{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,4]],"date-time":"2025-10-04T00:08:52Z","timestamp":1759536532872,"version":"build-2065373602"},"reference-count":12,"publisher":"Elsevier BV","issue":"6","license":[{"start":{"date-parts":[[2010,6,1]],"date-time":"2010-06-01T00:00:00Z","timestamp":1275350400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2010,6,1]],"date-time":"2010-06-01T00:00:00Z","timestamp":1275350400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["ajkd.org","clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["American Journal of Kidney Diseases"],"published-print":{"date-parts":[[2010,6]]},"DOI":"10.1053\/j.ajkd.2009.11.028","type":"journal-article","created":{"date-parts":[[2010,4,19]],"date-time":"2010-04-19T04:49:15Z","timestamp":1271652555000},"page":"1130-1135","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":14,"title":["An Unusual Case of Metabolic Alkalosis: A Window Into the Pathophysiology and Diagnosis of This Common Acid-Base Disturbance"],"prefix":"10.1053","volume":"55","author":[{"given":"F. John","family":"Gennari","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sarah","family":"Hussain-Khan","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alan","family":"Segal","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"issue":"3","key":"10.1053\/j.ajkd.2009.11.028_bib1","doi-asserted-by":"crossref","first-page":"407","DOI":"10.1016\/0092-8674(94)90250-X","article-title":"Liddle's syndrome: heritable human hypertension caused by mutations in the beta subunit of the epithelial sodium channel","volume":"79","author":"Shimkets","year":"1994","journal-title":"Cell"},{"issue":"8","key":"10.1053\/j.ajkd.2009.11.028_bib2","doi-asserted-by":"crossref","first-page":"2805","DOI":"10.1073\/pnas.0511184103","article-title":"Liddle's syndrome mutations increase Na+ transport through dual effects on epithelial Na+ channel surface expression and proteolytic cleavage","volume":"103","author":"Knight","year":"2006","journal-title":"Proc Natl Acad Sci U S A"},{"key":"10.1053\/j.ajkd.2009.11.028_bib3","series-title":"Comprehensive Clinical Nephrology","first-page":"159","article-title":"Metabolic alkalosis","author":"Gennari","year":"2007"},{"issue":"6","key":"10.1053\/j.ajkd.2009.11.028_bib4","doi-asserted-by":"crossref","first-page":"1356","DOI":"10.1038\/ki.1987.150","article-title":"Dietary NaCl determines severity of potassium depletion-induced metabolic alkalosis","volume":"31","author":"Hernandez","year":"1987","journal-title":"Kidney Int"},{"issue":"10","key":"10.1053\/j.ajkd.2009.11.028_bib5","doi-asserted-by":"crossref","first-page":"1558","DOI":"10.1172\/JCI105647","article-title":"Aldosterone in metabolic alkalosis","volume":"46","author":"Kassirer","year":"1967","journal-title":"J Clin Invest"},{"issue":"1","key":"10.1053\/j.ajkd.2009.11.028_bib6","doi-asserted-by":"crossref","first-page":"31","DOI":"10.7326\/0003-4819-73-1-31","article-title":"Saline-resistant metabolic alkalosis or \u201cchloride-wasting nephropathy.\u201d Report of four patients with severe potassium depletion","volume":"73","author":"Garella","year":"1970","journal-title":"Ann Intern Med"},{"issue":"6357","key":"10.1053\/j.ajkd.2009.11.028_bib7","doi-asserted-by":"crossref","first-page":"262","DOI":"10.1038\/355262a0","article-title":"A chimaeric 11 beta-hydroxylase\/aldosterone synthase gene causes glucocorticoid-remediable aldosteronism and human hypertension","volume":"355","author":"Lifton","year":"1992","journal-title":"Nature"},{"issue":"6","key":"10.1053\/j.ajkd.2009.11.028_bib8","doi-asserted-by":"crossref","first-page":"607","DOI":"10.1007\/s00467-002-1049-1","article-title":"The distinction between Liddle syndrome and apparent mineralocorticoid excess","volume":"18","author":"Bianchetti","year":"2003","journal-title":"Pediatr Nephrol"},{"issue":"4","key":"10.1053\/j.ajkd.2009.11.028_bib9","first-page":"1071","article-title":"Liddle's syndrome: prospective genetic screening and suppressed aldosterone secretion in an extended kindred","volume":"82","author":"Findling","year":"1997","journal-title":"J Clin Endocrinol Metab"},{"issue":"11","key":"10.1053\/j.ajkd.2009.11.028_bib10","doi-asserted-by":"crossref","first-page":"3176","DOI":"10.1681\/ASN.2006060570","article-title":"Apparent mineralocorticoid excess: report of six new cases and extensive personal experience","volume":"17","author":"Morineau","year":"2006","journal-title":"J Am Soc Nephrol"},{"issue":"1-3","key":"10.1053\/j.ajkd.2009.11.028_bib11","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/0960-0760(93)90114-C","article-title":"Congenital and acquired syndromes of apparent mineralocorticoid excess","volume":"45","author":"Edwards","year":"1993","journal-title":"J Steroid Biochem Mol Biol"},{"issue":"3","key":"10.1053\/j.ajkd.2009.11.028_bib12","doi-asserted-by":"crossref","first-page":"178","DOI":"10.1056\/NEJM199401203300305","article-title":"Brief report: Liddle's syndrome revisited\u2014a disorder of sodium reabsorption in the distal tubule","volume":"330","author":"Botero-Velez","year":"1994","journal-title":"N Engl J Med"}],"container-title":["American Journal of Kidney Diseases"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0272638610004750?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0272638610004750?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,3]],"date-time":"2025-10-03T01:54:32Z","timestamp":1759456472000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0272638610004750"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,6]]},"references-count":12,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2010,6]]}},"alternative-id":["S0272638610004750"],"URL":"https:\/\/doi.org\/10.1053\/j.ajkd.2009.11.028","relation":{},"ISSN":["0272-6386"],"issn-type":[{"type":"print","value":"0272-6386"}],"subject":[],"published":{"date-parts":[[2010,6]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"An Unusual Case of Metabolic Alkalosis: A Window Into the Pathophysiology and Diagnosis of This Common Acid-Base Disturbance","name":"articletitle","label":"Article Title"},{"value":"American Journal of Kidney Diseases","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1053\/j.ajkd.2009.11.028","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2010 National Kidney Foundation, Inc. Published by Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}