{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,4,3]],"date-time":"2022-04-03T00:46:21Z","timestamp":1648946781932},"reference-count":0,"publisher":"Georg Thieme Verlag KG","issue":"01","license":[{"start":{"date-parts":[[2018,3,22]],"date-time":"2018-03-22T00:00:00Z","timestamp":1521676800000},"content-version":"vor","delay-in-days":80,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["THORAC CARDIOV SURG Reports"],"published-print":{"date-parts":[[2018,1]]},"abstract":"<jats:p>\n            Background\u2003Factor X deficiency (also known as Stuart\u2013Prower factor deficiency) is an autosomal recessive extremely rare hereditary hematologic disorder, affecting around 1:1,000,000 of the general population.<\/jats:p><jats:p>\n            Case Presentation\u2003This case report describes a patient with hypoplastic left heart syndrome and severe factor X deficiency, who underwent staged surgical palliation. From stage 1 Norwood palliation, through superior cavopulmonary anastomosis and ending with total cavopulmonary connection with satisfactory hemostasis and no significant perioperative bleeding complication.<\/jats:p><jats:p>\n            Conclusion\u2003The need to maintain hemostasis while aiming to prevent intracardiac thrombosis requires multidisciplinary team approach including hematologist, cardiac surgeon, pediatric cardiac intensivist, and anesthesiologist along with meticulous hemostasis during surgery and careful monitoring of coagulation profile in the postoperative period.<\/jats:p>","DOI":"10.1055\/s-0038-1637743","type":"journal-article","created":{"date-parts":[[2018,3,22]],"date-time":"2018-03-22T23:56:50Z","timestamp":1521763010000},"page":"e12-e15","source":"Crossref","is-referenced-by-count":1,"title":["Staged Surgical Palliation for HLHS in a Girl with Severe Factor X Deficiency"],"prefix":"10.1055","volume":"07","author":[{"given":"Ahmed","family":"Elmahrouk","sequence":"additional","affiliation":[{"name":"Department of Cardiothoracic Surgery, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia"},{"name":"Department of Cardiothoracic Surgery, Tanta University Faculty of Medicine, Tanta, Egypt"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mohamed","family":"Ismail","sequence":"additional","affiliation":[{"name":"Department of Cardiothoracic Surgery, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia"},{"name":"Mansoura University Faculty of Medicine, Mansoura, Egypt"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Abdulbadee","family":"Bugis","sequence":"additional","affiliation":[{"name":"Department of Cardiothoracic Surgery, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nashwa","family":"Badawy","sequence":"additional","affiliation":[{"name":"Department of Cardiothoracic Surgery, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia"},{"name":"Cairo University Kasr Alainy Faculty of Medicine, Cairo, Egypt"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hesham","family":"Aboelghar","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Menoufia University Faculty of Medicine, Shebin El-Kom, Saudi Arabia"},{"name":"Department of Hematology and Oncology BMT, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tamer","family":"Hamouda","sequence":"additional","affiliation":[{"name":"Department of Cardiothoracic Surgery, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia"},{"name":"Department of Cardiothoracic Surgery, Faculty of Medicine, Benha University, Benha, Egypt"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ahmed","family":"Jamjoom","sequence":"additional","affiliation":[{"name":"Department of Cardiothoracic Surgery, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"194","published-online":{"date-parts":[[2018,3,22]]},"container-title":["The Thoracic and Cardiovascular Surgeon Reports"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.1055\/s-0038-1637743.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,5,6]],"date-time":"2019-05-06T20:10:43Z","timestamp":1557173443000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.thieme-connect.de\/DOI\/DOI?10.1055\/s-0038-1637743"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,1]]},"references-count":0,"journal-issue":{"issue":"01","published-online":{"date-parts":[[2018,2,20]]},"published-print":{"date-parts":[[2018,1]]}},"URL":"https:\/\/doi.org\/10.1055\/s-0038-1637743","relation":{},"ISSN":["2194-7635","2194-7643"],"issn-type":[{"value":"2194-7635","type":"print"},{"value":"2194-7643","type":"electronic"}],"subject":[],"published":{"date-parts":[[2018,1]]}}}