{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,6,29]],"date-time":"2024-06-29T12:40:15Z","timestamp":1719664815237},"reference-count":7,"publisher":"Georg Thieme Verlag KG","issue":"05","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Handchir Mikrochir Plast Chir"],"published-print":{"date-parts":[[2023,9]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Wir berichten \u00fcber die Behandlung einer 22-j\u00e4hrigen Patientin mit\n                    akuter Weichteilinfektion im Bereich einer Schn\u00fcrfurche bei\n                    palmoplantarem Keratoderm-kongenitalem Alopezie-Syndrom (PPKCA) Typ II, einer\n                    sehr seltenen Genodermatose mit weniger als 20 in der Literatur beschriebenen\n                    F\u00e4llen. Bei vorbestehender Schn\u00fcrfurche des rechten Kleinfingers\n                    mit Hyperkeratose kam es durch eine additive Weichteilinfektion distal des\n                    Sch\u00fcrrings zu einer Dekompensation des lymphatischen und ven\u00f6sen\n                    Abflusses mit drohendem Fingerverlust. Durch die dringliche operative Versorgung\n                    mit Entlastung und Sanierung der dorsalen Weichteilinfektion, mikrochirurgischer\n                    zirkul\u00e4rer Resektion des Schn\u00fcrrings sowie Wundverschluss konnte\n                    der Finger erhalten werden. Nach Weichteilkonsolidierung und ergotherapeutischer\n                    Be\u00fcbung erreichte die Patientin eine freie Beweglichkeit des\n                    Kleinfingers bei subjektiver Beschwerdefreiheit mit gutem \u00e4sthetischen\n                    Ergebnis.<\/jats:p>","DOI":"10.1055\/a-2013-2131","type":"journal-article","created":{"date-parts":[[2023,3,27]],"date-time":"2023-03-27T22:42:00Z","timestamp":1679956920000},"page":"368-372","source":"Crossref","is-referenced-by-count":0,"title":["Akute Weichteilinfektion mit drohendem Fingerverlust bei\n                    Schn\u00fcrfurchensyndrom einer 22-j\u00e4hrigen Patientin mit\n                    palmoplantarem Keratoderm-kongenitalem Alopezie-Syndrom Typ II"],"prefix":"10.1055","volume":"55","author":[{"given":"Moritz","family":"Gugelmeier","sequence":"additional","affiliation":[{"name":"Zentrum f\u00fcr Muskuloskelettale Medizin Klinik f\u00fcr\n                    Orthop\u00e4die, Unfall-, Hand- und Wiederherstellungschirurgie , Vivantes\n                    Klinikum im Friedrichshain, Berlin, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Arthur","family":"Kostron","sequence":"additional","affiliation":[{"name":"Zentrum f\u00fcr Muskuloskelettale Medizin Klinik f\u00fcr\n                    Orthop\u00e4die, Unfall-, Hand- und Wiederherstellungschirurgie , Vivantes\n                    Klinikum im Friedrichshain, Berlin, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas","family":"Poser","sequence":"additional","affiliation":[{"name":"Zentrum f\u00fcr Muskuloskelettale Medizin Klinik f\u00fcr\n                    Orthop\u00e4die, Unfall-, Hand- und Wiederherstellungschirurgie , Vivantes\n                    Klinikum im Friedrichshain, Berlin, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lisa C.","family":"Schneider","sequence":"additional","affiliation":[{"name":"Klinik f\u00fcr Dermatologie und Phlebologie, Vivantes Klinikum im\n                    Friedrichshain, Berlin, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Wiebke K.","family":"Peitsch","sequence":"additional","affiliation":[{"name":"Klinik f\u00fcr Dermatologie und Phlebologie, Vivantes Klinikum im\n                    Friedrichshain, Berlin, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas","family":"Fuchs","sequence":"additional","affiliation":[{"name":"Zentrum f\u00fcr Muskuloskelettale Medizin Klinik f\u00fcr\n                    Orthop\u00e4die, Unfall-, Hand- und Wiederherstellungschirurgie , Vivantes\n                    Klinikum im Friedrichshain, Berlin, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"194","published-online":{"date-parts":[[2023,3,27]]},"reference":[{"key":"ref1","doi-asserted-by":"publisher","first-page":"541","DOI":"10.1001\/archpedi.1988.02150050079037","article-title":"Epidemiology of the early amnion rupture spectrum of defects","volume":"142","author":"A Garza","year":"1988","journal-title":"Am J Dis Child"},{"key":"ref2","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1016\/s0007-1226(61)80002-7","article-title":"Congenital ring-constrictions","volume":"14","author":"TJS. Patterson","year":"1961","journal-title":"Br J Plast Surg"},{"key":"ref3","doi-asserted-by":"publisher","first-page":"500","DOI":"10.1002\/ajmg.1320320415","article-title":"Cataracts, alopecia, and sclerodactyly: a previously apparently undescribed\n                    ectodermal dysplasia syndrome on the island of Rodrigues","volume":"32","author":"C Wallis","year":"1989","journal-title":"Am J Med Genet"},{"key":"ref4","doi-asserted-by":"publisher","first-page":"632","DOI":"10.1111\/ced.12857","article-title":"Clinical and molecular characterization of two patients with palmoplantar\n                    keratoderma-congenital alopecia syndrome type 2","volume":"41","author":"M Castori","year":"2016","journal-title":"Clin Exp Dermatol"},{"key":"ref5","doi-asserted-by":"publisher","first-page":"2043","DOI":"10.1002\/ajmg.a.33490","article-title":"Palmoplantar keratoderma, pseudo-ainhum, and universal atrichia: A new patient\n                    and review of the palmoplantar keratoderma-congenital alopecia syndrome","volume":"152A","author":"M Castori","year":"2010","journal-title":"Am J Med Genet"},{"key":"ref6","doi-asserted-by":"publisher","DOI":"10.1016\/j.jid.2022.03.23 Epub ahead of print.","article-title":"Biallelic Variants in lanosterol synthase (LSS) cause palmoplantar\n                    keratoderma-congenital alopecia syndrome type 2","volume":"10","author":"F Yang","year":"2022","journal-title":"J Invest Dermatol"},{"key":"ref7","doi-asserted-by":"publisher","first-page":"972","DOI":"10.1097\/00006534-199509001-00033","article-title":"Constriction band-induced vascular compromise of the foot: classification and\n                    management of the \u201cintermediate\u201d stage of constriction-ring\n                    syndrome","volume":"96","author":"N. Weinzweig","year":"1995","journal-title":"Plast Reconstr Surg"}],"container-title":["Handchirurgie \u00b7 Mikrochirurgie \u00b7 Plastische Chirurgie"],"original-title":[],"language":"de","link":[{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.1055\/a-2013-2131.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,6,29]],"date-time":"2024-06-29T12:20:50Z","timestamp":1719663650000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.thieme-connect.de\/DOI\/DOI?10.1055\/a-2013-2131"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,3,27]]},"references-count":7,"journal-issue":{"issue":"05","published-online":{"date-parts":[[2023,9,21]]},"published-print":{"date-parts":[[2023,9]]}},"URL":"https:\/\/doi.org\/10.1055\/a-2013-2131","archive":["Portico","CLOCKSS"],"relation":{},"ISSN":["0722-1819","1439-3980"],"issn-type":[{"value":"0722-1819","type":"print"},{"value":"1439-3980","type":"electronic"}],"subject":[],"published":{"date-parts":[[2023,3,27]]}}}