{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,20]],"date-time":"2026-05-20T23:13:29Z","timestamp":1779318809174,"version":"3.51.4"},"reference-count":0,"publisher":"Hogrefe Publishing Group","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Vasa"],"published-print":{"date-parts":[[2000,2,1]]},"abstract":"<jats:p> We describe a patient with the previously unseen combination of Maffucci\u2019s and Stewart Treves syndrome who presented with an angiosarcoma of the hand. Maffucci\u2019s syndrome is characterized by the presence of multiple enchondroma and soft tissue hemangioma. The syndrome is a rare nonhereditary condition with a usual onset in childhood. Malignant transformations are a common feature of this syndrome. In 1948, Stewart and Treves first described six cases of lymphangiosarcoma after radical mastectomy. This syndrome is an unusual form of angiosarcoma occuring as a complication of lymphedema. Chronic lymphedema and lymphangiectasia preceding lymphangiosarcoma may not only be induced by radical mastectomy with axillary lymph node dissection and postoperative radiation therapy. Posttraumatic, congenital or spontaneous chronic lymphedema may also be associated with lymphangiosarcoma. A time interval of many years seems to be required before malignant transformation develops. Generally the syndrome has a very poor prognosis. Both syndromes described above are of a rare frequency. We report this case because of prior unknown coincidence of both syndromes. <\/jats:p>","DOI":"10.1024\/0301-1526.29.1.71","type":"journal-article","created":{"date-parts":[[2006,1,31]],"date-time":"2006-01-31T12:25:08Z","timestamp":1138710308000},"page":"71-73","source":"Crossref","is-referenced-by-count":16,"title":["H\u00e4mangiosarkom der linken Hand bei einem Patienten mit der seltenen Kombination eines Maffucci\u2019s mit einem Stewart Treves Syndrom"],"prefix":"10.1024","volume":"29","author":[{"family":"Bach","sequence":"first","affiliation":[{"name":"Department of Plastic and Hand Surgery, University of Freiburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"family":"Walgenbach","sequence":"additional","affiliation":[{"name":"Department of Plastic and Hand Surgery, University of Freiburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Raymund E.","family":"Horch","sequence":"additional","affiliation":[{"name":"Department of Plastic and Hand Surgery, University of Freiburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"101","container-title":["Vasa"],"original-title":[],"language":"de","link":[{"URL":"https:\/\/econtent.hogrefe.com\/doi\/pdf\/10.1024\/0301-1526.29.1.71","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,5,8]],"date-time":"2022-05-08T11:09:18Z","timestamp":1652008158000},"score":1,"resource":{"primary":{"URL":"https:\/\/econtent.hogrefe.com\/doi\/10.1024\/0301-1526.29.1.71"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2000,2,1]]},"references-count":0,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2000,2,1]]}},"alternative-id":["10.1024\/0301-1526.29.1.71"],"URL":"https:\/\/doi.org\/10.1024\/0301-1526.29.1.71","relation":{},"ISSN":["0301-1526","1664-2872"],"issn-type":[{"value":"0301-1526","type":"print"},{"value":"1664-2872","type":"electronic"}],"subject":[],"published":{"date-parts":[[2000,2,1]]}}}