{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,19]],"date-time":"2026-03-19T12:27:12Z","timestamp":1773923232622,"version":"3.50.1"},"reference-count":31,"publisher":"Federa\u00e7\u00e3o das Associa\u00e7\u00f5es de Ginecologia e Obstetr\u00edcia","issue":"05","license":[{"start":{"date-parts":[[2019,3,25]],"date-time":"2019-03-25T00:00:00Z","timestamp":1553472000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Rev Bras Ginecol Obstet"],"published-print":{"date-parts":[[2019,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Pentalogy of Cantrell (PC) is a rare congenital anomaly characterized by changes in the mesodermal median structures and congenital heart disease, often with a poor prognosis. In 1958, Cantrell et al2 defined the full spectrum of the syndrome with the following anomalies: defects of the anterior diaphragm, of the lower part of the sternum, of the supraumbilical region and the abdominal wall, of the diaphragmatic pericardium, and various intracardiac congenital abnormalities. The present report describes a case of ectopia cordis associated with PC and the importance of the participation of a multidisciplinary team in the treatment of this condition.<\/jats:p>","DOI":"10.1055\/s-0039-1679878","type":"journal-article","created":{"date-parts":[[2019,3,26]],"date-time":"2019-03-26T00:14:27Z","timestamp":1553559267000},"page":"352-356","source":"Crossref","is-referenced-by-count":7,"title":["Ectopia Cordis Associated with Pentalogy of Cantrell\u2014A Case Report"],"prefix":"10.61622","volume":"41","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-2345-4713","authenticated-orcid":false,"given":"Jos\u00e9 Mauro","family":"Madi","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology, Faculty of Medicine, Universidade de Caxias do Sul, Caxias do Sul, RS, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jos\u00e9 Roberto","family":"Festugatto","sequence":"additional","affiliation":[{"name":"Department of Radiology, Hospital Geral de Caxias do Sul, Universidade de Caxias do Sul, Caxias do Sul, RS, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Matheus","family":"Rizzon","sequence":"additional","affiliation":[{"name":"Department of Radiology, Hospital Geral de Caxias do Sul, Universidade de Caxias do Sul, Caxias do Sul, RS, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ana Paula","family":"Agostini","sequence":"additional","affiliation":[{"name":"Department of Pediatrics and Neonatology, Faculty of Medicine, Universidade de Caxias do Sul, Caxias do Sul, RS, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Breno Fauth de","family":"Ara\u00fajo","sequence":"additional","affiliation":[{"name":"Department of Pediatrics and Neonatology, Faculty of Medicine, Universidade de Caxias do Sul, Caxias do Sul, RS, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Rosa Maria Rahmi","family":"Garcia","sequence":"additional","affiliation":[{"name":"Department of Endocrinology, Faculty of Medicine, Universidade de Caxias do Sul, Caxias do Sul, RS, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"47794","published-online":{"date-parts":[[2019,3,25]]},"reference":[{"issue":"04","key":"ref1","doi-asserted-by":"crossref","first-page":"216","DOI":"10.1002\/jcu.20318","article-title":"Pentalogy of Cantrell: sonographic assessment","volume":"35","author":"C Desselle","year":"2007","journal-title":"J Clin Ultrasound"},{"issue":"05","key":"ref2","first-page":"602","article-title":"A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium, and heart","volume":"107","author":"J R Cantrell","year":"1958","journal-title":"Surg Gynecol Obstet"},{"issue":"12","key":"ref3","doi-asserted-by":"crossref","first-page":"1825","DOI":"10.7863\/jum.2010.29.12.1825","article-title":"Diagnosis of pentalogy of Cantrell using 2- and 3-dimensional sonography","volume":"29","author":"E B Rodgers","year":"2010","journal-title":"J Ultrasound Med"},{"issue":"06","key":"ref4","doi-asserted-by":"crossref","first-page":"649","DOI":"10.1007\/s10024-004-9104-5","article-title":"Pentalogy of Cantrell: a case report with pathologic findings","volume":"7","author":"M S Correa-Rivas","year":"2004","journal-title":"Pediatr Dev Pathol"},{"issue":"04","key":"ref5","first-page":"357","article-title":"Prenatal diagnosis of Cantrell's pentalogy: a case report","volume":"45","author":"L