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Despite controlled inflammation and favourable coronary evolution under immunosuppressive therapy, the patient required surgical valve repair. This case highlights the unpredictable nature of complex Kawasaki disease phenotypes and underscores the need for comprehensive vascular imaging and lifelong follow-up, as atypical features may lead to independent complications.<\/jats:p>","DOI":"10.1017\/s1047951126112086","type":"journal-article","created":{"date-parts":[[2026,5,21]],"date-time":"2026-05-21T06:12:34Z","timestamp":1779343954000},"page":"1064-1067","update-policy":"https:\/\/doi.org\/10.1017\/policypage","source":"Crossref","is-referenced-by-count":0,"title":["Giant coronary aneurysm and bivalvular insufficiency in severe Kawasaki disease: a case report"],"prefix":"10.1017","volume":"36","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0165-9603","authenticated-orcid":false,"given":"L\u00e9a","family":"Linglart","sequence":"first","affiliation":[{"id":[{"id":"https:\/\/ror.org\/00pg5jh14","id-type":"ROR","asserted-by":"publisher"}],"name":"M3C-Necker University Hospital"},{"name":"Hopital universitaire Necker-Enfants malades"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Regis","family":"Gaudin","sequence":"additional","affiliation":[{"name":"Hopital universitaire Necker-Enfants malades"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Damien","family":"Bonnet","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/00pg5jh14","id-type":"ROR","asserted-by":"publisher"}],"name":"M3C-Necker University Hospital"},{"name":"Paris Cit\u00e9 University"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fanny","family":"Bajolle","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/00pg5jh14","id-type":"ROR","asserted-by":"publisher"}],"name":"M3C-Necker University Hospital"},{"name":"Paris Cit\u00e9 University"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"56","published-online":{"date-parts":[[2026,5,21]]},"reference":[{"key":"S1047951126112086_ref12","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2015.04.036"},{"key":"S1047951126112086_ref8","first-page":"60516","article-title":"Kawasaki disease complicated with mitral insufficiency. 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