{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,21]],"date-time":"2026-09-21T19:21:14Z","timestamp":1790018474115,"version":"4.0.1"},"reference-count":43,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2020,10,22]],"date-time":"2020-10-22T00:00:00Z","timestamp":1603324800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2020,10,22]],"date-time":"2020-10-22T00:00:00Z","timestamp":1603324800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"funder":[{"DOI":"10.13039\/100000968","name":"American Heart Association","doi-asserted-by":"publisher","award":["16PRE30190012"],"award-info":[{"award-number":["16PRE30190012"]}],"id":[{"id":"10.13039\/100000968","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000050","name":"National Heart, Lung, and Blood Institute","doi-asserted-by":"publisher","award":["R01 HL083300"],"award-info":[{"award-number":["R01 HL083300"]}],"id":[{"id":"10.13039\/100000050","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000050","name":"National Heart, Lung, and Blood Institute","doi-asserted-by":"publisher","award":["P50-HL74731"],"award-info":[{"award-number":["P50-HL74731"]}],"id":[{"id":"10.13039\/100000050","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000050","name":"National Heart, Lung, and Blood Institute","doi-asserted-by":"publisher","award":["R01 HL092981-01A1"],"award-info":[{"award-number":["R01 HL092981-01A1"]}],"id":[{"id":"10.13039\/100000050","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/501100000274","name":"British Heart Foundation","doi-asserted-by":"publisher","id":[{"id":"10.13039\/501100000274","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000097","name":"National Center for Research Resources","doi-asserted-by":"publisher","award":["M01-RR-000240, RR024134"],"award-info":[{"award-number":["M01-RR-000240, RR024134"]}],"id":[{"id":"10.13039\/100000097","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100006108","name":"National Center for Advancing Translational Sciences","doi-asserted-by":"publisher","award":["UL1TR000003"],"award-info":[{"award-number":["UL1TR000003"]}],"id":[{"id":"10.13039\/100006108","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100006108","name":"National Center for Advancing Translational Sciences","doi-asserted-by":"publisher","award":["UL1TR002378"],"award-info":[{"award-number":["UL1TR002378"]}],"id":[{"id":"10.13039\/100006108","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000057","name":"National Institute of General Medical Sciences","doi-asserted-by":"publisher","award":["GM117946"],"award-info":[{"award-number":["GM117946"]}],"id":[{"id":"10.13039\/100000057","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000071","name":"National Institute of Child Health and Human Development","doi-asserted-by":"publisher","award":["R01 HD38979"],"award-info":[{"award-number":["R01 HD38979"]}],"id":[{"id":"10.13039\/100000071","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Sci Rep"],"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Atrioventricular septal defects (AVSD) are a severe congenital heart defect present in individuals with Down syndrome (DS) at a\u2009&gt;\u20092000-fold increased prevalence compared to the general population. This study aimed to identify risk-associated genes and pathways and to examine a potential polygenic contribution to AVSD in DS. We analyzed a total cohort of 702 individuals with DS with or without AVSD, with genomic data from whole exome sequencing, whole genome sequencing, and\/or array-based imputation. We utilized sequence kernel association testing and polygenic risk score (PRS) methods to examine rare and common variants. Our findings suggest that the Notch pathway, particularly<jats:italic>NOTCH4<\/jats:italic>, as well as genes involved in the ciliome including<jats:italic>CEP290<\/jats:italic>may play a role in AVSD in DS. These pathways have also been implicated in DS-associated AVSD in prior studies. A polygenic component for AVSD in DS has not been examined previously. Using weights based on the largest genome-wide association study of congenital heart defects available (2594 cases and 5159 controls; all general population samples), we found PRS to be associated with AVSD with odds ratios ranging from 1.2 to 1.3 per standard deviation increase in PRS and corresponding liability r<jats:sup>2<\/jats:sup>values of approximately 1%, suggesting at least a small polygenic contribution to DS-associated AVSD. Future studies with larger sample sizes will improve identification and quantification of genetic contributions to AVSD in DS.