","doi-asserted-by":"publisher","DOI":"10.1044\/jshr.2701.134"},{"key":"S0022215100145001_ref020","doi-asserted-by":"publisher","DOI":"10.1044\/jshr.3703.700"},{"key":"S0022215100145001_ref017","doi-asserted-by":"publisher","DOI":"10.1017\/S0022215100123552"},{"key":"S0022215100145001_ref003","first-page":"184","article-title":"Cochlear implantation in children with cochlear malformations","volume":"18","author":"Hoffman","year":"1997","journal-title":"American Journal of Otology"},{"key":"S0022215100145001_ref016","doi-asserted-by":"publisher","DOI":"10.1159\/000276746"},{"key":"S0022215100145001_ref014","doi-asserted-by":"publisher","DOI":"10.1017\/S0022215100127112"},{"key":"S0022215100145001_ref009","doi-asserted-by":"publisher","DOI":"10.1017\/S0022215100057376"},{"key":"S0022215100145001_ref008","doi-asserted-by":"publisher","DOI":"10.1097\/00005537-199708000-00005"},{"key":"S0022215100145001_ref011","doi-asserted-by":"publisher","DOI":"10.1177\/00034894800892S301"},{"key":"S0022215100145001_ref007","doi-asserted-by":"publisher","DOI":"10.1017\/S0142716400008651"},{"key":"S0022215100145001_ref015","first-page":"551","article-title":"Cochlear dysplasia and meningitis","volume":"15","author":"Phelps","year":"1994","journal-title":"American Journal of Otology"},{"key":"S0022215100145001_ref012","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2273.1990.tb00440.x"},{"key":"S0022215100145001_ref021","first-page":"201","article-title":"Etiology of hearing loss and cochlear computed tomography: findings in preimplant assessment","author":"Woolford","year":"1995","journal-title":"Annals of Otology \u2013 Rhinology and Laryngology"},{"key":"S0022215100145001_ref004","doi-asserted-by":"publisher","DOI":"10.1002\/lary.5540971301"},{"key":"S0022215100145001_ref018","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.ge.29.120195.003331"},{"key":"S0022215100145001_ref006","doi-asserted-by":"publisher","DOI":"10.1001\/archotol.1997.01900090090013"},{"key":"S0022215100145001_ref005","doi-asserted-by":"publisher","DOI":"10.1044\/jshd.5201.64"},{"key":"S0022215100145001_ref013","doi-asserted-by":"publisher","DOI":"10.1259\/0007-1285-65-773-370"},{"key":"S0022215100145001_ref002","doi-asserted-by":"publisher","DOI":"10.3109\/00016487009123382"},{"key":"S0022215100145001_ref010","doi-asserted-by":"publisher","DOI":"10.1016\/S0194-5998(97)70358-9"},{"key":"S0022215100145001_ref019","doi-asserted-by":"publisher","DOI":"10.1016\/S0959-4388(96)80059-6"}],"container-title":["The Journal of Laryngology &amp; Otology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.cambridge.org\/core\/services\/aop-cambridge-core\/content\/view\/S0022215100145001","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,5,9]],"date-time":"2019-05-09T20:43:28Z","timestamp":1557434608000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.cambridge.org\/core\/product\/identifier\/S0022215100145001\/type\/journal_article"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1999,8]]},"references-count":22,"journal-issue":{"issue":"8","published-print":{"date-parts":[[1999,8]]}},"alternative-id":["S0022215100145001"],"URL":"https:\/\/doi.org\/10.1017\/s0022215100145001","relation":{},"ISSN":["0022-2151","1748-5460"],"issn-type":[{"value":"0022-2151","type":"print"},{"value":"1748-5460","type":"electronic"}],"subject":[],"published":{"date-parts":[[1999,8]]}}}