{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,27]],"date-time":"2026-03-27T19:22:13Z","timestamp":1774639333747,"version":"3.50.1"},"reference-count":18,"publisher":"Cambridge University Press (CUP)","issue":"12","license":[{"start":{"date-parts":[[2024,10,18]],"date-time":"2024-10-18T00:00:00Z","timestamp":1729209600000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/www.cambridge.org\/core\/terms"}],"content-domain":{"domain":["cambridge.org"],"crossmark-restriction":true},"short-container-title":["Cardiol Young"],"published-print":{"date-parts":[[2024,12]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec id=\"S1047951124026519_as1\"><jats:title>Background:<\/jats:title><jats:p>Children with left aortic arch and aberrant right subclavian artery may present with either respiratory or swallowing symptoms beyond the classically described solid-food dysphagia. We describe the clinical features and outcomes of children undergoing surgical repair of an aberrant right subclavian artery.<\/jats:p><\/jats:sec><jats:sec id=\"S1047951124026519_as2\"><jats:title>Materials and methods:<\/jats:title><jats:p>This was a retrospective review of children undergoing repair of an aberrant right subclavian artery between 2017 and 2022. Primary outcome was symptom improvement. Pre- and post-operative questionnaires were used to assess dysphagia (PEDI-EAT-10) and respiratory symptoms (PEDI-TBM-7). Paired <jats:italic>t<\/jats:italic>-test and Fisher\u2019s exact test were used to analyse symptom resolution. Secondary outcomes included perioperative outcomes, complications, and length of stay.<\/jats:p><\/jats:sec><jats:sec id=\"S1047951124026519_as3\"><jats:title>Results:<\/jats:title><jats:p>Twenty children, median age 2 years (IQR 1\u201311), were included. All presented with swallowing symptoms, and 14 (70%) also experienced respiratory symptoms. Statistically significant improvements in symptoms were reported for both respiratory and swallowing symptoms. Paired (pre- and post-op) PEDI-EAT-10 and PEDI-TBM-7 scores were obtained for nine patients, resulting in mean (\u00b1 SD) scores decreasing (improvement in symptoms) from 19.9 (\u00b1 9.3) to 2.4 (\u00b1 2.5) <jats:italic>p<\/jats:italic> = 0.001, and 8.7 (\u00b1 4.7) to 2.8 (\u00b1 4.0) <jats:italic>p<\/jats:italic> = 0.006, respectively. Reoperation was required in one patient due to persistent dysphagia from an oesophageal stricture. Other complications included lymphatic drainage (<jats:italic>n<\/jats:italic> = 4) and transient left vocal cord hypomobility (<jats:italic>n<\/jats:italic> = 1).<\/jats:p><\/jats:sec><jats:sec id=\"S1047951124026519_as4\"><jats:title>Conclusion:<\/jats:title><jats:p>Children with a left aortic arch with aberrant right subclavian artery can present with oesophageal and respiratory symptoms beyond solid food dysphagia. A thorough multidisciplinary evaluation is imperative to identify patients who can benefit from surgical repair, which appears to be safe and effective.<\/jats:p><\/jats:sec>","DOI":"10.1017\/s1047951124026519","type":"journal-article","created":{"date-parts":[[2024,10,18]],"date-time":"2024-10-18T08:41:53Z","timestamp":1729240913000},"page":"2663-2669","update-policy":"https:\/\/doi.org\/10.1017\/policypage","source":"Crossref","is-referenced-by-count":1,"title":["Left aortic arch and aberrant right subclavian artery in children: spectrum of symptoms and response to surgical intervention"],"prefix":"10.1017","volume":"34","author":[{"ORCID":"https:\/\/orcid.org\/0009-0007-2649-2217","authenticated-orcid":false,"given":"Lianne","family":"Cole","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jennifer","family":"Brown","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jessica","family":"Yasuda","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Peter","family":"Ngo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Steven 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thoracic paravertebral block-radiological evidence of spread to stellate ganglion and fascial anatomy facilitating the spread","volume":"60","author":"Sripriya","year":"2022","journal-title":"Asian J Anesthesiol"},{"key":"S1047951124026519_ref18","doi-asserted-by":"publisher","DOI":"10.1016\/j.jvs.2023.01.014"},{"key":"S1047951124026519_ref17","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2020.04.018"},{"key":"S1047951124026519_ref5","doi-asserted-by":"publisher","DOI":"10.1093\/icvts\/ivaa091"},{"key":"S1047951124026519_ref15","first-page":"306","article-title":"Posterior tracheopexy for tracheomalacia: study of clinical and radiological consequences on esophagus","volume":"34","author":"Torre","year":"2023","journal-title":"Eur J Pediatr 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