<\/jats:p>","DOI":"10.1038\/s41598-020-74650-4","type":"journal-article","created":{"date-parts":[[2020,10,22]],"date-time":"2020-10-22T10:03:14Z","timestamp":1603360994000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":23,"title":["Identifying genetic factors that contribute to the increased risk of congenital heart defects in infants with Down syndrome"],"prefix":"10.1038","volume":"10","author":[{"given":"Cristina E.","family":"Trevino","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Aaron M.","family":"Holleman","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Holly","family":"Corbitt","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cheryl L.","family":"Maslen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tracie C.","family":"Rosser","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David J.","family":"Cutler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"H. Richard","family":"Johnston","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Benjamin L.","family":"Rambo-Martin","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jai","family":"Oberoi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kenneth J.","family":"Dooley","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"George T.","family":"Capone","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Roger H.","family":"Reeves","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Heather J.","family":"Cordell","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bernard D.","family":"Keavney","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.J.","family":"Agopian","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Elizabeth","family":"Goldmuntz","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Peter J.","family":"Gruber","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"suffix":"Jr.","given":"James E.","family":"O\u2019Brien","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Douglas C.","family":"Bittel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lalita","family":"Wadhwa","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Clifford L.","family":"Cua","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ivan P.","family":"Moskowitz","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jennifer G.","family":"Mulle","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael P.","family":"Epstein","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stephanie L.","family":"Sherman","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael E.","family":"Zwick","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2020,10,22]]},"reference":[{"key":"74650_CR1","doi-asserted-by":"publisher","first-page":"79","DOI":"10.1016\/S0022-3476(89)80605-5","volume":"114","author":"C Ferencz","year":"1989","unstructured":"Ferencz, C. et al. Congenital cardiovascular malformations associated with chromosome abnormalities: an epidemiologic study. J. Pediatr. 114, 79\u201386 (1989).","journal-title":"J. Pediatr."},{"key":"74650_CR2","doi-asserted-by":"publisher","first-page":"555","DOI":"10.1002\/ajmg.a.33874","volume":"155A","author":"RJ Hartman","year":"2011","unstructured":"Hartman, R. J. et al. Descriptive study of nonsyndromic atrioventricular septal defects in the National Birth Defects Prevention Study, 1997\u20132005. Am. J. Med. Genet. A 155A, 555\u2013564 (2011).","journal-title":"Am. J. Med. Genet. A"},{"key":"74650_CR3","doi-asserted-by":"publisher","first-page":"554","DOI":"10.1038\/gim.2014.144","volume":"17","author":"D Ramachandran","year":"2015","unstructured":"Ramachandran, D. et al. Contribution of copy-number variation to Down syndrome-associated atrioventricular septal defects. Genet. Med. 17, 554\u2013560 (2015).","journal-title":"Genet. Med."