Ondero\u011flu","year":"2003","journal-title":"Turk J Pediatr"},{"issue":"01","key":"ref6","doi-asserted-by":"crossref","first-page":"90","DOI":"10.1002\/ajmg.1320420118","article-title":"Pentalogy of Cantrell and associated midline anomalies: a possible ventral midline developmental field","volume":"42","author":"R Carmi","year":"1992","journal-title":"Am J Med Genet"},{"issue":"01","key":"ref7","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1016\/S0003-4975(00)01388-6","article-title":"Ectopia cordis and other midline defects","volume":"70","author":"J M Morales","year":"2000","journal-title":"Ann Thorac Surg"},{"key":"ref8","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1007\/s12055-005-0009-3","article-title":"Cantrell's syndrome: a report of two cases","volume":"21","author":"A P Iyer","year":"2005","journal-title":"Indian J Thoracic Cardiovascular Surg."},{"issue":"01","key":"ref9","doi-asserted-by":"crossref","first-page":"95","DOI":"10.1017\/S1047951105002192","article-title":"Cantrell's syndrome","volume":"16","author":"E Marijon","year":"2006","journal-title":"Cardiol Young"},{"issue":"01","key":"ref10","doi-asserted-by":"crossref","first-page":"71","DOI":"10.1017\/S1047951102000148","article-title":"Cardiac diverticulum and omphalocele: Cantrell's pentalogy or syndrome","volume":"12","author":"F J Halbertsma","year":"2002","journal-title":"Cardiol Young"},{"issue":"04","key":"ref11","doi-asserted-by":"crossref","first-page":"269","DOI":"10.1159\/000100788","article-title":"Prenatal and postnatal management of a patient with pentalogy of Cantrell and left ventricular aneurysm. A case report and literature review","volume":"22","author":"E J Grethel","year":"2007","journal-title":"Fetal Diagn Ther"},{"issue":"06","key":"ref12","doi-asserted-by":"crossref","first-page":"308","DOI":"10.1002\/jcu.20134","article-title":"Prenatal diagnosis of pentalogy of Cantrell in three cases, two with craniorachischisis","volume":"33","author":"I Polat","year":"2005","journal-title":"J Clin Ultrasound"},{"issue":"05","key":"ref13","doi-asserted-by":"crossref","first-page":"205","DOI":"10.1002\/(SICI)1096-9926(199811)58:5<205::AID-TERA7>3.0.CO;2-X","article-title":"Infant with midline thoracoabdominal schisis and limb defects","volume":"58","author":"E K Pivnick","year":"1998","journal-title":"Teratology"},{"issue":"01","key":"ref14","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1097\/00019605-200401000-00018","article-title":"An infant with pentalogy of Cantrell and limb defects diagnosed prenatally","volume":"13","author":"D Uygur","year":"2004","journal-title":"Clin Dysmorphol"},{"issue":"01","key":"ref15","doi-asserted-by":"crossref","first-page":"107","DOI":"10.1016\/j.jpedsurg.2003.09.030","article-title":"Combined pentalogy of Cantrell with tetralogy of Fallot, gallbladder agenesis, and polysplenia: a case report","volume":"39","author":"S Bittmann","year":"2004","journal-title":"J Pediatr Surg"},{"issue":"02","key":"ref16","doi-asserted-by":"crossref","first-page":"103","DOI":"10.1016\/S1028-4559(07)60003-5","article-title":"Syndromes and disorders associated with omphalocele (II): OEIS complex and Pentalogy of Cantrell","volume":"46","author":"C P Chen","year":"2007","journal-title":"Taiwan J Obstet Gynecol"},{"issue":"06","key":"ref17","doi-asserted-by":"crossref","first-page":"839","DOI":"10.1002\/ajmg.1320420619","article-title":"Pentalogy of Cantrell and ectopia cordis, a familial developmental field complex","volume":"42","author":"R A Martin","year":"1992","journal-title":"Am J Med Genet"},{"issue":"05","key":"ref18","first-page":"778","article-title":"Combined congenital defects of the anterior abdominal wall, sternum, diaphragm, pericardium, and heart: a case report and review of the syndrome","volume":"50","author":"W M Toyama","year":"1972","journal-title":"Pediatrics"},{"issue":"02","key":"ref19","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1046\/j.1469-0705.1997.10020137.x","article-title":"Prenatal diagnosis of ectopia cordis at 10 weeks of gestation using two-dimensional and three-dimensional ultrasonography","volume":"10","author":"R I Liang","year":"1997","journal-title":"Ultrasound Obstet Gynecol"},{"key":"ref20","first-page":"840","article-title":"Omphalocele and pericardial effusion: possible sonographic markers for the