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There have been proposed strategies to aid in monitoring anticoagulation in factor XII deficient patients, however, documentation of successful monitoring during CPB is infrequent. With the use of the Hemochron Signature Elite and ACT\u00a0+\u00a0cartridges, CPB in a factor XII deficient 8-month-old was completed with predictable and reliable anticoagulation monitoring. This case report explores the current suggestions for factor XII deficiency management with CPB.<\/jats:p>","DOI":"10.1051\/ject\/2024021","type":"journal-article","created":{"date-parts":[[2024,7,25]],"date-time":"2024-07-25T19:07:45Z","timestamp":1721934465000},"page":"125-127","source":"Crossref","is-referenced-by-count":1,"title":["Cardiopulmonary bypass in a pediatric patient with factor XII deficiency"],"prefix":"10.1051","volume":"56","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-7520-5110","authenticated-orcid":false,"given":"Julie M.","family":"Fenske","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Julie","family":"Tinius Juliani","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Cynthia","family":"Herrington","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"250","published-online":{"date-parts":[[2024,9,20]]},"reference":[{"issue":"4","key":"R1","doi-asserted-by":"crossref","first-page":"39","DOI":"10.4236\/ojbd.2015.54006","volume":"5","author":"Azaad","year":"2015","journal-title":"Open J Blood Dis"},{"issue":"8","key":"R2","doi-asserted-by":"crossref","first-page":"1670","DOI":"10.1111\/j.1538-7836.2010.03893.x","volume":"8","author":"Caen","year":"2010","journal-title":"J Thromb Hemost"},{"issue":"2","key":"R3","doi-asserted-by":"crossref","first-page":"625","DOI":"10.1016\/j.athoracsur.2009.07.042","volume":"89","author":"Conaglen","year":"2010","journal-title":"Ann Thorac Surg"},{"issue":"9","key":"R4","first-page":"3006","volume":"118","author":"Schmaier","year":"2008","journal-title":"J Clin Invest"},{"issue":"8","key":"R5","doi-asserted-by":"crossref","first-page":"1998","DOI":"10.1182\/blood.V80.8.1998.1998","volume":"80","author":"Andrew","year":"1992","journal-title":"Blood"},{"issue":"1","key":"R6","doi-asserted-by":"crossref","first-page":"165","DOI":"10.1182\/blood.V70.1.165.165","volume":"70","author":"Andrew","year":"1987","journal-title":"Blood"},{"issue":"7","key":"R7","doi-asserted-by":"crossref","first-page":"741","DOI":"10.1055\/s-0036-1593415","volume":"42","author":"Hanmod","year":"2016","journal-title":"Semin Thromb Hemost"},{"key":"R8","doi-asserted-by":"crossref","first-page":"39","DOI":"10.11604\/pamj.2019.33.39.18117","volume":"33","author":"Chaudhry","year":"2019","journal-title":"Pan Afr Med J"},{"issue":"1","key":"R9","doi-asserted-by":"crossref","first-page":"068","DOI":"10.1055\/s-0038-1642386","volume":"71","author":"Halbmayer","year":"1994","journal-title":"Throm Haemost"},{"key":"R10","doi-asserted-by":"crossref","first-page":"990","DOI":"10.1097\/00000542-199710000-00038","volume":"87","author":"Gerhardt","year":"1997","journal-title":"Anesthesiology"},{"issue":"7","key":"R11","doi-asserted-by":"crossref","first-page":"2031","DOI":"10.1053\/j.jvca.2021.05.021","volume":"36","author":"Erkinaro","year":"2022","journal-title":"J Cardiothorac Vasc Anesth"},{"issue":"1","key":"R12","doi-asserted-by":"crossref","first-page":"4965","DOI":"10.1182\/blood-2019-131614","volume":"134","author":"Regling","year":"2019","journal-title":"Blood"},{"issue":"4","key":"R13","first-page":"549","volume":"24","author":"De Vries","year":"2017","journal-title":"Interact CardioVasc Thorac Surg"},{"issue":"3","key":"R14","doi-asserted-by":"crossref","first-page":"254","DOI":"10.1051\/ject\/201446254","volume":"46","author":"Uppal","year":"2014","journal-title":"J Extra Corpor Technol"},{"issue":"3","key":"R15","doi-asserted-by":"crossref","first-page":"251","DOI":"10.1051\/ject\/201446251","volume":"46","author":"Cronbaugh","year":"2014","journal-title":"J Extra Corpor Technol"},{"issue":"4","key":"R16","doi-asserted-by":"crossref","first-page":"267","DOI":"10.5603\/AHP.a2022.0034","volume":"53","author":"Stelmach","year":"2022","journal-title":"Acta Haematol Polon"}],"container-title":["The Journal of ExtraCorporeal Technology"],"original-title":[],"link":[{"URL":"https:\/\/ject.edpsciences.org\/10.1051\/ject\/2024021\/pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,9,20]],"date-time":"2024-09-20T11:47:25Z","timestamp":1726832845000},"score":1,"resource":{"primary":{"URL":"https:\/\/ject.edpsciences.org\/10.1051\/ject\/2024021"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,9]]},"references-count":16,"journal-issue":{"issue":"3"},"alternative-id":["ject240018"],"URL":"https:\/\/doi.org\/10.1051\/ject\/2024021","relation":{},"ISSN":["0022-1058","2969-8960"],"issn-type":[{"value":"0022-1058","type":"print"},{"value":"2969-8960","type":"electronic"}],"subject":[],"published":{"date-parts":[[2024,9]]}}}