},{"key":"74650_CR4","doi-asserted-by":"publisher","first-page":"1961","DOI":"10.1534\/g3.115.019943","volume":"5","author":"D Ramachandran","year":"2015","unstructured":"Ramachandran, D. et al. Genome-wide association study of Down syndrome-associated atrioventricular septal defects. G3 5, 1961\u20131971 (2015).","journal-title":"G3"},{"key":"74650_CR5","doi-asserted-by":"publisher","first-page":"105","DOI":"10.1534\/g3.117.300366","volume":"8","author":"BL Rambo-Martin","year":"2018","unstructured":"Rambo-Martin, B. L. et al. Analysis of copy number variants on chromosome 21 in Down syndrome-associated congenital heart defects. G3 8, 105\u2013111 (2018).","journal-title":"G3"},{"key":"74650_CR6","doi-asserted-by":"publisher","first-page":"1410","DOI":"10.1101\/gr.147991.112","volume":"23","author":"MR Sailani","year":"2013","unstructured":"Sailani, M. R. et al. The complex SNP and CNV genetic architecture of the increased risk of congenital heart defects in Down syndrome. Genome Res. 23, 1410\u20131421 (2013).","journal-title":"Genome Res."},{"key":"74650_CR7","doi-asserted-by":"publisher","first-page":"646","DOI":"10.1016\/j.ajhg.2012.08.017","volume":"91","author":"C Ackerman","year":"2012","unstructured":"Ackerman, C. et al. An excess of deleterious variants in VEGF-A pathway genes in Down-syndrome-associated atrioventricular septal defects. Am. J. Hum. Genet. 91, 646\u2013659 (2012).","journal-title":"Am. J. Hum. Genet."},{"key":"74650_CR8","doi-asserted-by":"publisher","first-page":"574","DOI":"10.1016\/j.ajhg.2014.03.007","volume":"94","author":"S Al Turki","year":"2014","unstructured":"Al Turki, S. et al. Rare variants in NR2F2 cause congenital heart defects in humans. Am. J. Hum. Genet. 94, 574\u2013585 (2014).","journal-title":"Am. J. Hum. Genet."},{"key":"74650_CR9","first-page":"e135","volume":"32","author":"F-J Lin","year":"2012","unstructured":"Lin, F.-J. et al. Endocardial cushion morphogenesis and coronary vessel development require chicken ovalbumin upstream promoter-transcription factor II. Arterioscler. Thromb. Vasc. Biol. 32, e135\u2013e146 (2012).","journal-title":"Arterioscler. Thromb. Vasc. Biol."},{"key":"74650_CR10","doi-asserted-by":"publisher","first-page":"1037","DOI":"10.1101\/gad.13.8.1037","volume":"13","author":"FA Pereira","year":"1999","unstructured":"Pereira, F. A., Qiu, Y., Zhou, G., Tsai, M.-J. & Tsai, S. Y. The orphan nuclear receptor COUP-TFII is required for angiogenesis and heart development. Genes Dev. 13, 1037\u20131049 (1999).","journal-title":"Genes Dev."},{"key":"74650_CR11","doi-asserted-by":"publisher","first-page":"421","DOI":"10.1038\/nature13595","volume":"511","author":"Schizophrenia Working Group of the Psychiatric Genomics Consortium","year":"2014","unstructured":"Schizophrenia Working Group of the Psychiatric Genomics Consortium. Biological insights from 108 schizophrenia-associated genetic loci. Nature 511, 421\u2013427 (2014).","journal-title":"Nature"},{"key":"74650_CR12","doi-asserted-by":"publisher","first-page":"1219","DOI":"10.1038\/s41588-018-0183-z","volume":"50","author":"AV Khera","year":"2018","unstructured":"Khera, A. V. et al. Genome-wide polygenic scores for common diseases identify individuals with risk equivalent to monogenic mutations. Nat. Genet. 50, 1219\u20131224 (2018).","journal-title":"Nat. Genet."},{"key":"74650_CR13","doi-asserted-by":"publisher","first-page":"929","DOI":"10.1016\/j.ajhg.2010.05.002","volume":"86","author":"MC Wu","year":"2010","unstructured":"Wu, M. C. et al. Powerful SNP-set analysis for case-control genome-wide association studies. Am. J. Hum. Genet. 86, 929\u2013942 (2010).","journal-title":"Am. J. Hum. Genet."},{"key":"74650_CR14","doi-asserted-by":"publisher","first-page":"224","DOI":"10.1016\/j.ajhg.2012.06.007","volume":"91","author":"S Lee","year":"2012","unstructured":"Lee, S. et al. Optimal unified approach for rare-variant association testing with application to small-sample case-control whole-exome sequencing studies. Am. J. Hum. Genet. 