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Combined excretion was 10\u2010fold elevated in comparison to control during inadequate glucose maintenance, and still elevated following dietary improvement. 3MGC acid excretion correlated with plasma lactate and glucose. We speculate that imbalanced gluconeogenesis and de novo cholesterol synthesis result in secondarily increased 3MGC\/3MGR production.<\/jats:p>","DOI":"10.1023\/b:boli.0000005603.04633.21","type":"journal-article","created":{"date-parts":[[2003,12,1]],"date-time":"2003-12-01T18:29:34Z","timestamp":1070303374000},"page":"705-709","source":"Crossref","is-referenced-by-count":11,"title":["Case Report: 3\u2010Methyglutaconic Aciduria in a Chinese Patient with Glycogen Storage Disease Ib"],"prefix":"10.1002","volume":"26","author":[{"given":"L. K.","family":"Law","sequence":"first","affiliation":[{"name":"Department of Chemical Pathology The Chinese University of Hong Kong, Prince of Wales Hospital  N.T. 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