{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,30]],"date-time":"2026-04-30T09:55:55Z","timestamp":1777542955714,"version":"3.51.4"},"reference-count":37,"publisher":"Elsevier BV","issue":"3","license":[{"start":{"date-parts":[[1973,9,1]],"date-time":"1973-09-01T00:00:00Z","timestamp":115689600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2015,12,7]],"date-time":"2015-12-07T00:00:00Z","timestamp":1449446400000},"content-version":"vor","delay-in-days":15437,"URL":"http:\/\/www.elsevier.com\/open-access\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Kidney International"],"published-print":{"date-parts":[[1973,9]]},"DOI":"10.1038\/ki.1973.103","type":"journal-article","created":{"date-parts":[[2007,6,20]],"date-time":"2007-06-20T13:00:24Z","timestamp":1182344424000},"page":"216-228","source":"Crossref","is-referenced-by-count":44,"title":["Progressive and nonprogressive hereditary chronic nephritis"],"prefix":"10.1016","volume":"4","author":[{"given":"Jean-Pierre","family":"Gr\u00fcnfeld","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Etienne P.","family":"Bois","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nicole","family":"Hinglais","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1038\/ki.1973.103_bb0010","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1056\/NEJM196707132770206","article-title":"The hereditary renal diseases","volume":"277","author":"Perkoff","year":"1967","journal-title":"N Engl J Med"},{"key":"10.1038\/ki.1973.103_bb0015","first-page":"217","article-title":"Benign recurrent hematuria","volume":"109","author":"Ayoub","year":"1965","journal-title":"Am J Dis Child"},{"key":"10.1038\/ki.1973.103_bb0020","doi-asserted-by":"crossref","first-page":"207","DOI":"10.1016\/S0022-3476(66)80321-9","article-title":"Familial and nonfamilial benign hematuria","volume":"69","author":"McConville","year":"1966","journal-title":"J Pediatr"},{"key":"10.1038\/ki.1973.103_bb0025","first-page":"135","article-title":"Hereditary nephropathy without deafness","volume":"114","author":"Dockhorn","year":"1967","journal-title":"Am J Dis Child"},{"key":"10.1038\/ki.1973.103_bb0030","doi-asserted-by":"crossref","first-page":"764","DOI":"10.1016\/0002-9343(71)90184-7","article-title":"Hereditary nephritis: Clinical spectrum and mode of inheritance in five new kindreds","volume":"50","author":"Chazan","year":"1971","journal-title":"Am J Med"},{"key":"10.1038\/ki.1973.103_bb0035","first-page":"401","article-title":"Hereditary nephritis","volume":"90","author":"Chappell","year":"1960","journal-title":"Am J Dis Child"},{"key":"10.1038\/ki.1973.103_bb0040","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1001\/archpedi.1969.02100030155006","article-title":"Familial nephritis associated with the nephrotic syndrome in a family with severe involvement in females","volume":"117","author":"Albert","year":"1969","journal-title":"Am J Dis Child"},{"key":"10.1038\/ki.1973.103_bb0045","first-page":"473","article-title":"Characteristic ultrastructural lesion of the glomerular basement membrane in progressive hereditary nephritis (Alport's syndrome)","volume":"27","author":"Hinglais","year":"1972","journal-title":"Lab Invest"},{"key":"10.1038\/ki.1973.103_bb0050","series-title":"Nephrology","first-page":"163","author":"Hamburger","year":"1968"},{"key":"10.1038\/ki.1973.103_bb0055","series-title":"Nephrology","first-page":"216","author":"Hamburger","year":"1968"},{"key":"10.1038\/ki.1973.103_bb0060","doi-asserted-by":"crossref","first-page":"171","DOI":"10.1016\/0002-9343(61)90107-3","article-title":"Hereditary nephropathy, deafness and renal foam cells","volume":"31","author":"Whalen","year":"1961","journal-title":"Am