{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,22]],"date-time":"2026-10-22T04:35:34Z","timestamp":1792643734775,"version":"4.5.0"},"reference-count":3,"publisher":"Wiley","issue":"1","license":[{"start":{"date-parts":[[2003,7,1]],"date-time":"2003-07-01T00:00:00Z","timestamp":1057017600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[2003,7]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>\n                    <jats:bold>Summary:<\/jats:bold>\n                    We report a 7\u2010year\u2010old girl with hyperinsulinaemic hypoglycaemia and hepatomegaly due to congenital disorder of glycosylation (CDG) Ib without gastrointestinal symptoms. Oral mannose therapy produced clinical and biochemical normalization after 2 years of treatment.\n                  <\/jats:p>","DOI":"10.1023\/a:1024044017385","type":"journal-article","created":{"date-parts":[[2003,9,12]],"date-time":"2003-09-12T17:07:28Z","timestamp":1063386448000},"page":"83-85","source":"Crossref","is-referenced-by-count":24,"title":["Congenital disorder of glycosylation Ib (CDG\u2010Ib) without gastrointestinal symptoms"],"prefix":"10.1002","volume":"26","author":[{"given":"D.","family":"Penel\u2010Capelle","sequence":"first","affiliation":[{"name":"Unit of Metabolic Diseases, Department of Pediatrics Lille University Children's Hospital  Lille France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D.","family":"Dobbelaere","sequence":"additional","affiliation":[{"name":"Unit of Metabolic Diseases, Department of Pediatrics Lille University Children's Hospital  Lille France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J.","family":"Jaeken","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Center for Metabolic Disease University of Leuven, cLeuven  Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.","family":"Klein","sequence":"additional","affiliation":[{"name":"Laboratory of Biochemistry Hospital Calmette  Lille"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"M.","family":"Cartigny","sequence":"additional","affiliation":[{"name":"Unit of Endocrinology, Department of Pediatrics Lille University Children's Hospital  Lille France"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2003,7]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(99)70103-4"},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1097\/00019052-200112000-00021"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1086\/301873"}],"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1023%2FA%3A1024044017385","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1023\/A%3A1024044017385","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T09:05:43Z","timestamp":1694768743000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1023\/A%3A1024044017385"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2003,7]]},"references-count":3,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2003,7]]}},"alternative-id":["10.1023\/A:1024044017385"],"URL":"https:\/\/doi.org\/10.1023\/a:1024044017385","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[2003,7]]}}}