{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,11,19]],"date-time":"2024-11-19T05:19:44Z","timestamp":1731993584678,"version":"3.28.0"},"reference-count":20,"publisher":"EDP Sciences","license":[{"start":{"date-parts":[[2024,11,18]],"date-time":"2024-11-18T00:00:00Z","timestamp":1731888000000},"content-version":"vor","delay-in-days":17,"URL":"https:\/\/www.edpsciences.org\/en\/authors\/copyright-and-licensing"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Med Sci (Paris)"],"published-print":{"date-parts":[[2024,11]]},"abstract":"<jats:p>Les arthrogryposes multiples cong\u00e9nitales (AMC) regroupent l\u2019ensemble des pathologies avec des limitations articulaires \u00e0 au moins deux niveaux articulaires distincts, \u00e0 la naissance. Les limitations articulaires ne sont pas \u00e9volutives, mais les cons\u00e9quences fonctionnelles ont un impact tout au long de la vie des patients. Dans cet article, nous montrerons les r\u00e9sultats de notre \u00e9tude qui vise \u00e0 \u00e9valuer la corr\u00e9lation entre l\u2019infiltration graisseuse musculaire en IRM et les d\u00e9ficiences et limitations d\u2019activit\u00e9 chez des enfants pr\u00e9sentant une AMC. Notre \u00e9tude est une des premi\u00e8res \u00e0 \u00e9tablir le lien entre l\u2019imagerie musculaire et les aspects fonctionnels de l\u2019AMC, en population p\u00e9diatrique.<\/jats:p>","DOI":"10.1051\/medsci\/2024131","type":"journal-article","created":{"date-parts":[[2024,11,18]],"date-time":"2024-11-18T08:51:13Z","timestamp":1731919873000},"page":"26-29","source":"Crossref","is-referenced-by-count":0,"special_numbering":"Hors s\u00e9rie n\u00b0 1","title":["Arthrogryposes multiples cong\u00e9nitales \u00e0 l\u2019\u00e2ge p\u00e9diatrique"],"prefix":"10.1051","volume":"40","author":[{"given":"Alicia","family":"Milot","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mariya","family":"Raikova","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Claire","family":"Huzar","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"V\u00e9ronique","family":"Thellier","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nicolas","family":"Hergibo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marjolaine","family":"Gauthier","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gipsy","family":"Billy-Lopez","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Chantal","family":"Durand","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fr\u00e9d\u00e9rique","family":"Nugues","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"V\u00e9ronique","family":"Bourg","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Klaus","family":"Dieterich","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"250","published-online":{"date-parts":[[2024,11,18]]},"reference":[{"issue":"3","key":"R1","doi-asserted-by":"crossref","first-page":"288","DOI":"10.1002\/ajmg.c.31721","volume":"181","author":"Dahan-Oliel","year":"2019","journal-title":"Am J Med Genet"},{"issue":"2","key":"R2","doi-asserted-by":"crossref","first-page":"347","DOI":"10.1016\/j.ejogrb.2011.09.027","volume":"159","author":"Hoff","year":"2011","journal-title":"Eur J Obstet Gynecol Reprod Biol"},{"key":"R3","doi-asserted-by":"crossref","unstructured":"Le Tanno P, Latypova X, Rendu J, et al. 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