91, 224\u2013237 (2012).","journal-title":"Am. J. Hum. Genet."},{"key":"74650_CR15","doi-asserted-by":"publisher","first-page":"841","DOI":"10.1016\/j.ajhg.2013.04.015","volume":"92","author":"I Ionita-Laza","year":"2013","unstructured":"Ionita-Laza, I., Lee, S., Makarov, V., Buxbaum, J. D. & Lin, X. Sequence kernel association tests for the combined effect of rare and common variants. Am. J. Hum. Genet. 92, 841\u2013853 (2013).","journal-title":"Am. J. Hum. Genet."},{"key":"74650_CR16","doi-asserted-by":"publisher","first-page":"e0191319","DOI":"10.1371\/journal.pone.0191319","volume":"13","author":"TT Hoang","year":"2018","unstructured":"Hoang, T. T. et al. The congenital heart disease genetic network study: cohort description. PLoS ONE 13, e0191319 (2018).","journal-title":"PLoS ONE"},{"key":"74650_CR17","doi-asserted-by":"crossref","unstructured":"Pediatric Cardiac Genomics Consortium et al. The Congenital Heart Disease Genetic Network Study: rationale, design, and early results. Circ. Res.112, 698\u2013706 (2013).","DOI":"10.1161\/CIRCRESAHA.111.300297"},{"key":"74650_CR18","doi-asserted-by":"publisher","first-page":"E1923","DOI":"10.1073\/pnas.1618065114","volume":"114","author":"HR Johnston","year":"2017","unstructured":"Johnston, H. R. et al. PEMapper and PECaller provide a simplified approach to whole-genome sequencing. Proc. Natl. Acad. Sci. U. S. A. 114, E1923\u2013E1932 (2017).","journal-title":"Proc. Natl. Acad. Sci. U. S. A."},{"key":"74650_CR19","doi-asserted-by":"publisher","first-page":"14","DOI":"10.1186\/s13059-018-1387-3","volume":"19","author":"AV Kotlar","year":"2018","unstructured":"Kotlar, A. V., Trevino, C. E., Zwick, M. E., Cutler, D. J. & Wingo, T. S. Bystro: rapid online variant annotation and natural-language filtering at whole-genome scale. Genome Biol. 19, 14 (2018).","journal-title":"Genome Biol."},{"key":"74650_CR20","first-page":"1358","volume":"38","author":"BS Weir","year":"1984","unstructured":"Weir, B. S. & Cockerham, C. C. Estimating F-statistics for the analysis of population structure. Evolution 38, 1358\u20131370 (1984).","journal-title":"Evolution"},{"key":"74650_CR21","doi-asserted-by":"publisher","first-page":"7","DOI":"10.1186\/s13742-015-0047-8","volume":"4","author":"CC Chang","year":"2015","unstructured":"Chang, C. C. et al. Second-generation PLINK: rising to the challenge of larger and richer datasets. GigaScience 4, 7 (2015).","journal-title":"GigaScience"},{"key":"74650_CR22","unstructured":"Purcell, S. M. & Chang, C. C. PLINK [v1.9b6.6]. www.cog-genomics.org\/plink\/1.9\/."},{"key":"74650_CR23","unstructured":"R Core Team. R: a language and environment for statistical computing. https:\/\/www.R-project.org\/ (R Foundation for Statistical Computing, 2017)."},{"key":"74650_CR24","doi-asserted-by":"publisher","first-page":"1284","DOI":"10.1038\/ng.3656","volume":"48","author":"S Das","year":"2016","unstructured":"Das, S. et al. Next-generation genotype imputation service and methods. Nat. Genet. 48, 1284\u20131287 (2016).","journal-title":"Nat. Genet."},{"key":"74650_CR25","doi-asserted-by":"publisher","first-page":"1279","DOI":"10.1038\/ng.3643","volume":"48","author":"S McCarthy","year":"2016","unstructured":"McCarthy, S. et al. A reference panel of 64,976 haplotypes for genotype imputation. Nat. Genet. 48, 1279\u20131283 (2016).","journal-title":"Nat. Genet."},{"key":"74650_CR26","doi-asserted-by":"publisher","first-page":"7","DOI":"10.1186\/2046-2530-2-7","volume":"2","author":"TJ van Dam","year":"2013","unstructured":"van Dam, T. J., Wheway, G., Slaats, G. G., Huynen, M. A. & Giles, R. H. The SYSCILIA gold standard (SCGSv1) of known ciliary components and its applications within a systems biology consortium. Cilia 2, 7 (2013).","journal-title":"Cilia"},{"key":"74650_CR27","doi-asserted-by":"crossref","DOI":"10.1093\/oso\/9780198503279.001.0001","volume-title":"Post-Genome Informatics","author":"M Kanehisa","year":"2000","unstructured":"Kanehisa, M. Post-Genome Informatics (Oxford University Press, Oxford, 2000)."