{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,9]],"date-time":"2026-07-09T11:03:45Z","timestamp":1783595025665,"version":"3.55.0"},"reference-count":31,"publisher":"American Academy of Audiology","issue":"9","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["j am acad audiol"],"published-print":{"date-parts":[[2024,10,1]]},"abstract":"<jats:p><jats:bold>Abstract<\/jats:bold>  <jats:bold>Background<\/jats:bold>\u2003We describe a 42-year-old patient with reported \u201cshaking\u201d vision referred due to concerns of possible vestibular system dysfunction. The patient has known history of Usher syndrome type I, bilateral cochlear implants, and severe\n vision impairment. <jats:bold>Purpose<\/jats:bold>\u2003This case describes an unusual nystagmus previously only reported in individuals with central demyelinating disorders, significant light deprivation, or in congenital\/early-onset visual pathway impairment. <jats:bold>Research Design<\/jats:bold>\u2003Case study.\n <jats:bold>Data Collection and Analysis<\/jats:bold>\u2003Retrospective chart review of vestibular function. <jats:bold>Results<\/jats:bold>\u2003Vestibular function was likely absent in this case. There was no evidence of vestibular (jerk) nystagmus for sinusoidal harmonic acceleration stimuli or repeatable responses\n for cervical vestibular evoked myogenic potentials. Significant pendular low-amplitude high-frequency oscillations of approximately 6\u2009Hz were present for horizontal and vertical tracings throughout testing. <jats:bold>Conclusion<\/jats:bold>\u2003Nystagmus may not always be associated with vestibular\n system impairment. In this case, the patient's reported \u201cshaking\u201d vision was attributed to pendular low-amplitude high-frequency nystagmus and hypothesized to relate to long-standing significant vision impairment. This presentation is unusual in adults and has historically been\n associated with individuals with significant central pathology or in those with long duration light deprivation.<\/jats:p>","DOI":"10.1055\/a-2318-1389","type":"journal-article","created":{"date-parts":[[2024,5,3]],"date-time":"2024-05-03T05:22:50Z","timestamp":1714713770000},"page":"263-269","source":"Crossref","is-referenced-by-count":1,"title":["Pendular Nystagmus Presenting in Usher Syndrome Type I: A Case Report"],"prefix":"10.3766","volume":"35","author":[{"given":"Jamie M.","family":"Bogle","sequence":"first","affiliation":[{"name":"Division of Audiology, Department of Otorhinolaryngology\/Head and Neck Surgery, Mayo Clinic Arizona, Scottsdale, Arizona"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David A.","family":"Zapala","sequence":"additional","affiliation":[{"name":"Division of Audiology, Department of Otolaryngology\/Head and Neck Surgery, Mayo Clinic Florida, Jacksonville, 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