{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,8]],"date-time":"2026-07-08T10:12:03Z","timestamp":1783505523423,"version":"3.55.0"},"reference-count":6,"publisher":"Springer Science and Business Media LLC","issue":"3","license":[{"start":{"date-parts":[[2014,6,16]],"date-time":"2014-06-16T00:00:00Z","timestamp":1402876800000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Pediatr Res"],"published-print":{"date-parts":[[2014,9]]},"DOI":"10.1038\/pr.2014.79","type":"journal-article","created":{"date-parts":[[2014,6,16]],"date-time":"2014-06-16T15:58:23Z","timestamp":1402934303000},"page":"321-321","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["Nasal NO, high-speed video microscopy, electron microscopy, and genetics: a primary ciliary dyskinesia puzzle to complete"],"prefix":"10.1038","volume":"76","author":[{"given":"Deborah","family":"Snijders","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ilaria","family":"Bertozzi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Angelo","family":"Barbato","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2014,6,16]]},"reference":[{"key":"BFpr201479_CR1","doi-asserted-by":"publisher","first-page":"158","DOI":"10.1038\/pr.2013.200","volume":"75","author":"A Horani","year":"2014","unstructured":"Horani A, Brody SL, Ferkol TW . Picking up speed: advances in the genetics of primary ciliary dyskinesia. Pediatr Res 2014;75:158\u201364.","journal-title":"Pediatr Res"},{"key":"BFpr201479_CR2","doi-asserted-by":"publisher","first-page":"1264","DOI":"10.1183\/09031936.00176608","volume":"34","author":"A Barbato","year":"2009","unstructured":"Barbato A, Frischer T, Kuehni CE, et al. Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children. Eur Respir J 2009;34:1264\u201376.","journal-title":"Eur Respir J"},{"key":"BFpr201479_CR3","doi-asserted-by":"publisher","first-page":"14","DOI":"10.1186\/2046-2530-1-14","volume":"1","author":"CM Smith","year":"2012","unstructured":"Smith CM, Djakow J, Free RC, et al. ciliaFA: a research tool for automated, high-throughput measurement of ciliary beat frequency using freely available software. Cilia 2012;1:14.","journal-title":"Cilia"},{"key":"BFpr201479_CR4","doi-asserted-by":"publisher","first-page":"175","DOI":"10.2500\/ajra.2010.24.3448","volume":"24","author":"M Armengot","year":"2010","unstructured":"Armengot M, Milara J, Mata M, Carda C, Cortijo J . Cilia motility and structure in primary and secondary ciliary dyskinesia. Am J Rhinol Allergy 2010;24:175\u201380.","journal-title":"Am J Rhinol Allergy"},{"key":"BFpr201479_CR5","doi-asserted-by":"publisher","first-page":"518","DOI":"10.1016\/S0091-6749(03)01799-8","volume":"112","author":"MA Chilvers","year":"2003","unstructured":"Chilvers MA, Rutman A, O\u2019Callaghan C . Ciliary beat pattern is associated with specific ultrastructural defects in primary ciliary dyskinesia. J Allergy Clin Immunol 2003;112:518\u201324.","journal-title":"J Allergy Clin Immunol"},{"key":"BFpr201479_CR6","doi-asserted-by":"publisher","first-page":"78","DOI":"10.1186\/1750-1172-7-78","volume":"7","author":"JF Papon","year":"2012","unstructured":"Papon JF, Bassinet L, Cariou-Patron G, et al. Quantitative analysis of ciliary beating in primary ciliary dyskinesia: a pilot study. Orphanet J Rare Dis 2012;7:78.","journal-title":"Orphanet J Rare Dis"}],"container-title":["Pediatric Research"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.nature.com\/articles\/pr201479.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/www.nature.com\/articles\/pr201479","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/www.nature.com\/articles\/pr201479.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,5,20]],"date-time":"2023-05-20T20:57:14Z","timestamp":1684616234000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.nature.com\/articles\/pr201479"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2014,6,16]]},"references-count":6,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2014,9]]}},"alternative-id":["BFpr201479"],"URL":"https:\/\/doi.org\/10.1038\/pr.2014.79","relation":{},"ISSN":["0031-3998","1530-0447"],"issn-type":[{"value":"0031-3998","type":"print"},{"value":"1530-0447","type":"electronic"}],"subject":[],"published":{"date-parts":[[2014,6,16]]},"assertion":[{"value":"16 June 2014","order":1,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}}]}}