},{"key":"74650_CR28","doi-asserted-by":"publisher","first-page":"1299","DOI":"10.1038\/nature04226","volume":"437","author":"International HapMap Consortium","year":"2005","unstructured":"International HapMap Consortium. A haplotype map of the human genome. Nature 437, 1299\u20131320 (2005).","journal-title":"Nature"},{"key":"74650_CR29","doi-asserted-by":"publisher","first-page":"822","DOI":"10.1038\/ng.2637","volume":"45","author":"HJ Cordell","year":"2013","unstructured":"Cordell, H. J. et al. Genome-wide association study of multiple congenital heart disease phenotypes identifies a susceptibility locus for atrial septal defect at chromosome 4p16. Nat. Genet. 45, 822\u2013824 (2013).","journal-title":"Nat. Genet."},{"key":"74650_CR30","doi-asserted-by":"publisher","first-page":"1473","DOI":"10.1093\/hmg\/dds552","volume":"22","author":"HJ Cordell","year":"2013","unstructured":"Cordell, H. J. et al. Genome-wide association study identifies loci on 12q24 and 13q32 associated with tetralogy of Fallot. Hum. Mol. Genet. 22, 1473\u20131481 (2013).","journal-title":"Hum. Mol. Genet."},{"key":"74650_CR31","doi-asserted-by":"publisher","first-page":"e001449","DOI":"10.1161\/CIRCGENETICS.116.001449","volume":"10","author":"AJ Agopian","year":"2017","unstructured":"Agopian, A. J. et al. Genome-wide association studies and meta-analyses for congenital heart defects. Circ. Cardiovasc. Genet. 10, e001449 (2017).","journal-title":"Circ. Cardiovasc. Genet."},{"key":"74650_CR32","doi-asserted-by":"publisher","first-page":"288","DOI":"10.1186\/1471-2105-11-288","volume":"11","author":"R M\u00e4gi","year":"2010","unstructured":"M\u00e4gi, R. & Morris, A. P. GWAMA: software for genome-wide association meta-analysis. BMC Bioinform. 11, 288 (2010).","journal-title":"BMC Bioinform."},{"key":"74650_CR33","doi-asserted-by":"publisher","DOI":"10.1093\/gigascience\/giz082","author":"SW Choi","year":"2019","unstructured":"Choi, S. W. & O\u2019Reilly, P. F. PRSice-2: Polygenic Risk Score software for biobank-scale data. GigaScience https:\/\/doi.org\/10.1093\/gigascience\/giz082 (2019).","journal-title":"GigaScience"},{"key":"74650_CR34","doi-asserted-by":"publisher","first-page":"1158","DOI":"10.1086\/522036","volume":"81","author":"KN Conneely","year":"2007","unstructured":"Conneely, K. N. & Boehnke, M. So many correlated tests, so little time! Rapid adjustment of P values for multiple correlated tests. Am. J. Hum. Genet. 81, 1158\u20131168 (2007).","journal-title":"Am. J. Hum. Genet."},{"key":"74650_CR35","doi-asserted-by":"publisher","first-page":"45","DOI":"10.1016\/j.devcel.2013.06.007","volume":"26","author":"JD Wythe","year":"2013","unstructured":"Wythe, J. D. et al. ETS factors regulate Vegf-dependent arterial specification. Dev. Cell 26, 45\u201358 (2013).","journal-title":"Dev. Cell"},{"key":"74650_CR36","doi-asserted-by":"publisher","first-page":"910","DOI":"10.1161\/01.RES.0000124300.76171.C9","volume":"94","author":"M Noseda","year":"2004","unstructured":"Noseda, M. et al. Notch activation results in phenotypic and functional changes consistent with endothelial-to-mesenchymal transformation. Circ. Res. 94, 910\u2013917 (2004).","journal-title":"Circ. Res."},{"key":"74650_CR37","doi-asserted-by":"publisher","DOI":"10.1155\/2010\/603159","author":"M Torrado","year":"2010","unstructured":"Torrado, M., Iglesias, R., Nespereira, B. & Mikhailov, A. T. Identification of candidate genes potentially relevant to chamber-specific remodeling in postnatal ventricular myocardium. J. Biomed. Biotechnol. https:\/\/doi.org\/10.1155\/2010\/603159 (2010).","journal-title":"J. Biomed. Biotechnol."},{"key":"74650_CR38","first-page":"3011","volume":"25","author":"O Burnicka-Turek","year":"2016","unstructured":"Burnicka-Turek, O. et al. Cilia gene mutations cause atrioventricular septal defects by multiple mechanisms. Hum. Mol. Genet. 25, 3011\u20133028 (2016).","journal-title":"Hum. Mol. Genet."