{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,7]],"date-time":"2026-08-07T15:01:29Z","timestamp":1786114889874,"version":"build-2736575974"},"reference-count":25,"publisher":"Georg Thieme Verlag KG","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Handchir Mikrochir Plast Chir"],"abstract":"<jats:title>Zusammenfassung<\/jats:title>\n                  <jats:p>Das Popliteale Pterygium-Syndrom (PPS) ist eine seltene, autosomal-dominant vererbte Fehlbildung mit typischer Ausbildung eines Haut- und Weichteilstrangs in der Kniekehle. Funktionseinschr\u00e4nkungen durch Beugekontrakturen, Spitzfu\u00df- und H\u00fcftfehlstellungen sind h\u00e4ufig. In der Literatur dominieren Einzelfallberichte, fundierte Langzeitergebnisse fehlen bislang.<\/jats:p>\n                  <jats:p>In einer retrospektiven Fallserie wurden vier Patienten mit poplitealem Pterygium und funktionell relevanter Beugekontraktur operativ behandelt. Das operative Vorgehen umfasste die vollst\u00e4ndige Resektion des fibr\u00f6sen Stranges, multiple Z-Plastiken, eine mikrochirurgische Neurolyse des N. ischiadicus sowie eine Achillessehnenverl\u00e4ngerung. Die mittlere Nachbeobachtungszeit betrug 16 Jahre (5\u201323 Jahre). Postoperativ kamen individualisierte Orthesen und in zwei F\u00e4llen eigens konstruierte Dehnungsmaschinen zum Einsatz.<\/jats:p>\n                  <jats:p>Die Extension im Kniegelenk verbesserte sich im Mittel um 30\u00b0 (von pr\u00e4operativ 45\u00b0 auf 15\u00b0 postoperativ). Alle Patienten waren bis zum letzten Follow-up ohne Gehhilfe mobil, ein wachstumsbedingtes Rezidiv trat in einem Fall auf. Neuromschmerzen oder sekund\u00e4re Paresen wurden nicht beobachtet.<\/jats:p>\n                  <jats:p>Bei funktionell relevanten poplitealen Pterygien kann ein einmaliges operatives Vorgehen mit vollst\u00e4ndiger Strangresektion, Neurolyse und multiplen Z-Plastiken in Kombination mit einer konsequenten postoperativen Dehn- und Orthesenbehandlung eine dauerhafte Funktionsverbesserung erm\u00f6glichen. Die vorliegende Fallserie zeigt erstmals Langzeitergebnisse \u00fcber mehr als zwei Jahrzehnte.<\/jats:p>","DOI":"10.1055\/a-2854-5510","type":"journal-article","created":{"date-parts":[[2026,8,5]],"date-time":"2026-08-05T22:46:09Z","timestamp":1785969969000},"source":"Crossref","is-referenced-by-count":0,"title":["Das Popliteale Pterygium Syndrom (PPS) \u2013 Multimodales Behandlungskonzept und Langzeitergebnisse in 4 F\u00e4llen"],"prefix":"10.1055","author":[{"given":"Andrea","family":"Wenger","sequence":"additional","affiliation":[{"name":"BG Unfallklinik, Germany","place":["T\u00fcbingen"],"department":["Hand-, Plastische-, Rekonstruktive- und Verbrennungschirurgie"]},{"name":"Eberhard Karls Universit\u00e4t T\u00fcbingen, BW, Germany","place":["T\u00fcbingen"],"department":["Medizinische Fakult\u00e4t"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael","family":"Sch\u00e4fer","sequence":"additional","affiliation":[{"name":"Pohlig Otto Bock Care, Germany","place":["Traunstein"],"department":["Orthop\u00e4dietechnik"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hildegunde","family":"Piza-Katzer","sequence":"additional","affiliation":[{"name":"Medizinische Universit\u00e4t Innsbruck, Austria","place":["Innsbruck"],"department":["Universit\u00e4tsklinik f\u00fcr Plastische und Wiederherstellungsschirurgie"]},{"name":"Privatordination, Austria","place":["Wien"],"department":["Plast. und Wiederherstellungschirurgie"]}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"194","published-online":{"date-parts":[[2026,8,5]]},"reference":[{"key":"ref1","first-page":"320","article-title":"Popliteal pterygium syndrome. 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