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Les auteurs proposent, au vu de l\u2019ensemble des cas qu\u2019ils suivent dans leur service et de la bibliographie actuelle sur chaque pathologie, de classer ces syndromes en quatre cat\u00e9gories physiopathologiques afin de conseiller pour chaque classe une prise en charge adapt\u00e9e. En connaissant l\u2019\u00e9tiopathog\u00e9nie d\u2019une affection, on l\u2019appr\u00e9hende et la traite diff\u00e9remment. Plus de cinquante cas ont \u00e9t\u00e9 r\u00e9pertori\u00e9s, mais il a \u00e9t\u00e9 d\u00e9cid\u00e9 de ne pr\u00e9senter que les pathologies les plus typiques sur le plan physiopathologique. Cette classification comprend les anomalies organiques d\u2019une ou de plusieurs matrices fonctionnelles, les anomalies localis\u00e9es des structures anatomiques, les anomalies g\u00e9n\u00e9ralis\u00e9es du tissu m\u00e9senchymateux, les syndromes mixtes.<\/jats:p>","DOI":"10.1051\/orthodfr\/2011121","type":"journal-article","created":{"date-parts":[[2011,5,31]],"date-time":"2011-05-31T11:53:06Z","timestamp":1306842786000},"page":"223-232","source":"Crossref","is-referenced-by-count":4,"title":["Proposition de classification des syndromes malformatifs cranio-maxillo-faciaux"],"prefix":"10.1684","volume":"82","author":[{"given":"Antoine","family":"Delforge","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gwena\u00ebl","family":"Raoul","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Axel","family":"Wiss","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jean-Baptiste","family":"Kerbrat","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jo\u00ebl","family":"Ferri","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"18929","published-online":{"date-parts":[[2011,6,1]]},"reference":[{"key":"R1","doi-asserted-by":"crossref","first-page":"629","DOI":"10.1016\/j.ajodo.2005.01.032","volume":"130","author":"Ben-Bassat","year":"2006","journal-title":"Am J Orthod Dentofacial Orthop"},{"key":"R2","doi-asserted-by":"crossref","first-page":"563","DOI":"10.1097\/01.scs.0000168765.56109.54","volume":"16","author":"Cascone","year":"2005","journal-title":"J Craniofac Surg"},{"key":"R3","doi-asserted-by":"crossref","first-page":"241","DOI":"10.1051\/orthodfr\/200071241","volume":"71","author":"Ferri","year":"2000","journal-title":"\u00c9tude pr\u00e9liminaire. 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