},{"key":"74650_CR39","doi-asserted-by":"publisher","first-page":"a028266","DOI":"10.1101\/cshperspect.a028266","volume":"9","author":"NT Klena","year":"2017","unstructured":"Klena, N. T., Gibbs, B. C. & Lo, C. W. Cilia and ciliopathies in congenital heart disease. Cold Spring Harb. Perspect. Biol. 9, a028266 (2017).","journal-title":"Cold Spring Harb. Perspect. Biol."},{"key":"74650_CR40","doi-asserted-by":"publisher","first-page":"e41616","DOI":"10.1371\/journal.pone.0041616","volume":"7","author":"C Ripoll","year":"2012","unstructured":"Ripoll, C. et al. Molecular signatures of cardiac defects in Down syndrome lymphoblastoid cell lines suggest altered ciliome and hedgehog pathways. PLoS ONE 7, e41616 (2012).","journal-title":"PLoS ONE"},{"key":"74650_CR41","doi-asserted-by":"publisher","first-page":"1676","DOI":"10.1007\/s00246-018-1951-3","volume":"39","author":"KM Alharbi","year":"2018","unstructured":"Alharbi, K. M. et al. Targeted next-generation sequencing of 406 genes identified genetic defects underlying congenital heart disease in Down syndrome patients. Pediatr. Cardiol. 39, 1676\u20131680 (2018).","journal-title":"Pediatr. Cardiol."},{"key":"74650_CR42","doi-asserted-by":"publisher","first-page":"214","DOI":"10.1002\/gepi.21614","volume":"36","author":"SH Lee","year":"2012","unstructured":"Lee, S. H., Goddard, M. E., Wray, N. R. & Visscher, P. M. A better coefficient of determination for genetic profile analysis. Genet. Epidemiol. 36, 214\u2013224 (2012).","journal-title":"Genet. Epidemiol."},{"key":"74650_CR43","doi-asserted-by":"publisher","DOI":"10.1371\/annotation\/b91ba224","author":"F Dudbridge","year":"2013","unstructured":"Dudbridge, F. Correction: Power and predictive accuracy of polygenic risk scores. PLOS Genet. https:\/\/doi.org\/10.1371\/annotation\/b91ba224 (2013).","journal-title":"PLOS Genet."}],"updated-by":[{"DOI":"10.1038\/s41598-021-94021-x","type":"correction","label":"Correction","source":"publisher","updated":{"date-parts":[[2021,7,20]],"date-time":"2021-07-20T00:00:00Z","timestamp":1626739200000}}],"container-title":["Scientific Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.nature.com\/articles\/s41598-020-74650-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/www.nature.com\/articles\/s41598-020-74650-4","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/www.nature.com\/articles\/s41598-020-74650-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,8,16]],"date-time":"2024-08-16T07:52:42Z","timestamp":1723794762000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.nature.com\/articles\/s41598-020-74650-4"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,10,22]]},"references-count":43,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2020,12]]}},"alternative-id":["74650"],"URL":"https:\/\/doi.org\/10.1038\/s41598-020-74650-4","relation":{"correction":[{"id-type":"doi","id":"10.1038\/s41598-021-94021-x","asserted-by":"object"}]},"ISSN":["2045-2322"],"issn-type":[{"value":"2045-2322","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,10,22]]},"assertion":[{"value":"13 August 2020","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"5 October 2020","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"22 October 2020","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"20 July 2021","order":4,"name":"change_date","label":"Change Date","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"Correction","order":5,"name":"change_type","label":"Change Type","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"A Correction to this paper has been published:","order":6,"name":"change_details","label":"Change Details","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"https:\/\/doi.org\/10.1038\/s41598-021-94021-x","URL":"https:\/\/doi.org\/10.1038\/s41598-021-94021-x","order":7,"name":"change_details","label":"Change Details","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"The authors declare no competing interests.","order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing interests"}}],"article-number":"18051"}}