{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,11,6]],"date-time":"2024-11-06T05:24:53Z","timestamp":1730870693734,"version":"3.28.0"},"reference-count":36,"publisher":"Georg Thieme Verlag KG","issue":"02","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Laryngorhinootologie"],"published-print":{"date-parts":[[2024,2]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Das Beh\u00e7et- und das Cogan-Syndrom bilden zusammen die Gruppe der Vaskulitiden der variablen Gef\u00e4\u00dfe nach der Chapel-Hill Nomenklatur. Sie k\u00f6nnen Arterien und Venen jeder Gr\u00f6\u00dfe betreffen. Wie die Bezeichnung \u201eSyndrom\u201c bei beiden Krankheitsbildern bereits widerspiegelt, k\u00f6nnen beide individuell sehr unterschiedliche Symptome bieten. Beide z\u00e4hlen formal zu den seltenen Erkrankungen, wobei das Cogan-Syndrom mit der Beschreibung von lediglich einigen hundert F\u00e4llen weltweit deutlich seltener als das Beh\u03c2et-Syndrom ist. F\u00fcr letzteres gibt es Diagnose- und Klassifikationskriterien, und auch europ\u00e4ische (EULAR, European Alliance of Associations for Rheumatology) Therapieempfehlungen. Symptomatologie, Diagnostik und Therapie, aber auch einige \u00dcberlegungen zur Pathogenese dieser beiden Vaskulitiden werden im Folgenden beleuchtet.<\/jats:p>","DOI":"10.1055\/a-2192-3950","type":"journal-article","created":{"date-parts":[[2023,11,21]],"date-time":"2023-11-21T23:55:46Z","timestamp":1700610946000},"page":"113-119","source":"Crossref","is-referenced-by-count":1,"title":["Beh\u00e7et- und Cogan-Syndrom"],"prefix":"10.1055","volume":"103","author":[{"given":"Ina","family":"K\u00f6tter","sequence":"additional","affiliation":[{"name":"Nephrology and Rheumatology, University Hospital Hamburg Eppendorf Center of Internal Medicine, Hamburg, Germany"},{"name":"Rheumatology and Immunology, Klinikum Bad Bramstedt GmbH, Bad Bramstedt, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"194","published-online":{"date-parts":[[2023,11,21]]},"reference":[{"key":"ref1","first-page":"1152","article-title":"\u00dcber rezidivierende, aphth\u00f6se, durch ein Virus verursachte Geschw\u00fcre im Mund, am Auge und an den Genitalien","volume":"105","author":"H Behcet","year":"1937","journal-title":"Dermatol Wschr"},{"key":"ref2","first-page":"586","article-title":"A case of relapsing iritis with hypopion (in Greek)","author":"B Adamantiades","year":"1930","journal-title":"Archia Iatrikis Etairas (Proceedings of hte Medical Society of Athens)"},{"key":"ref3","doi-asserted-by":"publisher","first-page":"603","DOI":"10.1007\/s10157-013-0869-6","article-title":"Overview of the 2012 revised International Chapel Hill Consensus Conference nomenclature of vasculitides","volume":"17","author":"JC Jennette","year":"2013","journal-title":"Clin Exp Nephrol"},{"key":"ref4","doi-asserted-by":"publisher","first-page":"695","DOI":"10.1001\/archopht.1959.00940090697004","article-title":"Syndrome of nonsyphilitic interstitial keratitis and vestibuloauditory symptoms; 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