J Med"},{"key":"10.1038\/ki.1973.103_bb0065","doi-asserted-by":"crossref","first-page":"753","DOI":"10.1016\/S0002-9343(70)80057-2","article-title":"Familial hereditary nephropathy (Alport's syndrome)","volume":"49","author":"Purriel","year":"1970","journal-title":"Am J Med"},{"key":"10.1038\/ki.1973.103_bb0070","doi-asserted-by":"crossref","first-page":"37","DOI":"10.1016\/S0022-3476(70)80042-7","article-title":"Diffuse familial nephropathy: A clinicopathological study","volume":"77","author":"Kaufman","year":"1970","journal-title":"J Pediat"},{"key":"10.1038\/ki.1973.103_bb0075","doi-asserted-by":"crossref","first-page":"967","DOI":"10.1542\/peds.35.6.967","article-title":"Hereditary renal dysfunction and deafness","volume":"35","author":"Cassady","year":"1965","journal-title":"Pediatrics"},{"key":"10.1038\/ki.1973.103_bb0080","doi-asserted-by":"crossref","first-page":"390","DOI":"10.1136\/bjo.50.7.390","article-title":"Anterior lenticonus and Alport's syndrome","volume":"50","author":"Arnott","year":"1966","journal-title":"Br J Ophthalmol"},{"key":"10.1038\/ki.1973.103_bb0085","doi-asserted-by":"crossref","first-page":"241","DOI":"10.1542\/peds.20.2.241","article-title":"Hereditary renal disease associated with nerve deafness and ocular lesions","volume":"26","author":"Goldbloom","year":"1957","journal-title":"Pediatrics"},{"key":"10.1038\/ki.1973.103_bb0090","first-page":"140","article-title":"Hereditary factors in chronic Bright's disease: A study of two affected kindreds","volume":"70","author":"Robin","year":"1957","journal-title":"Trans Assoc Am Physicians"},{"key":"10.1038\/ki.1973.103_bb0095","series-title":"Hereditary Developmental and immunologic Aspects of Kidney Disease","first-page":"3","article-title":"Hereditary hematuria","author":"Opitz","year":"1962"},{"key":"10.1038\/ki.1973.103_bb0100","first-page":"649","article-title":"N\u00e9phropathie h\u00e9maturique familiale avec surdit\u00e9 (syndrome d'Alport): A propos de 2 s\u00e9ries d'observations","volume":"20","author":"Chaptal","year":"1965","journal-title":"Pediatrie"},{"key":"10.1038\/ki.1973.103_bb0105","doi-asserted-by":"crossref","first-page":"156","DOI":"10.1001\/archinte.1968.00300070060011","article-title":"Hereditary chronic nephritis complicated by nephrotic syndrome","volume":"122","author":"Knepshield","year":"1968","journal-title":"Arch Intern Med"},{"key":"10.1038\/ki.1973.103_bb0110","doi-asserted-by":"crossref","first-page":"459","DOI":"10.1001\/archinte.1970.00310030069005","article-title":"Hereditary nephritis with the nephrotic syndrome","volume":"125","author":"Felts","year":"1970","journal-title":"Arch Intern Med"},{"key":"10.1038\/ki.1973.103_bb0115","doi-asserted-by":"crossref","first-page":"941","DOI":"10.1016\/S0140-6736(60)90834-5","article-title":"Familial glomerulonephritis and aminoaciduria","volume":"1","author":"Wallace","year":"1960","journal-title":"Lancet"},{"key":"10.1038\/ki.1973.103_bb0120","doi-asserted-by":"crossref","first-page":"1075","DOI":"10.1016\/S0140-6736(64)92605-4","article-title":"Hyperprolinemia and hereditary nephritis","volume":"3","author":"Kopelman","year":"1964","journal-title":"Lancet"},{"key":"10.1038\/ki.1973.103_bb0125","doi-asserted-by":"crossref","first-page":"545","DOI":"10.1203\/00006450-196911000-00004","article-title":"Hereditary nephritis : Early clinical, functional and morphological studies","volume":"3","author":"Antonovych","year":"1969","journal-title":"Pediatr Res"},{"key":"10.1038\/ki.1973.103_bb0130","first-page":"396","article-title":"Hereditary nephropathy with hematuria (Alport's syndrome)","volume":"102","author":"Chiricosta","year":"1970","journal-title":"Can Med Assoc