{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,6]],"date-time":"2026-10-06T04:33:01Z","timestamp":1791261181319,"version":"4.1.0"},"reference-count":10,"publisher":"Cambridge University Press (CUP)","issue":"3","license":[{"start":{"date-parts":[[2005,5,3]],"date-time":"2005-05-03T00:00:00Z","timestamp":1115078400000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/www.cambridge.org\/core\/terms"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Cardiol Young"],"published-print":{"date-parts":[[2005,6]]},"abstract":"<jats:p>Over a period of 6 days, a three-week-old male developed a long-segment coarctation, with sub-total obstruction of the descending aorta, immediately distal to the left subclavian artery. On the 24th day of life, the stenotic region was repaired by placement of a pulmonary allograft patch measuring 3 centimetres in length. Severe diffuse vascular medial thickening was discovered at the operation. Subsequent fluorescence in-situ hybridization proved positive for Williams' syndrome. To our knowledge, this is the first report of rapidly progressive infantile arteriopathy in the setting of Williams' syndrome.<\/jats:p>","DOI":"10.1017\/s104795110500065x","type":"journal-article","created":{"date-parts":[[2005,5,3]],"date-time":"2005-05-03T07:10:35Z","timestamp":1115104235000},"page":"312-314","source":"Crossref","is-referenced-by-count":15,"title":["Rapid progression of long-segment coarctation in a patient with Williams' syndrome"],"prefix":"10.1017","volume":"15","author":[{"given":"Cammon","family":"Arrington","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Martin","family":"Tristani-Firouzi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael","family":"Puchalski","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"56","published-online":{"date-parts":[[2005,5,3]]},"reference":[{"key":"S104795110500065X_ref002","doi-asserted-by":"crossref","unstructured":"Ewart AK , Morris CA , Atkinson D , et al. 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