{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,10]],"date-time":"2026-06-10T08:55:16Z","timestamp":1781081716090,"version":"3.54.1"},"reference-count":23,"publisher":"Cambridge University Press (CUP)","issue":"3","license":[{"start":{"date-parts":[[2015,9,18]],"date-time":"2015-09-18T00:00:00Z","timestamp":1442534400000},"content-version":"unspecified","delay-in-days":9179,"URL":"https:\/\/www.cambridge.org\/core\/terms"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Can. j. neurol. sci."],"published-print":{"date-parts":[[1990,8]]},"abstract":"<jats:title>ABSTRACT:<\/jats:title><jats:p>Two patients with neuroacanthocytosis are described. One presented with parkinsonism and the other resembled diurnal dystonia of the Segawa type. Both patients responded well to dopaminomimetic therapy. A PET scan with fluorodopa revealed a nigrostriatal deficit in the first patient.<\/jats:p>","DOI":"10.1017\/s0317167100030602","type":"journal-article","created":{"date-parts":[[2016,7,28]],"date-time":"2016-07-28T11:41:20Z","timestamp":1469706080000},"page":"298-301","source":"Crossref","is-referenced-by-count":16,"title":["Parkinsonism with Neuroacanthocytosis"],"prefix":"10.1017","volume":"17","author":[{"given":"R.F.","family":"Peppard","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"C.S.","family":"Lu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nai-Shin","family":"Chu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"P.","family":"Teal","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"W.R.W.","family":"Martin","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D.B.","family":"Calne","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"56","published-online":{"date-parts":[[2015,9,18]]},"reference":[{"key":"S0317167100030602_ref019","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.35.3.366"},{"key":"S0317167100030602_ref007","first-page":"396","volume-title":"Clinical hematology and fundamentals of hemostasis","author":"Pittiglio","year":"1987"},{"key":"S0317167100030602_ref001","doi-asserted-by":"crossref","first-page":"381","DOI":"10.1182\/blood.V5.4.381.381","article-title":"Malformation of the erythrocytes in a case of atypical retinitis pigmentosa","volume":"5","author":"Bassen","year":"1950","journal-title":"Blood"},{"key":"S0317167100030602_ref013","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.35.11.1679-a"},{"key":"S0317167100030602_ref017","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.44.7.645"},{"key":"S0317167100030602_ref005","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/95.4.749"},{"key":"S0317167100030602_ref008","first-page":"468","article-title":"Red cell defonnability and lipid composition in two forms of acanthocytosis: enrichment of acanthocytic populations by density gradient centrifugation","volume":"113","author":"Clark","year":"1989","journal-title":"J Lab Clin Med"},{"key":"S0317167100030602_ref021","doi-asserted-by":"publisher","DOI":"10.1002\/ana.410030312"},{"key":"S0317167100030602_ref014","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1981.00510060037003"},{"key":"S0317167100030602_ref011","first-page":"327","volume-title":"Extrapyramidal disorders. Handbook of Clinical Neurology","volume":"49","author":"Bruyn","year":"1986"},{"key":"S0317167100030602_ref004","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1968.00480040069007"},{"key":"S0317167100030602_ref023","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.37.4.645"},{"key":"S0317167100030602_ref002","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9343(69)90089-8"},{"key":"S0317167100030602_ref003","first-page":"134","article-title":"Acanthocytosis and neurological disorder without betalipoproteinemia","volume":"18","author":"Critchley","year":"1968","journal-title":"Ann Neurol"},{"key":"S0317167100030602_ref006","first-page":"556","volume-title":"McGraw-Hill","author":"Williams","year":"1983"},{"key":"S0317167100030602_ref009","first-page":"291","article-title":"Acanthocytosis and neurological impairment - a review","volume":"264","author":"Hardie","year":"1989","journal-title":"Quat J Med"},{"key":"S0317167100030602_ref010","doi-asserted-by":"publisher","DOI":"10.1038\/317246a0"},{"key":"S0317167100030602_ref012","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/106.3.717"},{"key":"S0317167100030602_ref015","first-page":"118","volume-title":"Neurol Med Chir","volume":"15","author":"Kondo","year":"1981"},{"key":"S0317167100030602_ref016","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1982.00510170040011"},{"key":"S0317167100030602_ref018","doi-asserted-by":"publisher","DOI":"10.1016\/0022-510X(82)90169-1"},{"key":"S0317167100030602_ref020","first-page":"215","article-title":"Hereditary progressive dystonia with marked diurnal fluctuation","volume":"14","author":"Segawa","year":"1976","journal-title":"Adv Neurol"},{"key":"S0317167100030602_ref022","first-page":"105","article-title":"An autopsy case of chorea-acanthocytosis","volume":"365","author":"Sato","year":"1984","journal-title":"NoToShinkei"}],"container-title":["Canadian Journal of Neurological Sciences \/ Journal Canadien des Sciences Neurologiques"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.cambridge.org\/core\/services\/aop-cambridge-core\/content\/view\/S0317167100030602","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,7,4]],"date-time":"2022-07-04T01:32:21Z","timestamp":1656898341000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.cambridge.org\/core\/product\/identifier\/S0317167100030602\/type\/journal_article"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1990,8]]},"references-count":23,"journal-issue":{"issue":"3","published-print":{"date-parts":[[1990,8]]}},"alternative-id":["S0317167100030602"],"URL":"https:\/\/doi.org\/10.1017\/s0317167100030602","relation":{},"ISSN":["0317-1671","2057-0155"],"issn-type":[{"value":"0317-1671","type":"print"},{"value":"2057-0155","type":"electronic"}],"subject":[],"published":{"date-parts":[[1990,8]]}}}