{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,1]],"date-time":"2026-02-01T05:26:23Z","timestamp":1769923583480,"version":"3.49.0"},"reference-count":44,"publisher":"Georg Thieme Verlag KG","issue":"01","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Zentralbl Chir"],"published-print":{"date-parts":[[2022,2]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Kongenitale pulmonale Malformationen stellen eine heterogene Gruppe seltener\n                    Erkrankungen dar, die auf Fehlentwicklungen w\u00e4hrend der embryonalen und fetalen\n                    Wachstumsphase basieren. Zu ihnen geh\u00f6ren der Trachealbronchus, die bronchiale\n                    Atresie, die bronchogene Zyste, die Lungensequestration, das kongenitale lob\u00e4re\n                    Emphysem sowie die sogenannte Congenital pulmonary Airway Malformation. Eines\n                    der Leitsymptome dieser Malformationen ist die durch ihren verdr\u00e4ngenden Effekt\n                    bedingte postnatale respiratorische Insuffizienz, welche eine rasche operative\n                    Versorgung erfordert. Auch bei asymptomatischen Malformationen wird aufgrund des\n                    erh\u00f6hten Infektrisikos die Resektion empfohlen.<\/jats:p><jats:p>In der folgenden \u00dcbersicht wird auf die Ursachen, das klinische Bild und die\n                    therapeutischen Optionen dieser angeborenen Fehlbildungen der Lunge und des\n                    Bronchialsystems eingegangen.<\/jats:p>","DOI":"10.1055\/a-1669-9574","type":"journal-article","created":{"date-parts":[[2022,1,19]],"date-time":"2022-01-19T23:33:47Z","timestamp":1642635227000},"page":"90-97","source":"Crossref","is-referenced-by-count":1,"title":["Angeborene Fehlbildungen der Lunge \u2013 eine \u00dcbersicht"],"prefix":"10.1055","volume":"147","author":[{"given":"Birte","family":"Ohm","sequence":"additional","affiliation":[{"name":"Klinik f\u00fcr Thoraxchirurgie, Universit\u00e4tsklinikum Freiburg, Medizinische\n                    Fakult\u00e4t, Albert-Ludwigs-Universit\u00e4t Freiburg, Freiburg,\n                    Deutschland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Wolfgang","family":"Jungraithmayr","sequence":"additional","affiliation":[{"name":"Klinik f\u00fcr Thoraxchirurgie, Universit\u00e4tsklinikum Freiburg, Medizinische\n                    Fakult\u00e4t, Albert-Ludwigs-Universit\u00e4t Freiburg, Freiburg,\n                    Deutschland"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"194","published-online":{"date-parts":[[2022,1,19]]},"reference":[{"key":"ref1","doi-asserted-by":"publisher","first-page":"273","DOI":"10.1007\/s00247-011-2303-0","article-title":"Prenatal diagnosis of congenital lung malformations","volume":"42","author":"L Alamo","year":"2012","journal-title":"Pediatr Radiol"},{"key":"ref2","doi-asserted-by":"publisher","first-page":"1328","DOI":"10.1164\/rccm.201706-1243OC","article-title":"Novel molecular and phenotypic insights into congenital lung malformations","volume":"197","author":"DT 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