{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,22]],"date-time":"2026-09-22T14:32:30Z","timestamp":1790087550960,"version":"4.0.1"},"reference-count":46,"publisher":"Cambridge University Press (CUP)","issue":"6","license":[{"start":{"date-parts":[[2005,1,21]],"date-time":"2005-01-21T00:00:00Z","timestamp":1106265600000},"content-version":"unspecified","delay-in-days":51,"URL":"https:\/\/www.cambridge.org\/core\/terms"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Cardiol Young"],"published-print":{"date-parts":[[2004,12]]},"abstract":"<jats:p><jats:italic>Objectives:<\/jats:italic>To estimate the incidence of, and profile the spread of, congenital cardiac defects, and to assess the accuracy of the echocardiographic diagnosis as performed by a neonatologist.<jats:italic>Design:<\/jats:italic>Hospital-based study.<jats:italic>Methods:<\/jats:italic>All neonates meeting our criterions, specifically those with a persistent murmur 48 hours after birth, underwent an echocardiographic examination to exclude an underlying congenital cardiac defect. All scans performed by the neonatologist were videotaped and reviewed by a paediatric cardiologist. We assessed concordance according to inter-rater agreement.<jats:italic>Results:<\/jats:italic>Out of 11,085 live births, there were 83 infants with a congenital cardiac defect, giving an incidence of 7.49 per 1000 live births, with 95% confidence interval from 5.88 to 9.09. Of the infants with a murmur persisting at or greater than 48 hours after birth, who had a median age of 4.5 days, 75% had a congenital heart defect, with ventricular septal defect being the commonest, encountered in 56.7% of cases. Concordance between the neonatologist and the cardiologist was good, with Cohen's Kappa coefficient being calculated at 0.68, and 95% confidence interval from 0.51 to 0.85.<jats:italic>Conclusion:<\/jats:italic>The incidence of congenital cardiac malformations as determined in our hospital-based study in the United Arab Emirates is similar to that described in the Gulf region and worldwide. A persistent murmur at or greater than 48 hours after birth is strongly suggestive of an underlying congenital cardiac malformation. Our experience shows that a neonatologist appropriately trained in echocardiography can perform as well as a paediatric cardiologist. Where specialist resources are limited, this allows for early diagnosis, earlier referral if necessary, and early institution of appropriate therapy.<\/jats:p>","DOI":"10.1017\/s104795110400602x","type":"journal-article","created":{"date-parts":[[2005,1,28]],"date-time":"2005-01-28T15:59:26Z","timestamp":1106927966000},"page":"585-593","source":"Crossref","is-referenced-by-count":24,"title":["A study of congenital cardiac disease in a neonatal population \u2013 the validity of echocardiography undertaken by a neonatologist"],"prefix":"10.1017","volume":"14","author":[{"given":"Gregory R.","family":"Samson","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Suresh R.","family":"Kumar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"56","published-online":{"date-parts":[[2005,1,21]]},"reference":[{"key":"S104795110400602X_ref009","unstructured":"Skinner J , Alverson D , Hunter S (eds). 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