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Leucine tolerance increased progressively from the 22nd week of gestation from 350 to 2100 mg\/day. The risk of metabolic decompensation in the postpartum period can be minimized by careful monitoring of the mother after delivery.<\/jats:p>","DOI":"10.1023\/a:1005396823030","type":"journal-article","created":{"date-parts":[[2002,12,21]],"date-time":"2002-12-21T21:48:34Z","timestamp":1040507314000},"page":"89-94","source":"Crossref","is-referenced-by-count":36,"title":["Pregnancy in a woman with maple syrup urine disease"],"prefix":"10.1002","volume":"21","author":[{"given":"S.","family":"Gr\u00ffnewald","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"F.","family":"Hinrichs","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"U.","family":"Wendel","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[1998,4]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0146-0005(05)80024-2"},{"key":"e_1_2_1_3_1","volume-title":"N\u00e4hrwerttabelle f\u00fcr die Ern\u00e4hrung bei angeborenen St\u00f6rungen des Aminos\u00e4urenstoffwechsels","author":"Arbeitsgemeinschaft f\u00fcr P\u00e4diatrische Di\u00e4tetik","year":"1996"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM199006073222307"},{"key":"e_1_2_1_5_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF00714298"},{"key":"e_1_2_1_6_1","doi-asserted-by":"publisher","DOI":"10.1007\/PL00014241"},{"key":"e_1_2_1_7_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0140-6736(05)64755-1"},{"key":"e_1_2_1_8_1","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9378(95)90049-7"},{"key":"e_1_2_1_9_1","first-page":"126","article-title":"Pregnancy and von Gierke's disease","volume":"47","author":"Farber M","year":"1976","journal-title":"Obstet Gynecol"},{"key":"e_1_2_1_10_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF01954383"},{"key":"e_1_2_1_11_1","doi-asserted-by":"crossref","first-page":"500","DOI":"10.1542\/peds.33.4.500","article-title":"Free amino acids of cord plasma as compared with maternal plasma during pregnancy","volume":"20","author":"Ghadimi H","year":"1964","journal-title":"Pediatrics"},{"key":"e_1_2_1_12_1","doi-asserted-by":"publisher","DOI":"10.1007\/PL00014238"},{"key":"e_1_2_1_13_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(84)80367-4"},{"key":"e_1_2_1_14_1","volume-title":"Die Zusammensetzung der Lebensmittel","author":"Souci SW","year":"1994"},{"key":"e_1_2_1_15_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320440523"},{"key":"e_1_2_1_16_1","first-page":"115","article-title":"Maternal pyridoxine\u2010unresponsive homocystinuria: normal outcome of a pregnancy","volume":"59","author":"Walter JH","year":"1994","journal-title":"Abstracts 32nd SSIEM Annual Symposium"},{"key":"e_1_2_1_17_1","doi-asserted-by":"publisher","DOI":"10.7326\/0003-4819-120-3-199402010-00007"},{"key":"e_1_2_1_18_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF01799836"}],"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1023%2FA%3A1005396823030","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1023\/A%3A1005396823030","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T22:48:08Z","timestamp":1694818088000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1023\/A%3A1005396823030"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1998,4]]},"references-count":17,"journal-issue":{"issue":"2","published-print":{"date-parts":[[1998,4]]}},"alternative-id":["10.1023\/A:1005396823030"],"URL":"https:\/\/doi.org\/10.1023\/a:1005396823030","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[1998,4]]}}}