{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,17]],"date-time":"2026-08-17T05:37:03Z","timestamp":1786945023695,"version":"build-2736575974"},"reference-count":29,"publisher":"Georg Thieme Verlag KG","issue":"08","license":[{"start":{"date-parts":[[2025,4,1]],"date-time":"2025-04-01T00:00:00Z","timestamp":1743465600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pneumologie"],"published-print":{"date-parts":[[2025,8]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Die Prim\u00e4re Cili\u00e4re Dyskinesie (PCD) ist eine Multisystemerkrankung, die durch eine\n      Dysfunktion motiler Zilien entsteht. Charakteristisch ist eine chronische Sekretretention der\n      oberen und unteren Atemwege, die zu einer destruierenden Lungenerkrankung mit Ausbildung von\n      Bronchiektasen f\u00fchrt. Es gibt kaum evidenzbasierte Therapien f\u00fcr Patientinnen und Patienten\n      mit PCD, die meisten Behandlungskonzepte sind an andere Atemwegserkrankungen angelehnt oder\n      beruhen auf der Meinung von Expertinnen und Experten. Der vorliegende Artikel befasst sich mit\n      der physiotherapeutischen Versorgung von Menschen mit PCD und gibt eine \u00dcbersicht \u00fcber\n      Empfehlungen aus der vorhandenen Literatur sowie \u00fcber langj\u00e4hrige Erfahrung in der\n      physiotherapeutischen Behandlung von Patientinnen und Patienten mit PCD. Da es aktuell keine\n      kurative Therapie f\u00fcr die PCD gibt, ist die symptomatische Behandlung mit dem Fokus auf dem\n      Sekretmanagement von gro\u00dfer Bedeutung. Diese umfasst v.a. Inhalation, Sekretmobilisation,\n      k\u00f6rperliche Aktivit\u00e4t und die gezielte Verwendung von Hilfsmitteln sowie Rehabilitation. Eine\n      Anleitung und Steuerung der Physiotherapie sollten nach M\u00f6glichkeit durch speziell\n      ausgebildete Therapeutinnen und Therapeuten erfolgen.<\/jats:p>","DOI":"10.1055\/a-2502-8151","type":"journal-article","created":{"date-parts":[[2025,4,1]],"date-time":"2025-04-01T19:58:03Z","timestamp":1743537483000},"page":"577-584","source":"Crossref","is-referenced-by-count":1,"title":["Physiotherapie bei Prim\u00e4rer Cili\u00e4rer Dyskinesie (PCD)"],"prefix":"10.1055","volume":"79","author":[{"given":"Christina","family":"Kr\u00e4mer","sequence":"additional","affiliation":[{"name":"Zentrale Einrichtung Therapeutische Gesundheitsberufe, Universit\u00e4tsklinikum M\u00fcnster, M\u00fcnster, Deutschland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jasmin","family":"Flock","sequence":"additional","affiliation":[{"name":"Praxis f\u00fcr Klein & Gro\u00df, Physiotherapie Kirbach, Duisburg, 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