{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,4,2]],"date-time":"2022-04-02T06:43:25Z","timestamp":1648881805412},"reference-count":6,"publisher":"Cambridge University Press (CUP)","issue":"1","license":[{"start":{"date-parts":[[2013,2,27]],"date-time":"2013-02-27T00:00:00Z","timestamp":1361923200000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/www.cambridge.org\/core\/terms"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Cardiol Young"],"published-print":{"date-parts":[[2014,2]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>A 12-year-old girl presented with a protein-losing enteropathy. Symptoms started 4 weeks after undergoing the Fontan procedure at the age of 1.5 years for mitral atresia, ventricular septal defect, and double-outlet right ventricle. Upon referral for 3 weeks of rehabilitation after multiple interventional measures and drug treatments, she appeared in a dystrophic state, with decreased plasma protein and electrolyte levels along with occasional tetanic convulsions. Blood glucose levels after a lactose tolerance test were markedly reduced. The introduction of a lactose-free diet was quickly effective, with plasma protein and electrolyte levels raised to normal levels, and the girl's body weight increased without ascites or oedema. Molecular genetic examination revealed a homozygous C\/C<jats:sub>13910<\/jats:sub> polymorphism in the LCT gene. <jats:italic>Conclusion:<\/jats:italic> Protein-losing enteropathy in the Fontan circulation may be provoked by lactase deficiency and should therefore be ruled out to exclude this rather common condition.<\/jats:p>","DOI":"10.1017\/s1047951112001928","type":"journal-article","created":{"date-parts":[[2013,2,27]],"date-time":"2013-02-27T13:48:39Z","timestamp":1361972919000},"page":"175-177","source":"Crossref","is-referenced-by-count":0,"title":["Protein-losing enteropathy following the Fontan procedure in a child with intestinal lactase deficiency treated with lactose-free diet"],"prefix":"10.1017","volume":"24","author":[{"given":"Wolfgang","family":"Kienast","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Klaus","family":"Haeseler","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Reinhard","family":"Herterich","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"56","published-online":{"date-parts":[[2013,2,27]]},"reference":[{"key":"S1047951112001928_ref4","doi-asserted-by":"publisher","DOI":"10.1515\/CCLM.2008.189"},{"key":"S1047951112001928_ref3","doi-asserted-by":"publisher","DOI":"10.1007\/s00431-010-1235-2"},{"key":"S1047951112001928_ref2","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-5223(98)70406-4"},{"key":"S1047951112001928_ref5","doi-asserted-by":"publisher","DOI":"10.1111\/j.1753-4887.2007.tb00286.x"},{"key":"S1047951112001928_ref1","unstructured":"Robert Koch Institut: Referenzperzentile f\u00fcr anthropometrische Ma\u00dfzahlen und Blutdruck aus der Studie zur Gesundheit von Kindern und Jugendlichen in Deutschland (KiGGS) 2003\u20132006. Robert Koch-Institut, Berlin, 2011; pp. 21\u201331."},{"key":"S1047951112001928_ref6","doi-asserted-by":"publisher","DOI":"10.1542\/peds.2006-1721"}],"container-title":["Cardiology in the Young"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.cambridge.org\/core\/services\/aop-cambridge-core\/content\/view\/S1047951112001928","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,4,23]],"date-time":"2019-04-23T00:24:00Z","timestamp":1555979040000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.cambridge.org\/core\/product\/identifier\/S1047951112001928\/type\/journal_article"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2013,2,27]]},"references-count":6,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2014,2]]}},"alternative-id":["S1047951112001928"],"URL":"https:\/\/doi.org\/10.1017\/s1047951112001928","relation":{},"ISSN":["1047-9511","1467-1107"],"issn-type":[{"value":"1047-9511","type":"print"},{"value":"1467-1107","type":"electronic"}],"subject":[],"published":{"date-parts":[[2013,2,27]]}}}