{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,3]],"date-time":"2026-07-03T09:54:15Z","timestamp":1783072455057,"version":"3.54.6"},"reference-count":154,"publisher":"Georg Thieme Verlag KG","issue":"05","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Klin Padiatr"],"published-print":{"date-parts":[[2020,9]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Die Leitlinie wurde im Konsens aller relevanten deutschen Fachgesellschaften zusammen mit Patientenvertretern erstellt. Standard der pr\u00e4- und postnatalen Bildgebung von Nierenzysten ist die Sonografie, die auch im Abdomen und inneren Genitale extrarenale Manifestationen ausschlie\u00dfen soll. Die MRT hat einzelne Indikationen. Bei Verdacht auf zystische Nierenerkrankungen ist eine kindernephrologische Vorstellung indiziert. Die pr\u00e4natale Betreuung muss auf sehr unterschiedliche Schweregrade zugeschnitten werden. Bei renalem Oligohydramnion wird eine Entbindung in einem Perinatalzentrum der h\u00f6chsten Stufe empfohlen. Neugeborenen sollte eine Nierenersatztherapie nicht allein aufgrund des Alters vorenthalten werden. Bei unilateraler multizystischer Nierendysplasie ist keine funktionelle Bildgebung oder Nephrektomie notwendig, aber (wie auch bei uni- oder bilateraler Nierenhypo-\/dysplasie mit Zysten) eine langfristige nephrologische \u00dcberwachung. Bei der ARPKD (autosomal rezessive polyzystische Nierenerkrankung), Nephronophthise, Bardet-Biedl-Syndrom und HNF1B-Mutationen m\u00fcssen extrarenale Manifestationen beachtet werden; eine genetische Testung ist hier sinnvoll. Kinder mit tuber\u00f6ser Sklerose, Tumorpr\u00e4dispositionen (z.\u2009B. von Hippel Lindau Syndrom) oder hohem Risiko f\u00fcr erworbene Nierenzysten sollten regelm\u00e4\u00dfige Nierensonografien erhalten. Auch asymptomatische Kinder von Eltern mit ADPKD (aut. dominanter polyzystischer Nierenerkrankung) sollten regelm\u00e4\u00dfig auf Hypertonie und Proteinurie untersucht werden. Eine pr\u00e4symptomatische sonografische oder genetische Diagnostik dieser Minderj\u00e4hrigen sollte nur nach ausf\u00fchrlicher Aufkl\u00e4rung erwogen werden. Einfache (isolierte) Zysten sind bei Kindern sehr selten und eine ADPKD eines Elternteils sollte ausgeschlossen sein. Komplexe Nierenzysten bed\u00fcrfen weiterer Abkl\u00e4rung.<\/jats:p>","DOI":"10.1055\/a-1179-0728","type":"journal-article","created":{"date-parts":[[2020,7,13]],"date-time":"2020-07-13T22:48:39Z","timestamp":1594680519000},"page":"228-248","source":"Crossref","is-referenced-by-count":11,"title":["Nierenzysten und zystische Nierenerkrankungen bei Kindern (AWMF S2k-Leitlinie)"],"prefix":"10.1055","volume":"232","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-2337-6724","authenticated-orcid":false,"given":"Charlotte","family":"Gimpel","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine IV, Medical Center \u2013 University of Freiburg, Freiburg"},{"name":"Faculty of Medicine, University of Freiburg, Freiburg im Breisgau"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carsten","family":"Bergmann","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine IV, Medical Center \u2013 University of Freiburg, Freiburg"},{"name":"Faculty of Medicine, University of Freiburg, Freiburg im Breisgau"},{"name":"Medizinische Genetik Mainz, Limbach Genetics, Mainz"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Florian","family":"Brinkert","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, University Medical Center Hamburg-Eppendorf, Hamburg"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Metin","family":"Cetiner","sequence":"additional","affiliation":[{"name":"Department of Pediatrics II, University Hospital Essen, Essen"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ulrich","family":"Gembruch","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Prenatal Medicine, University Hospital of Bonn, Bonn"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dieter","family":"Haffner","sequence":"additional","affiliation":[{"name":"Department of Pediatric Kidney, Liver and Metabolic Diseases, Hannover Medical School, Hannover"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Markus","family":"Kemper","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Asklepios Kliniken Hamburg GmbH, Asklepios Klinik Nord, Standort Heidberg, Hamburg"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jens","family":"K\u00f6nig","sequence":"additional","affiliation":[{"name":"Department of General Pediatrics, University Children's Hospital M\u00fcnster, M\u00fcnster"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Max","family":"Liebau","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, University Hospital Cologne, Cologne"},{"name":"Center for Molecular Medicine, University of Cologne, Cologne"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rolf Felix","family":"Maier","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, University Hospital of Giessen and Marburg, 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Main"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rainer","family":"Rossi","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Vivantes Klinikum Neuk\u00f6lln, Berlin"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Joachim","family":"Stegmann","sequence":"additional","affiliation":[{"name":"Department of Radiology, Catholic Children\u02bcs Hospital Wilhelmstift, Hamburg"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Udo","family":"Vester","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, HELIOS Hospital Duisburg, Duisburg"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Constantin von","family":"Kaisenberg","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynaecology, Center for Perinatal Medicine, Hannover Medical School, 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