{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,17]],"date-time":"2026-06-17T15:44:35Z","timestamp":1781711075211,"version":"3.54.5"},"reference-count":28,"publisher":"Cambridge University Press (CUP)","issue":"6","license":[{"start":{"date-parts":[[2014,9,24]],"date-time":"2014-09-24T00:00:00Z","timestamp":1411516800000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/www.cambridge.org\/core\/terms"}],"content-domain":{"domain":["journals.cambridge.org"],"crossmark-restriction":true},"short-container-title":["Cardiol Young"],"published-print":{"date-parts":[[2015,8]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p><jats:italic>Objective:<\/jats:italic>Symptomatic neonates with Ebstein\u2019s anomaly pose significant challenge. Within this cohort, neonates with associated anatomical pulmonary atresia have higher mortality. We review our experience with this difficult subset.<jats:italic>Methods:<\/jats:italic>A total of 32 consecutive symptomatic neonates with Ebstein\u2019s anomaly underwent surgical intervention between 1994 and 2013. Of them, 20 neonates (62%, 20\/32) had associated pulmonary atresia. Patients\u2019 weights ranged from 1.9 to 3.4 kg. All patients without pulmonary atresia had two-ventricle repair. Of the 20 neonates, 16 (80%, 16\/20) with Ebstein\u2019s anomaly and pulmonary atresia had two-ventricle repair and 4 had single-ventricle palliation, of which 2 underwent Starnes\u2019 palliation and 2 Blalock\u2013Taussig shunts. Six recent patients with Ebstein\u2019s anomaly and pulmonary atresia had right ventricle to pulmonary artery valved conduit as part of their two-ventricle repair.<jats:italic>Results:<\/jats:italic>Overall early mortality was 28% (9\/32). For those without pulmonary atresia, mortality was 8.3% (1\/12). For the entire cohort of neonates with Ebstein\u2019s anomaly and pulmonary atresia, mortality was 40% (8\/20; p=0.05). Mortality for neonates with Ebstein\u2019s anomaly and pulmonary atresia having two-ventricle repair was 44% (7\/16). Mortality for neonates with Ebstein\u2019s anomaly and pulmonary atresia having two-ventricle repair utilising right ventricle to pulmonary artery conduit was 16% (1\/6). For those having one-ventricle repair, the mortality was 25% (1\/4).<jats:italic>Conclusions:<\/jats:italic>Surgical management of neonates with Ebstein\u2019s anomaly remains challenging. For neonates with Ebstein\u2019s anomaly and anatomical pulmonary atresia, single-ventricle palliation is associated with lower early mortality compared with two-ventricle repair. This outcome advantage is negated by inclusion of right ventricle to pulmonary artery conduit as part of the two-ventricle repair.<\/jats:p>","DOI":"10.1017\/s1047951114001747","type":"journal-article","created":{"date-parts":[[2014,9,24]],"date-time":"2014-09-24T10:44:28Z","timestamp":1411555468000},"page":"1119-1123","update-policy":"https:\/\/doi.org\/10.1017\/policypage","source":"Crossref","is-referenced-by-count":19,"title":["Surgical management of symptomatic neonates with Ebstein\u2019s anomaly: choice of operation"],"prefix":"10.1017","volume":"25","author":[{"given":"Christopher J.","family":"Knott-Craig","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Thittamaranahalli Kariyappa S.","family":"Kumar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alejandro R.","family":"Arevalo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vijaya M.","family":"Joshi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"56","published-online":{"date-parts":[[2014,9,24]]},"reference":[{"key":"S1047951114001747_ref2","first-page":"2219","volume-title":"Sabiston and Spencer Surgery of the Chest","author":"Dearani","year":"2005"},{"key":"S1047951114001747_ref18","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2011.01.029"},{"key":"S1047951114001747_ref21","doi-asserted-by":"publisher","DOI":"10.1016\/S0003-4975(97)00090-8"},{"key":"S1047951114001747_ref13","doi-asserted-by":"publisher","DOI":"10.1053\/j.pcsu.2009.01.023"},{"key":"S1047951114001747_ref16","doi-asserted-by":"publisher","DOI":"10.1053\/j.pcsu.2007.01.008"},{"key":"S1047951114001747_ref11","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2009.07.062"},{"key":"S1047951114001747_ref9","doi-asserted-by":"crossref","first-page":"1082","DOI":"10.1016\/S0022-5223(19)36627-9","article-title":"Ebstein\u2019s anomaly appearing in the neonate. 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