{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,18]],"date-time":"2026-10-18T22:51:26Z","timestamp":1792363886487,"version":"4.4.0"},"reference-count":0,"publisher":"Georg Thieme Verlag KG","issue":"01","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Eur J Pediatr Surg"],"published-print":{"date-parts":[[2018,2]]},"abstract":"<jats:p>\n            Aim\u2003To define current management of congenital pulmonary airway malformation (CPAM).<\/jats:p><jats:p>\n            Methods\u2003A total of 181 European Pediatric Surgeons' Association members (91% senior) from 48 countries completed an online questionnaire.<\/jats:p><jats:p>\n            Main Results\u2003Prenatal: 93% respondents work in centers with prenatal diagnosis facilities, and 27% in centers offering in utero surgery. Prenatal counseling is performed by 86% respondents, 22% of whom see &gt;10 cases per year. Risk of single pre-\/postnatal complications is deemed low (&lt;5%) by more than 60% of respondents. Eighty-six percent respondents do not offer pregnancy termination for prenatally diagnosed CPAM. Fetal hydrops is the most frequent indication for termination (87%), followed by parental willingness (52%). Prenatal surgery is an option for 44% respondents, preferring thoracoamniotic shunt (82%).<\/jats:p><jats:p>Postnatal: 75% respondents operate on asymptomatic patients, 18% before 6 months of age, 62% between 6 and 12 months of age, and 20% after 12 months of age. Risk of infection (86%), cancer (63%), and symptoms development (62%) are indications for surgery in asymptomatic CPAM. Sixty-three percent prefer a thoracotomy. Lobectomy is the preferred procedure (58% respondents). Motivations against surgery include lesion &lt;1 cm (64%), risk of postoperative complications (37%), and lack of evidence favoring surgery (27%). Seventeen percent respondents have seen at least one patient with CPAM with lung cancer, in 89% of the cases within the CPAM. Of all the respondents, 83% and 22% offered dedicated follow-up and genetic screening, respectively.<\/jats:p><jats:p>\n            Conclusion\u2003Current pre- and postnatal management of CPAM lacks uniformity, particularly for surgical indication, timing, and approach. Efforts should be made toward standardization. Risk of CPAM-associated cancer is not clear.<\/jats:p>","DOI":"10.1055\/s-0037-1604020","type":"journal-article","created":{"date-parts":[[2017,7,14]],"date-time":"2017-07-14T18:40:38Z","timestamp":1500057638000},"page":"001-005","source":"Crossref","is-referenced-by-count":60,"title":["Current Management of Congenital Pulmonary Airway Malformations: A \u201cEuropean Pediatric Surgeons' Association\u201d Survey"],"prefix":"10.1055","volume":"28","author":[{"given":"Francesco","family":"Morini","sequence":"first","affiliation":[{"name":"Department of Medical and Surgical Neonatology, Bambino Gesu Children's Research Hospital, Rome, Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Augusto","family":"Zani","sequence":"first","affiliation":[{"name":"Division of General and Thoracic Surgery, The Hospital for Sick Children, Toronto, Ontario, Canada"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andrea","family":"Conforti","sequence":"first","affiliation":[{"name":"Department of Medical and Surgical Neonatology, Bambino Gesu Children's Research Hospital, Rome, Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ernest","family":"van Heurn","sequence":"first","affiliation":[{"name":"Department of Pediatric Surgery, AMC\/VUMC, Amsterdam, The Netherlands"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Simon","family":"Eaton","sequence":"first","affiliation":[{"name":"Department of Pediatric Surgery, University College London Institute of Child Health, London, United Kingdom"},{"name":"Department of Paediatric Surgery, Great Ormond Street Hospital for Children NHS Trust, London, United Kingdom"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Prem","family":"Puri","sequence":"first","affiliation":[{"name":"Department of Paediatric Surgery, National Children's Research Centre, Dublin, Ireland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Risto","family":"Rintala","sequence":"first","affiliation":[{"name":"Department of Paediatric Surgery, Hospital for Children and Adolescents, Helsinki, Finland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marija","family":"Lukac","sequence":"first","affiliation":[{"name":"Division of Medicine, Department of Pediatric Surgery, Belgrade, Serbia"},{"name":"Department of Neonatal Surgery, University Children's Hospital, Belgrade, Serbia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Joachim","family":"Kuebler","sequence":"first","affiliation":[{"name":"Department of Pediatric Surgery, Hannover Medical School, Hannover, Niedersachsen, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Florian","family":"Friedmacher","sequence":"first","affiliation":[{"name":"National Children's Research Centre, Our Lady's Children's Hospital, Crumlin, Dublin, Ireland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rene","family":"Wijnen","sequence":"first","affiliation":[{"name":"Department of Pediatric Surgery, Sophia Children's Hospital, Erasmus MC, Rotterdam, The Netherlands"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Juan","family":"Tovar","sequence":"first","affiliation":[{"name":"Department of Pediatric Surgery, Hospital Universitario La Paz, Madrid, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Agostino","family":"Pierro","sequence":"first","affiliation":[{"name":"Division of General and Thoracic Surgery, The Hospital for Sick Children, Toronto, Ontario, Canada"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pietro","family":"Bagolan","sequence":"additional","affiliation":[{"name":"Department of Medical and Surgical Neonatology, Bambino Gesu Children's Research Hospital, Rome, Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"194","published-online":{"date-parts":[[2017,7,14]]},"container-title":["European Journal of Pediatric Surgery"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.1055\/s-0037-1604020.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2018,1,19]],"date-time":"2018-01-19T18:31:07Z","timestamp":1516386667000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.thieme-connect.de\/DOI\/DOI?10.1055\/s-0037-1604020"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,7,14]]},"references-count":0,"journal-issue":{"issue":"01","published-online":{"date-parts":[[2018,1,19]]},"published-print":{"date-parts":[[2018,2]]}},"URL":"https:\/\/doi.org\/10.1055\/s-0037-1604020","relation":{},"ISSN":["0939-7248","1439-359X"],"issn-type":[{"value":"0939-7248","type":"print"},{"value":"1439-359X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,7,14]]}}}