{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,19]],"date-time":"2026-09-19T13:45:53Z","timestamp":1789825553688,"version":"4.0.1"},"reference-count":43,"publisher":"Georg Thieme Verlag KG","issue":"09","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Klin Monbl Augenheilkd"],"published-print":{"date-parts":[[2026,9]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>Macular telangiectasia type 2 (MacTel type 2) is a progressive neurodegenerative macular disease whose diagnosis, prognostic assessment, and longitudinal monitoring rely critically on the recognition of its characteristic clinical and imaging features. This systematic review provides a comprehensive overview of the most important diagnostic findings in MacTel type 2, encompassing both biomicroscopic clinical signs and the full spectrum of multimodal imaging modalities currently employed in clinical practice\u2014including color fundus photography, fluorescein angiography, fundus autofluorescence, multicolor imaging, spectral-domain optical coherence tomography (OCT), and OCT angiography. For each modality, key diagnostic signs, their contribution to disease staging, and their value in monitoring disease progression are discussed. Additionally, a specific focus on emerging imaging techniques is provided with potential relevance to future diagnostic and research applications. In\n          MacTel type 2, a multimodal imaging approach represents the most effective strategy for accurate diagnosis, reliable staging of disease severity, and meaningful prognostic assessment.<\/jats:p>","DOI":"10.1055\/a-2937-4106","type":"journal-article","created":{"date-parts":[[2026,8,27]],"date-time":"2026-08-27T23:11:15Z","timestamp":1787872275000},"page":"901-910","source":"Crossref","is-referenced-by-count":1,"title":["Macular Telangiectasia Type 2: Current and Emerging Diagnostic Imaging Modalities"],"prefix":"10.1055","volume":"243","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-3926-0825","authenticated-orcid":false,"given":"Chantal","family":"Dysli","sequence":"additional","affiliation":[{"name":"Inselspital University Hospital Bern, BE, Switzerland","place":["Bern"],"department":["Department of Ophthalmology"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nicola","family":"Sagurski","sequence":"additional","affiliation":[{"name":"Inselspital University Hospital Bern, BE, Switzerland","place":["Bern"],"department":["Department of Ophthalmology"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lorenzo","family":"Ferro Desideri","sequence":"additional","affiliation":[{"name":"Inselspital University Hospital Bern, BE, Switzerland","place":["Bern"],"department":["Department of Ophthalmology"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Martin S.","family":"Zinkernagel","sequence":"additional","affiliation":[{"name":"Inselspital University Hospital Bern, BE, Switzerland","place":["Bern"],"department":["Department of Ophthalmology"]}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"194","published-online":{"date-parts":[[2026,8,27]]},"reference":[{"key":"ref1","doi-asserted-by":"crossref","first-page":"49","DOI":"10.1016\/j.preteyeres.2012.11.002","article-title":"Macular telangiectasia type 2","volume":"34","author":"P Charbel Issa","year":"2013","journal-title":"Prog Retin Eye Res"},{"key":"ref2","doi-asserted-by":"crossref","first-page":"101401","DOI":"10.1016\/j.preteyeres.2025.101401","article-title":"Clinical histopathology and pathogenesis of macular telangiectasia type 2","volume":"110","author":"D P Ntentakis","year":"2026","journal-title":"Prog Retin Eye Res"},{"issue":"10","key":"ref3","doi-asserted-by":"crossref","first-page":"1536","DOI":"10.1016\/S0161-6420(93)31447-8","article-title":"Idiopathic juxtafoveolar retinal telangiectasis. 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