pentalogy of Cantrell or its variants","volume":"87","author":"C Siles","year":"1996","journal-title":"Obstet Gynecol"},{"issue":"03","key":"ref21","doi-asserted-by":"crossref","first-page":"172","DOI":"10.1007\/s00246-006-0032-1","article-title":"Diagnosis of pentalogy of cantrell in the fetus using magnetic resonance imaging and ultrasound","volume":"28","author":"C J McMahon","year":"2007","journal-title":"Pediatr Cardiol"},{"issue":"01","key":"ref22","doi-asserted-by":"crossref","first-page":"84","DOI":"10.1067\/mpd.2003.mpd031","article-title":"Usefulness of helical CT angiography and MRI in the diagnosis and treatment of pentalogy of Cantrell","volume":"142","author":"T Oka","year":"2003","journal-title":"J Pediatr"},{"issue":"09","key":"ref23","doi-asserted-by":"crossref","first-page":"638","DOI":"10.1007\/s002470000288","article-title":"MR imaging of pentalogy of Cantrell variant with an intact diaphragm and pericardium","volume":"30","author":"A Song","year":"2000","journal-title":"Pediatr Radiol"},{"issue":"02","key":"ref24","doi-asserted-by":"crossref","first-page":"112","DOI":"10.1002\/jcu.20498","article-title":"Prenatal diagnosis of Pentalogy of Cantrell in the first trimester: is 3-dimensional sonography needed?","volume":"37","author":"F M Peixoto-Filho","year":"2009","journal-title":"J Clin Ultrasound"},{"issue":"06","key":"ref25","doi-asserted-by":"crossref","first-page":"544","DOI":"10.1159\/000095670","article-title":"Diagnosis of Pentalogy of Cantrell by three-dimensional ultrasound in third trimester of pregnancy. A case report","volume":"21","author":"E Araujo J\u00fanior","year":"2006","journal-title":"Fetal Diagn Ther"},{"issue":"01","key":"ref26","doi-asserted-by":"crossref","first-page":"29","DOI":"10.1007\/s00431-007-0578-9","article-title":"Pentalogy of Cantrell: two patients and a review to determine prognostic factors for optimal approach","volume":"167","author":"J HL van Hoorn","year":"2008","journal-title":"Eur J Pediatr"},{"issue":"03","key":"ref27","first-page":"85","article-title":"Two rare cases of the Pentalogy of Cantrell or its variants","volume":"31","author":"A Aslan","year":"2004","journal-title":"Acta Med Austriaca"},{"issue":"12","key":"ref28","first-page":"1087","article-title":"Cantrell syndrome in one of a set of monozygotic twins","volume":"47","author":"R Y Bhat","year":"2006","journal-title":"Singapore Med J"},{"issue":"02","key":"ref29","doi-asserted-by":"crossref","first-page":"95","DOI":"10.4103\/2249-4847.116410","article-title":"Pentalogy of cantrell: an extremely rare congenital anomaly","volume":"2","author":"S Chandran","year":"2013","journal-title":"J Clin Neonatol"},{"issue":"03","key":"ref30","doi-asserted-by":"crossref","first-page":"805","DOI":"10.1002\/ajmg.1320300313","article-title":"Trisomy 18 associated with ectopia cordis and occipital meningocele","volume":"30","author":"D Bick","year":"1988","journal-title":"Am J Med Genet"},{"issue":"07","key":"ref31","doi-asserted-by":"crossref","first-page":"1703","DOI":"10.1007\/s00246-013-0706-4","article-title":"Spectrum of Cantrell's pentalogy: case series from a single tertiary care center and review of the literature","volume":"34","author":"K K Mallula","year":"2013","journal-title":"Pediatr Cardiol"}],"container-title":["Revista Brasileira de Ginecologia e Obstetr\u00edcia \/ RBGO Gynecology and Obstetrics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journalrbgo.org\/article\/ectopia-cordis-associated-with-pentalogy-of-cantrell-a-case-report\/","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.1055\/s-0039-1679878.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,7,18]],"date-time":"2024-07-18T20:56:59Z","timestamp":1721336219000},"score":1,"resource":{"primary":{"URL":"https:\/\/journalrbgo.org\/article\/ectopia-cordis-associated-with-pentalogy-of-cantrell-a-case-report\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,3,25]]},"references-count":31,"journal-issue":{"issue":"05","published-online":{"date-parts":[[2019,6,10]]},"published-print":{"date-parts":[[2019,5]]}},"URL":"https:\/\/doi.org\/10.1055\/s-0039-1679878","archive":["Portico","CLOCKSS"],"relation":{},"ISSN":["0100-7203","1806-9339"],"issn-type":[{"value":"0100-7203","type":"print"},{"value":"1806-9339","type":"electronic"}],"subject":[],"published":{"date-parts":[[2019,3,25]]}}}