{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,16]],"date-time":"2025-10-16T09:24:55Z","timestamp":1760606695793,"version":"3.37.3"},"reference-count":12,"publisher":"Georg Thieme Verlag KG","issue":"01","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Eur J Pediatr Surg"],"published-print":{"date-parts":[[2024,2]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>\n          Introduction\u2003Coexistent congenital duodenal obstruction and esophageal atresia (EA) is known to have significant morbidity and mortality. Management strategies are not well-defined for this association. The data from the Turkish EA registry is evaluated.<\/jats:p><jats:p>\n          Materials and Methods\u2003A database search was done for the years 2015 to 2022.<\/jats:p><jats:p>\n          Results\u2003Among 857 EA patients, 31 (3.6%) had congenital duodenal obstruction. The mean birth weight was 2,104 (\u00b1 457) g with 6 babies weighing less than 1,500\u2009g. Twenty-six (84%) had type C EA. The duodenal obstruction was complete in 15 patients and partial in 16. Other anomalies were detected in 27 (87%) patients. VACTERL-H was present in 15 (48%), anorectal malformation in 10 (32%), a major cardiac malformation in 6 (19%), and trisomy-21 in 3 (10%). Duodenal obstruction diagnosis was delayed in 10 (32%) babies for a median of 7.5 (1\u2013109) days. Diagnosis for esophageal pathologies was delayed in 2. Among 19 babies with a simultaneous diagnosis, 1 died without surgery, 6 underwent triple repair for tracheoesophageal fistula (TEF), EA, and duodenal obstruction, and 3 for TEF and duodenal obstruction in the same session. A staged repair was planned in the remaining 9 patients. In total, 15 (48%) patients received a gastrostomy, the indication was long-gap EA in 8. Twenty-five (77%) patients survived. The cause of mortality was sepsis (n\u2009=\u20093) and major cardiac malformations (n\u2009=\u20093).<\/jats:p><jats:p>\n          Conclusion\u2003Congenital duodenal obstruction associated with EA is a complex problem. Delayed diagnosis is common. Management strategies regarding single-stage repairs or gastrostomy insertions vary notably depending on the patient characteristics and institutional preferences.<\/jats:p>","DOI":"10.1055\/a-2123-5026","type":"journal-article","created":{"date-parts":[[2023,7,5]],"date-time":"2023-07-05T23:20:37Z","timestamp":1688599237000},"page":"044-049","source":"Crossref","is-referenced-by-count":2,"title":["Esophageal Atresia Associated with Congenital Duodenal Obstruction: Turkish Esophageal Atresia Registry (TEAR) Evaluation"],"prefix":"10.1055","volume":"34","author":[{"given":"\u00c7i\u011fdem Ulukaya","family":"Durakba\u015fa","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Istanbul Medeniyet University Faculty of Medicine, Istanbul, Turkey"},{"name":"Department of Pediatric Surgery, Goztepe Prof. Dr. Suleyman Yalcin City Hospital, Istanbul, Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1505-6042","authenticated-orcid":false,"given":"Tutku","family":"Soyer","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H\u00fcseyin","family":"\u0130lhan","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Eskisehir Osmangazi University Faculty of Medicine, Eskisehir, Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3696-4090","authenticated-orcid":false,"given":"Mustafa Onur","family":"Oztan","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Izmir Katip Celebi University, Izmir, Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9031-0373","authenticated-orcid":false,"given":"Osman","family":"Uzunlu","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Pamukkale University, Denizli, Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Binali","family":"Firinci","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Ataturk University School of Medicine, Erzurum, Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Rah\u015fan","family":"\u00d6zcan","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Istanbul University-Cerrahpasa Cerrahpasa Faculty of Medicine, Istanbul, Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Akgun","family":"Oral","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Dr. Behcet Uz Child Disease and Surgery 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