{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,7]],"date-time":"2026-10-07T19:51:44Z","timestamp":1791402704899,"version":"4.3.3"},"reference-count":387,"publisher":"Georg Thieme Verlag KG","issue":"S 01","license":[{"start":{"date-parts":[[2021,4,30]],"date-time":"2021-04-30T00:00:00Z","timestamp":1619740800000},"content-version":"vor","delay-in-days":29,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Laryngorhinootologie"],"published-print":{"date-parts":[[2021,4]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Die Differenzialdiagnose von Erkrankungen des vestibul\u00e4ren Labyrinths stellt eine grosse Herausforderung dar, da sich hinter dem sehr h\u00e4ufigen Leitsymptom \u00abSchwindel\u00bb viele verschiedene und v. a. seltene Erkrankungen verbergen k\u00f6nnen. Der vorliegende Beitrag gibt einen \u00dcberblick \u00fcber die f\u00fcr den HNO-Arzt wichtigen seltenen Erkrankungen des vestibul\u00e4ren Labyrinths ausgehend von ihrer klinischen Pr\u00e4sentation als akutes (AVS), episodisches (EVS) oder chronisches vestibul\u00e4res Syndrom (CVS). Der Schwerpunkt liegt dabei auf den EVS, sortiert nach ihrer Dauer und dem Vorhandensein von Triggern (Sekunden, ohne Trigger: Vestibularisparoxysmie, Tumarkin-Krise; Sekunden, l\u00e4rm- und druckinduziert: Syndrome des \u00abdritten Fensters\u00bb; Sekunden bis Minuten, positionsabh\u00e4ngig: seltene Varianten und Differenzialdiagnosen des benignen paroxysmalen Lagerungsschwindels; Stunden bis Tage, spontan: intralabyrinth\u00e4re Schwannome, Tumoren des endolymphatischen Sacks, Autoimmunerkrankungen des Innenohres). Des Weiteren werden seltene Differenzialdiagnosen eines AVS (Neuritis vestibularis inf., Otolithenfunktionsst\u00f6rungen, vaskul\u00e4re Ursachen, akute bilaterale Vestibulopathie) und eines CVS (bilaterale Vestibulopathie) erl\u00e4utert. Dabei werden insbesondere die entscheidenden diagnostischen Massnahmen f\u00fcr die Identifikation der einzelnen Krankheitsbilder und die Warnzeichen f\u00fcr potentiell gef\u00e4hrliche Ursachen (z.\u2009B. Labyrinthinfarkt\/-blutung) dargelegt. Somit dient dieser Beitrag dem HNO-Arzt in Klinik und Praxis als eine Art \u00abVademecum\u00bb f\u00fcr die z\u00fcgige Identifikation und zeitnahe Therapie seltener Erkrankungen des Gleichgewichtsorgans.<\/jats:p>","DOI":"10.1055\/a-1349-7475","type":"journal-article","created":{"date-parts":[[2021,4,30]],"date-time":"2021-04-30T19:32:31Z","timestamp":1619811151000},"page":"S1-S40","source":"Crossref","is-referenced-by-count":5,"special_numbering":"S","title":["Seltene Erkrankungen des vestibul\u00e4ren Labyrinths: von Zebras, Cham\u00e4leons und W\u00f6lfen im Schafspelz"],"prefix":"10.1055","volume":"100","author":[{"given":"Julia","family":"Dlugaiczyk","sequence":"additional","affiliation":[{"name":"Klinik f\u00fcr Ohren-, Nasen-, Hals- und Gesichtschirurgie & Interdisziplin\u00e4res Zentrum f\u00fcr Schwindel und neurologische Sehst\u00f6rungen, Universit\u00e4tsspital Z\u00fcrich (USZ), Universit\u00e4t Z\u00fcrich (UZH), Z\u00fcrich, Schweiz"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"194","published-online":{"date-parts":[[2021,4,30]]},"reference":[{"key":"ref2","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1016\/B978-0-444-63437-5.00005-4","article-title":"The epidemiology of dizziness and vertigo","volume":"137","author":"H K Neuhauser","year":"2016","journal-title":"Handb Clin Neurol"},{"key":"ref3","doi-asserted-by":"crossref","first-page":"S90","DOI":"10.1007\/s00415-015-7973-3","article-title":"Vestibular paroxysmia: a treatable neurovascular cross-compression syndrome","volume":"263","author":"T Brandt","year":"2016","journal-title":"J Neurol"},{"key":"ref5","first-page":"304","article-title":"The B\u00e1r\u00e1ny Classification of vestibular disorders, its clinical implementation and future prospects","volume":"68","author":"A Bisdorff","year":"2020","journal-title":"HNO"},{"key":"ref7","doi-asserted-by":"crossref","first-page":"258","DOI":"10.3389\/fneur.2017.00258","article-title":"The Video Head Impulse Test","volume":"8","author":"G M Halmagyi","year":"2017","journal-title":"Front Neurol"},{"key":"ref8","doi-asserted-by":"crossref","first-page":"47","DOI":"10.1016\/j.cnp.2019.01.005","article-title":"Vestibular evoked myogenic potentials in practice: Methods, pitfalls and clinical applications","volume":"4","author":"S M Rosengren","year":"2019","journal-title":"Clin Neurophysiol Pract"},{"key":"ref9","doi-asserted-by":"crossref","first-page":"1539","DOI":"10.1016\/j.clinph.2019.04.719","article-title":"Why and when to refer patients for vestibular evoked myogenic potentials: A critical review","volume":"130","author":"E S Papathanasiou","year":"2019","journal-title":"Clin Neurophysiol"},{"key":"ref10","doi-asserted-by":"crossref","first-page":"324","DOI":"10.1007\/s00106-019-00767-2","article-title":"Evidence-based diagnostic use of VEMPs : From neurophysiological principles to clinical application. 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