{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,10]],"date-time":"2026-02-10T19:53:03Z","timestamp":1770753183356,"version":"3.50.0"},"reference-count":0,"publisher":"Portland Press Ltd.","issue":"1","content-domain":{"domain":["portlandpress.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[1986,7,1]]},"abstract":"<jats:p>1. The neuronal ceroid-lipofuscinoses is a group of diseases characterized by a widespread accumulation in the body of pigments believed to be end-products of lipid-peroxidation damaged organelles. It was recently shown that cerebrospinal fluid from patients with infantile and juvenile neuronal ceroid-lipofuscinosis were less protective against superoxide radical-induced hydroxyl radical formation compared with controls [3].<\/jats:p>\n               <jats:p>2. The content of superoxide dismutase isoenzymes in cerebrospinal fluid and in plasma from patients with different forms of neuronal ceroid-lipofuscinosis was analysed. No significant difference from controls could be demonstrated in samples from patients with juvenile neuronal ceroid-lipofuscinosis. The few samples from patients with infantile and late infantile neuronal ceroid-lipofuscinosis analysed all fell within the range defined by the controls.<\/jats:p>","DOI":"10.1042\/cs0710057","type":"journal-article","created":{"date-parts":[[2015,8,7]],"date-time":"2015-08-07T11:07:31Z","timestamp":1438945651000},"page":"57-60","update-policy":"https:\/\/doi.org\/10.1042\/crossmark_policy","source":"Crossref","is-referenced-by-count":9,"title":["Superoxide dismutase isoenzymes in cerebrospinal fluid and plasma from patients with neuronal ceroid-lipofuscinoses"],"prefix":"10.1042","volume":"71","author":[{"given":"Stefan L.","family":"Marklund","sequence":"first","affiliation":[{"name":"Department of Clinical Chemistry, Ume\u00e5 University Hospital, Ume\u00e5, Sweden"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hannu","family":"Heiskala","sequence":"additional","affiliation":[{"name":"Children's Hospital, University of Helsinki, Helsinki, Finland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tuomas","family":"Westermarck","sequence":"additional","affiliation":[{"name":"Helsinki Central Institution for the Mentally Retarded, Kirkonummi, Finland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pirkko","family":"Santavuori","sequence":"additional","affiliation":[{"name":"Children's Hospital, University of Helsinki, Helsinki, Finland"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"288","container-title":["Clinical Science"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/portlandpress.com\/clinsci\/article-pdf\/71\/1\/57\/457108\/cs0710057.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/portlandpress.com\/clinsci\/article-pdf\/71\/1\/57\/457108\/cs0710057.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,12,2]],"date-time":"2021-12-02T20:43:08Z","timestamp":1638477788000},"score":1,"resource":{"primary":{"URL":"https:\/\/portlandpress.com\/clinsci\/article\/71\/1\/57\/74040\/Superoxide-dismutase-isoenzymes-in-cerebrospinal"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1986,7,1]]},"references-count":0,"journal-issue":{"issue":"1","published-print":{"date-parts":[[1986,7,1]]}},"URL":"https:\/\/doi.org\/10.1042\/cs0710057","relation":{},"ISSN":["0143-5221","1470-8736"],"issn-type":[{"value":"0143-5221","type":"print"},{"value":"1470-8736","type":"electronic"}],"subject":[],"published":{"date-parts":[[1986,7,1]]}}}