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It often presents with symptoms and signs involving the ear, nose, and head and neck area.<\/jats:p><\/jats:sec><jats:sec id=\"S0022215114001492_sec2\"><jats:title>Objective:<\/jats:title><jats:p>To highlight salient features of ENT-related issues in granulomatosis with polyangiitis, and raise awareness of the condition.<\/jats:p><\/jats:sec><jats:sec id=\"S0022215114001492_sec3\"><jats:title>Methods:<\/jats:title><jats:p>A case report of a patient with limited disease and an insidious onset is presented, along with a review of the current literature. In addition, basic initial management is described.<\/jats:p><\/jats:sec><jats:sec id=\"S0022215114001492_sec4\"><jats:title>Results:<\/jats:title><jats:p>Eighty-six publications were used to describe salient features of ENT-related issues in granulomatosis with polyangiitis.<\/jats:p><\/jats:sec><jats:sec id=\"S0022215114001492_sec5\"><jats:title>Conclusion:<\/jats:title><jats:p>The time to diagnosis has not reduced significantly in the last 10 years in the UK. A high index of suspicion is required for an earlier diagnosis of granulomatosis with polyangiitis.<\/jats:p><\/jats:sec>","DOI":"10.1017\/s0022215114001492","type":"journal-article","created":{"date-parts":[[2014,7,22]],"date-time":"2014-07-22T13:24:41Z","timestamp":1406035481000},"page":"730-737","source":"Crossref","is-referenced-by-count":6,"title":["Presentation and initial assessment of ENT problems in patients with granulomatosis with polyangiitis (Wegener's)"],"prefix":"10.1017","volume":"128","author":[{"given":"M","family":"Martinez Del 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