J"},{"key":"10.1038\/ki.1973.103_bb0135","first-page":"563","article-title":"Alport's syndrome of hereditary nephritis and deafness","volume":"37","author":"Crawfurd","year":"1968","journal-title":"Q J Med"},{"key":"10.1038\/ki.1973.103_bb0140","first-page":"29","article-title":"G\u00e9n\u00e9tique du syndrome d'Alport : N\u00e9phropathie familiale avec surdit\u00e9","volume":"12","author":"Feingold","year":"1971","journal-title":"Humangenetik"},{"key":"10.1038\/ki.1973.103_bb0145","doi-asserted-by":"crossref","first-page":"331","DOI":"10.1111\/j.1399-0004.1971.tb00293.x","article-title":"Genetics of hereditary nephropathy with deafness (Alport's disease)","volume":"2","author":"Preus","year":"1971","journal-title":"Clin Genet"},{"key":"10.1038\/ki.1973.103_bb0150","doi-asserted-by":"crossref","first-page":"733","DOI":"10.1001\/archinte.1958.00260220049005","article-title":"A follow-up study of hereditary chronic nephritis","volume":"102","author":"Perkoff","year":"1958","journal-title":"Arch Intern Med"},{"key":"10.1038\/ki.1973.103_bb0155","first-page":"289","article-title":"Syndrome of hereditary hematuria, nephropathy and deafness","volume":"33","author":"Sturtz","year":"1958","journal-title":"Mayo Clin Proc"},{"key":"10.1038\/ki.1973.103_bb0160","doi-asserted-by":"crossref","first-page":"737","DOI":"10.1016\/0002-9343(63)90237-7","article-title":"Hereditary nephritis: Report of a kindred","volume":"35","author":"Mulrow","year":"1963","journal-title":"Am J Med"},{"key":"10.1038\/ki.1973.103_bb0165","series-title":"Actualit\u00e9s N\u00e9phrologiques de l'H\u00f4pital Necker","first-page":"29","article-title":"La n\u00e9phropathie h\u00e9r\u00e9ditaire avec surdit\u00e9 et atteinte oculaire","author":"Junod","year":"1963"},{"key":"10.1038\/ki.1973.103_bb0170","first-page":"7","article-title":"Le syndrome d'Alport ou n\u00e9phropathie h\u00e9r\u00e9ditaire avec surdit\u00e9: Nouvelle \u00e9tude familiale","volume":"15","author":"Burguet","year":"1966","journal-title":"J Genet Hum"},{"key":"10.1038\/ki.1973.103_bb0175","doi-asserted-by":"crossref","first-page":"451","DOI":"10.1001\/archinte.1970.00310030061004","article-title":"Hereditary nephritis in the Negro: Report of a kindred","volume":"125","author":"Grace","year":"1970","journal-title":"Arch Intern Med"},{"key":"10.1038\/ki.1973.103_bb0180","first-page":"271","article-title":"Le syndrome d'Alport : Etude clinique et g\u00e9n\u00e9tique","volume":"17","author":"Beaudoing","year":"1970","journal-title":"Ann Pediatr (Paris)"},{"key":"10.1038\/ki.1973.103_bb0185","first-page":"555","article-title":"A family showing hereditary nephropathy","volume":"23","author":"Pashayazn","year":"1971","journal-title":"Am J Hum Genet"},{"key":"10.1038\/ki.1973.103_bb0190","first-page":"757","article-title":"Contribution \u00e0 l'\u00e9tude du syndrome d'Alport: A propos d'un cas","volume":"18","author":"Schneegans","year":"1971","journal-title":"Ann Pediatr (Paris)"}],"container-title":["Kidney International"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S008525381531228X?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S008525381531228X?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2024,2,15]],"date-time":"2024-02-15T05:10:28Z","timestamp":1707973828000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S008525381531228X"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1973,9]]},"references-count":37,"journal-issue":{"issue":"3","published-print":{"date-parts":[[1973,9]]}},"alternative-id":["S008525381531228X"],"URL":"https:\/\/doi.org\/10.1038\/ki.1973.103","relation":{},"ISSN":["0085-2538"],"issn-type":[{"value":"0085-2538","type":"print"}],"subject":[],"published":{"date-parts":[[1973,9]]}}}